- Metabolite
- HMDB0000060 (Acetoacetic acid)
- Biospecimen
- Blood
- Status
- Detected and Quantified
- Data source
- Referenced
- Concentration
- 910 uM
- Age
- Children (1-13 years old)
- Sex
- Male
- Condition
- Succinyl CoA: 3-ketoacid CoA transferase deficiency
Comments
After 12 hours fasting. Higher than control
References
- Snyderman SE, Sansaricq C, Middleton B: Succinyl-CoA:3-ketoacid CoA-transferase deficiency. Pediatrics. 1998 Apr;101(4 Pt 1):709-11. [PubMed:9521962 ]