- Metabolite
- HMDB0000959 (Tiglylglycine)
- Biospecimen
- Urine
- Status
- Detected and Quantified
- Data source
- Referenced
- Concentration
- 930.484-993.797 umol/mmol creatinine
- Age
- Children (1 - 13 years old)
- Sex
- Female
- Condition
- Ketosis
Comments
Ketosis in 3-Ketothiolase deficiency
References
- B. Middleton et al. (1986). B. Middleton et al. 3-Ketothiolase deficiency. Eur J Pediatr (1986) 144:586-589. Eur J Pediatr.