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Human Metabolome Database Version 3.5

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Showing metabocard for Water (HMDB02111)

Record Information
Version 3.5
Creation Date 2006-05-22 08:17:36 -0600
Update Date 2013-02-08 17:11:24 -0700
HMDB ID HMDB02111
Secondary Accession Numbers None
Metabolite Identification
Common Name Water
Description Water is a chemical substance that is essential to all known forms of life. It appears colorless to the naked eye in small quantities, though it is actually slightly blue in color. It covers 71% of Earth's surface. Current estimates suggest that there are 1.4 billion cubic kilometers (330 million m3) of it available on Earth, and it exists in many forms. It appears mostly in the oceans (saltwater) and polar ice caps, but it is also present as clouds, rain water, rivers, freshwater aquifers, lakes, and sea ice. Water in these bodies perpetually moves through a cycle of evaporation, precipitation, and runoff to the sea. Clean water is essential to human life. In many parts of the world, it is in short supply. From a biological standpoint, water has many distinct properties that are critical for the proliferation of life that set it apart from other substances. It carries out this role by allowing organic compounds to react in ways that ultimately allow replication. All known forms of life depend on water. Water is vital both as a solvent in which many of the body's solutes dissolve and as an essential part of many metabolic processes within the body. Metabolism is the sum total of anabolism and catabolism. In anabolism, water is removed from molecules (through energy requiring enzymatic chemical reactions) in order to grow larger molecules (e.g. starches, triglycerides and proteins for storage of fuels and information). In catabolism, water is used to break bonds in order to generate smaller molecules (e.g. glucose, fatty acids and amino acids to be used for fuels for energy use or other purposes). Water is thus essential and central to these metabolic processes. Water is also central to photosynthesis and respiration. Photosynthetic cells use the sun's energy to split off water's hydrogen from oxygen. Hydrogen is combined with CO2 (absorbed from air or water) to form glucose and release oxygen. All living cells use such fuels and oxidize the hydrogen and carbon to capture the sun's energy and reform water and CO2 in the process (cellular respiration). Water is also central to acid-base neutrality and enzyme function. An acid, a hydrogen ion (H+, that is, a proton) donor, can be neutralized by a base, a proton acceptor such as hydroxide ion (OH-) to form water. Water is considered to be neutral, with a pH (the negative log of the hydrogen ion concentration) of 7. Acids have pH values less than 7 while bases have values greater than 7. Stomach acid (HCl) is useful to digestion. However, its corrosive effect on the esophagus during reflux can temporarily be neutralized by ingestion of a base such as aluminum hydroxide to produce the neutral molecules water and the salt aluminum chloride. Human biochemistry that involves enzymes usually performs optimally around a biologically neutral pH of 7.4. (Wikipedia).
Structure Thumb
Download: MOL | SDF | SMILES | InChI
Display: 2D Structure | 3D Structure
Synonyms
  1. Dihydrogen oxide
  2. Steam
Chemical Formula H2O
Average Molecular Weight 18.0153
Monoisotopic Molecular Weight 18.010564686
IUPAC Name water
Traditional IUPAC Name water
CAS Registry Number 7732-18-5
SMILES O
InChI Identifier InChI=1S/H2O/h1H2
InChI Key XLYOFNOQVPJJNP-UHFFFAOYSA-N
Chemical Taxonomy
Kingdom Inorganic Compounds
Super Class Homogeneous Non-metal Compounds
Class Other Non-metal Organides
Sub Class Other Non-metal Oxides
Other Descriptors
  • a small molecule(Cyc)
  • inorganic hydroxy compound(ChEBI)
  • mononuclear parent hydride(ChEBI)
  • oxygen hydride(ChEBI)
Substituents
  • N/A
Direct Parent Other Non-metal Oxides
Ontology
Status Detected and Quantified
Origin
  • Food
  • Drug
  • Endogenous
  • Cosmetic
  • Plant
Biofunction
  • Osmolyte, enzyme cofactor, signalling
Application Not Available
Cellular locations
  • Cytoplasm
  • Extracellular
  • Mitochondria
  • Nucleus
  • Lysosome
  • Endoplasmic reticulum
  • Golgi apparatus
  • Peroxisome
Physical Properties
State Liquid
Experimental Properties
Property Value Reference
Melting Point 0 °C Not Available
Boiling Point Not Available Not Available
Water Solubility 55.5 mol/L Not Available
LogP -1.38 HANSCH,C ET AL. (1995)
Predicted Properties
Property Value Source
Water Solubility ALOGPS
LogP -0.65 ChemAxon
pKa (strongest acidic) 15.7 ChemAxon
pKa (strongest basic) -1.8 ChemAxon
Hydrogen Acceptor Count 1 ChemAxon
Hydrogen Donor Count 1 ChemAxon
Polar Surface Area 25.3 A2 ChemAxon
Rotatable Bond Count 0 ChemAxon
Refractivity 3.7 ChemAxon
Polarizability 1.51 ChemAxon
Formal Charge 0 ChemAxon
Physiological Charge 0 ChemAxon
Spectra
Not Available
Biological Properties
Cellular Locations
  • Cytoplasm
  • Extracellular
  • Mitochondria
  • Nucleus
  • Lysosome
  • Endoplasmic reticulum
  • Golgi apparatus
  • Peroxisome
Biofluid Locations
  • Amniotic Fluid
  • Aqueous Humour
  • Ascites Fluid
  • Blood
  • Breast Milk
  • Cerebrospinal Fluid (CSF)
  • Lymph
  • Saliva
  • Sweat
  • Tears
Tissue Location
  • All Tissues
Pathways
Name SMPDB Link KEGG Link
Citric Acid Cycle SMP00057 map00020 Link_out
Gluconeogenesis SMP00128 map00010 Link_out
Phenylalanine and Tyrosine Metabolism SMP00008 map00360 Link_out
Urea Cycle SMP00059 map00330 Link_out
Glucose-Alanine Cycle SMP00127 Not Available
Mitochondrial Electron Transport Chain SMP00355 map00190 Link_out
D-Arginine and D-Ornithine Metabolism SMP00036 map00472 Link_out
Ammonia Recycling SMP00009 map00910 Link_out
Glycolysis SMP00040 map00010 Link_out
Ethanol Degradation SMP00449 Not Available
Homocysteine Degradation SMP00455 Not Available
Lactose Degradation SMP00457 Not Available
Pyruvaldehyde Degradation SMP00459 Not Available
Carnitine Synthesis SMP00465 Not Available
Transfer of Acetyl Groups into Mitochondria SMP00466 Not Available
Trehalose Degradation SMP00467 Not Available
Degradation of Superoxides SMP00468 Not Available
Catecholamine Biosynthesis SMP00012 map00350 Link_out
Plasmalogen Synthesis SMP00479 Not Available
Arachidonic Acid Metabolism SMP00075 map00590 Link_out
Amino Sugar Metabolism SMP00045 map00520 Link_out
Mitochondrial Beta-Oxidation of Short Chain Saturated Fatty Acids SMP00480 Not Available
Glycine and Serine Metabolism SMP00004 map00260 Link_out
Spermidine and Spermine Biosynthesis SMP00445 Not Available
Folate Metabolism SMP00053 map00670 Link_out
Pterine Biosynthesis SMP00005 map00790 Link_out
Mitochondrial Beta-Oxidation of Long Chain Saturated Fatty Acids SMP00482 Not Available
Mitochondrial Beta-Oxidation of Medium Chain Saturated Fatty Acids SMP00481 Not Available
Normal Concentrations
Biofluid Status Value Age Sex Condition Comments
Amniotic Fluid Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Aqueous Humour Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Ascites Fluid Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Blood Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Breast Milk Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Cerebrospinal Fluid (CSF) Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Lymph Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Saliva Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Sweat Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Tears Detected and Quantified
Article_icon
55,000,000 uM Adult (>18 years old) Both Normal Not Available
Abnormal Concentrations
Not Available
Associated Disorders and Diseases
Disease References None
Associated OMIM IDs None
DrugBank ID Not Available
Phenol Explorer Compound ID Not Available
Phenol Explorer Metabolite ID Not Available
FoodDB ID FDB013390
KNApSAcK ID Not Available
Chemspider ID 937 Link_out
KEGG Compound ID C00001 Link_out
BioCyc ID Not Available
BiGG ID 33474 Link_out
Wikipedia Link Water Link_out
NuGOwiki Link HMDB02111 Link_out
Metagene Link HMDB02111 Link_out
METLIN ID 3194 Link_out
PubChem Compound 962 Link_out
PDB ID HOH Link_out
ChEBI ID 15377 Link_out
References
Synthesis Reference Not Available
Material Safety Data Sheet (MSDS) Download (PDF)
General References Not Available

Enzymes
Name: Deoxycytidylate deaminase
Reactions:
  • dCMP + H2O = dUMP + NH3 [RN:R01663]
Gene Name: DCTD
Uniprot ID: P32321 Link_out
Protein Sequence: FASTA
Gene Sequence: FASTA
Name: Cytosolic 5'-nucleotidase 1B
Reactions:
  • a 5'-ribonucleotide + H2O = a ribonucleoside + phosphate [RN:R07297]
Gene Name: NT5C1B
Uniprot ID: Q96P26 Link_out
Protein Sequence: FASTA
Gene Sequence: FASTA
Name: Cytosolic 5'-nucleotidase 1A
Reactions:
  • a 5'-ribonucleotide + H2O = a ribonucleoside + phosphate [RN:R07297]
Gene Name: NT5C1A
Uniprot ID: Q9BXI3 Link_out
Protein Sequence: FASTA
Gene Sequence: FASTA
Name: 5'(3')-deoxyribonucleotidase, cytosolic type
Reactions:
    Gene Name: NT5C
    Uniprot ID: Q8TCD5 Link_out
    Protein Sequence: FASTA
    Gene Sequence: FASTA
    Name: 5'(3')-deoxyribonucleotidase, mitochondrial
    Reactions:
      Gene Name: NT5M
      Uniprot ID: Q9NPB1 Link_out
      Protein Sequence: FASTA
      Gene Sequence: FASTA
      Name: Acyl-coenzyme A thioesterase 12
      Reactions:
      • acetyl-CoA + H2O = CoA + acetate [RN:R00227]
      Gene Name: ACOT12
      Uniprot ID: Q8WYK0 Link_out
      Protein Sequence: FASTA
      Gene Sequence: FASTA
      Name: Fatty acid synthase
      Reactions:
      • a (3R)-3-hydroxypalmitoyl-[acyl-carrier protein] = a hexadec-2-enoyl-[acyl-carrier protein] + H2O [RN:R04462]
      Gene Name: FASN
      Uniprot ID: P49327 Link_out
      Protein Sequence: FASTA
      Gene Sequence: FASTA
      Name: Hydroxymethylglutaryl-CoA synthase, mitochondrial
      Reactions:
      • acetyl-CoA + H2O + acetoacetyl-CoA = (S)-3-hydroxy-3-methylglutaryl-CoA + CoA [RN:R01978]
      Gene Name: HMGCS2
      Uniprot ID: P54868 Link_out
      Protein Sequence: FASTA
      Gene Sequence: FASTA
      Name: Citrate synthase, mitochondrial
      Reactions:
      • acetyl-CoA + H2O + oxaloacetate = citrate + CoA [RN:R00351]
      Gene Name: CS
      Uniprot ID: O75390 Link_out
      Protein Sequence: FASTA
      Gene Sequence: FASTA
      Name: Hydroxymethylglutaryl-CoA synthase, cytoplasmic
      Reactions:
      • acetyl-CoA + H2O + acetoacetyl-CoA = (S)-3-hydroxy-3-methylglutaryl-CoA + CoA [RN:R01978]
      Gene Name: HMGCS1
      Uniprot ID: Q01581 Link_out
      Protein Sequence: FASTA
      Gene Sequence: FASTA
      Name: Acyl-protein thioesterase 1
      Reactions:
        Gene Name: LYPLA1
        Uniprot ID: O75608 Link_out
        Protein Sequence: FASTA
        Gene Sequence: FASTA
        Name: Group XV phospholipase A2
        Reactions:
          Gene Name: PLA2G15
          Uniprot ID: Q8NCC3 Link_out
          Protein Sequence: FASTA
          Gene Sequence: FASTA
          Name: Calcium-dependent phospholipase A2
          Reactions:
          • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
          Gene Name: PLA2G5
          Uniprot ID: P39877 Link_out
          Protein Sequence: FASTA
          Gene Sequence: FASTA
          Name: Group IIF secretory phospholipase A2
          Reactions:
          • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
          Gene Name: PLA2G2F
          Uniprot ID: Q9BZM2 Link_out
          Protein Sequence: FASTA
          Gene Sequence: FASTA
          Name: Cytosolic phospholipase A2
          Reactions:
          • 2-lysophosphatidylcholine + H2O = glycerophosphocholine + a carboxylate [RN:R07291]
          Gene Name: PLA2G4A
          Uniprot ID: P47712 Link_out
          Protein Sequence: FASTA
          Gene Sequence: FASTA
          Name: Phospholipase A2
          Reactions:
          • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
          Gene Name: PLA2G1B
          Uniprot ID: P04054 Link_out
          Protein Sequence: FASTA
          Gene Sequence: FASTA
          Name: Group XIIB secretory phospholipase A2-like protein
          Reactions:
            Gene Name: PLA2G12B
            Uniprot ID: Q9BX93 Link_out
            Protein Sequence: FASTA
            Gene Sequence: FASTA
            Name: Group 10 secretory phospholipase A2
            Reactions:
            • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
            Gene Name: PLA2G10
            Uniprot ID: O15496 Link_out
            Protein Sequence: FASTA
            Gene Sequence: FASTA
            Name: Group IIE secretory phospholipase A2
            Reactions:
            • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
            Gene Name: PLA2G2E
            Uniprot ID: Q9NZK7 Link_out
            Protein Sequence: FASTA
            Gene Sequence: FASTA
            Name: Acyl-protein thioesterase 2
            Reactions:
              Gene Name: LYPLA2
              Uniprot ID: O95372 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: 85 kDa calcium-independent phospholipase A2
              Reactions:
              • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
              Gene Name: PLA2G6
              Uniprot ID: O60733 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Eosinophil lysophospholipase
              Reactions:
              • 2-lysophosphatidylcholine + H2O = glycerophosphocholine + a carboxylate [RN:R07291]
              Gene Name: CLC
              Uniprot ID: Q05315 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Group IID secretory phospholipase A2
              Reactions:
              • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
              Gene Name: PLA2G2D
              Uniprot ID: Q9UNK4 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Phospholipase D2
              Reactions:
              • a phosphatidylcholine + H2O = choline + a phosphatidate [RN:R01310]
              Gene Name: PLD2
              Uniprot ID: O14939 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Ectonucleoside triphosphate diphosphohydrolase 1
              Reactions:
              • ATP + 2 H2O = AMP + 2 phosphate [RN:R00085]
              Gene Name: ENTPD1
              Uniprot ID: P49961 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Soluble calcium-activated nucleotidase 1
              Reactions:
              • a nucleoside diphosphate + H2O = a nucleotide + phosphate [RN:R00329]
              Gene Name: CANT1
              Uniprot ID: Q8WVQ1 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Ectonucleoside triphosphate diphosphohydrolase 3
              Reactions:
              • ATP + 2 H2O = AMP + 2 phosphate [RN:R00085]
              Gene Name: ENTPD3
              Uniprot ID: O75355 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Tyrosinase
              Reactions:
              • L-tyrosine + L-dopa + O2 = L-dopa + dopaquinone + H2O [RN:R02078]
              Gene Name: TYR
              Uniprot ID: P14679 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Serum paraoxonase/lactonase 3
              Reactions:
              • an aryl dialkyl phosphate + H2O = dialkyl phosphate + an aryl alcohol [RN:R03979]
              Gene Name: PON3
              Uniprot ID: Q15166 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Alkaline phosphatase, placental type
              Reactions:
              • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
              Gene Name: ALPP
              Uniprot ID: P05187 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Serum paraoxonase/arylesterase 2
              Reactions:
              • an N-acyl-L-homoserine lactone + H2O = an N-acyl-L-homoserine [RN:R08970]
              Gene Name: PON2
              Uniprot ID: Q15165 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Intestinal-type alkaline phosphatase
              Reactions:
              • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
              Gene Name: ALPI
              Uniprot ID: P09923 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Alkaline phosphatase, tissue-nonspecific isozyme
              Reactions:
              • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
              Gene Name: ALPL
              Uniprot ID: P05186 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Tartrate-resistant acid phosphatase type 5
              Reactions:
              • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
              Gene Name: ACP5
              Uniprot ID: P13686 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Prostatic acid phosphatase
              Reactions:
              • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
              Gene Name: ACPP
              Uniprot ID: P15309 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Alkaline phosphatase, placental-like
              Reactions:
              • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
              Gene Name: ALPPL2
              Uniprot ID: P10696 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Ribonucleoside-diphosphate reductase large subunit
              Reactions:
              • 2'-deoxyribonucleoside diphosphate + thioredoxin disulfide + H2O = ribonucleoside diphosphate + thioredoxin [RN:R04294]
              Gene Name: RRM1
              Uniprot ID: P23921 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Ribonucleoside-diphosphate reductase subunit M2
              Reactions:
              • 2'-deoxyribonucleoside diphosphate + thioredoxin disulfide + H2O = ribonucleoside diphosphate + thioredoxin [RN:R04294]
              Gene Name: RRM2
              Uniprot ID: P31350 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Ectonucleotide pyrophosphatase/phosphodiesterase family member 1
              Reactions:
              • a dinucleotide + H2O = 2 mononucleotides [RN:R00056]
              Gene Name: ENPP1
              Uniprot ID: P22413 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Peroxisomal sarcosine oxidase
              Reactions:
              • L-pipecolate + O2 = 2,3,4,5-tetrahydropyridine-2-carboxylate + H2O2 [RN:R02204]
              Gene Name: PIPOX
              Uniprot ID: Q9P0Z9 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Peroxisomal N(1)-acetyl-spermine/spermidine oxidase
              Reactions:
              • (1) N1-acetylspermidine + O2 + H2O = putrescine + 3-acetamidopropanal + H2O2 [RN:R09074]
              • (2) N1-acetylspermine + O2 + H2O = spermidine + 3-acetamidopropanal + H2O2 [RN:R03899]
              Gene Name: PAOX
              Uniprot ID: Q6QHF9 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Aldehyde oxidase
              Reactions:
              • an aldehyde + H2O + O2 = a carboxylic acid + H2O2 [RN:R00635]
              Gene Name: AOX1
              Uniprot ID: Q06278 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lathosterol oxidase
              Reactions:
              • 5alpha-cholest-7-en-3beta-ol + NAD(P)H + H+ + O2 = cholesta-5,7-dien-3beta-ol + NAD(P)+ + 2 H2O [RN:R03310 R07215]
              Gene Name: SC5DL
              Uniprot ID: O75845 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Dimethylaniline monooxygenase [N-oxide-forming] 5
              Reactions:
              • N,N-dimethylaniline + NADPH + H+ + O2 = N,N-dimethylaniline N-oxide + NADP+ + H2O [RN:R03344]
              Gene Name: FMO5
              Uniprot ID: P49326 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: D-aspartate oxidase
              Reactions:
              • D-aspartate + H2O + O2 = oxaloacetate + NH3 + H2O2 [RN:R00359]
              Gene Name: DDO
              Uniprot ID: Q99489 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Heme oxygenase 2
              Reactions:
              • heme + 3 AH2 + 3 O2 = biliverdin + Fe2+ + CO + 3 A + 3 H2O [RN:R00311]
              Gene Name: HMOX2
              Uniprot ID: P30519 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Dimethylaniline monooxygenase [N-oxide-forming] 2
              Reactions:
              • N,N-dimethylaniline + NADPH + H+ + O2 = N,N-dimethylaniline N-oxide + NADP+ + H2O [RN:R03344]
              Gene Name: FMO2
              Uniprot ID: Q99518 Link_out
              Protein Sequence: FASTA
              Name: Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial
              Reactions:
              • (S)-1-pyrroline-5-carboxylate + NAD(P)+ + 2 H2O = L-glutamate + NAD(P)H + H+ [RN:R00707 R00708]
              Gene Name: ALDH4A1
              Uniprot ID: P30038 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Amine oxidase [flavin-containing] B
              Reactions:
              • RCH2NHR' + H2O + O2 = RCHO + R'NH2 + H2O2 [RN:R01853]
              Gene Name: MAOB
              Uniprot ID: P27338 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Peroxisomal acyl-coenzyme A oxidase 2
              Reactions:
              • (25R)-3alpha,7alpha,12alpha-trihydroxy-5beta-cholestan-26-oyl-CoA + H2O + acceptor = (24R,25R)-3alpha,7alpha,12alpha,24-tetrahydroxy-5beta-cholestan-26- oyl-CoA + reduced acceptor [RN:R07374]
              Gene Name: ACOX2
              Uniprot ID: Q99424 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Dimethylaniline monooxygenase [N-oxide-forming] 4
              Reactions:
              • N,N-dimethylaniline + NADPH + H+ + O2 = N,N-dimethylaniline N-oxide + NADP+ + H2O [RN:R03344]
              Gene Name: FMO4
              Uniprot ID: P31512 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Ectonucleotide pyrophosphatase/phosphodiesterase family member 2
              Reactions:
              • 1-alkyl-sn-glycero-3-phosphoethanolamine + H2O = 1-alkyl-sn-glycerol 3-phosphate + ethanolamine [RN:R04362]
              Gene Name: ENPP2
              Uniprot ID: Q13822 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Amine oxidase [flavin-containing] A
              Reactions:
              • RCH2NHR' + H2O + O2 = RCHO + R'NH2 + H2O2 [RN:R01853]
              Gene Name: MAOA
              Uniprot ID: P21397 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Dimethylaniline monooxygenase [N-oxide-forming] 3
              Reactions:
              • N,N-dimethylaniline + NADPH + H+ + O2 = N,N-dimethylaniline N-oxide + NADP+ + H2O [RN:R03344]
              Gene Name: FMO3
              Uniprot ID: P31513 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Xanthine dehydrogenase/oxidase
              Reactions:
              • xanthine + H2O + O2 = urate + H2O2 [RN:R02107]
              Gene Name: XDH
              Uniprot ID: P47989 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Ectonucleotide pyrophosphatase/phosphodiesterase family member 3
              Reactions:
              • a dinucleotide + H2O = 2 mononucleotides [RN:R00056]
              Gene Name: ENPP3
              Uniprot ID: O14638 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Heme oxygenase 1
              Reactions:
              • heme + 3 AH2 + 3 O2 = biliverdin + Fe2+ + CO + 3 A + 3 H2O [RN:R00311]
              Gene Name: HMOX1
              Uniprot ID: P09601 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Retinal dehydrogenase 1
              Reactions:
              • retinal + NAD+ + H2O = retinoate + NADH + 2 H+ [RN:R02123]
              Gene Name: ALDH1A1
              Uniprot ID: P00352 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Dimethylglycine dehydrogenase, mitochondrial
              Reactions:
              • N,N-dimethylglycine + acceptor + H2O = sarcosine + formaldehyde + reduced acceptor [RN:R01565]
              Gene Name: DMGDH
              Uniprot ID: Q9UI17 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Retinal dehydrogenase 2
              Reactions:
              • retinal + NAD+ + H2O = retinoate + NADH + 2 H+ [RN:R02123]
              Gene Name: ALDH1A2
              Uniprot ID: O94788 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: D-amino-acid oxidase
              Reactions:
              • a D-amino acid + H2O + O2 = a 2-oxo acid + NH3 + H2O2 [RN:R01340]
              Gene Name: DAO
              Uniprot ID: P14920 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Glucosamine-6-phosphate isomerase 1
              Reactions:
              • D-glucosamine 6-phosphate + H2O = D-fructose 6-phosphate + NH3 [RN:R00765]
              Gene Name: GNPDA1
              Uniprot ID: P46926 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Pancreatic triacylglycerol lipase
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: PNLIP
              Uniprot ID: P16233 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: 1-phosphatidylinositol-4,5-bisphosphate phosphodiesterase beta-1
              Reactions:
              • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1D-myo-inositol 1,4,5-trisphosphate + diacylglycerol
              Gene Name: PLCB1
              Uniprot ID: Q9NQ66 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: 1-phosphatidylinositol-4,5-bisphosphate phosphodiesterase beta-4
              Reactions:
              • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1D-myo-inositol 1,4,5-trisphosphate + diacylglycerol
              Gene Name: PLCB4
              Uniprot ID: Q15147 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: 1-phosphatidylinositol-4,5-bisphosphate phosphodiesterase beta-2
              Reactions:
              • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1D-myo-inositol 1,4,5-trisphosphate + diacylglycerol
              Gene Name: PLCB2
              Uniprot ID: Q00722 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Hepatic triacylglycerol lipase
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: LIPC
              Uniprot ID: P11150 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lysosomal acid lipase/cholesteryl ester hydrolase
              Reactions:
              • a steryl ester + H2O = a sterol + a fatty acid [RN:R02115]
              Gene Name: LIPA
              Uniprot ID: P38571 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: 1-phosphatidylinositol-4,5-bisphosphate phosphodiesterase beta-3
              Reactions:
              • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1D-myo-inositol 1,4,5-trisphosphate + diacylglycerol
              Gene Name: PLCB3
              Uniprot ID: Q01970 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Pancreatic lipase-related protein 1
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: PNLIPRP1
              Uniprot ID: P54315 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: 1-phosphatidylinositol-4,5-bisphosphate phosphodiesterase gamma-2
              Reactions:
              • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1D-myo-inositol 1,4,5-trisphosphate + diacylglycerol
              Gene Name: PLCG2
              Uniprot ID: P16885 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lipid phosphate phosphohydrolase 2
              Reactions:
              • a 1,2-diacylglycerol 3-phosphate + H2O = a 1,2-diacyl-sn-glycerol + phosphate [RN:R02239]
              Gene Name: PPAP2C
              Uniprot ID: O43688 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Patatin-like phospholipase domain-containing protein 3
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: PNPLA3
              Uniprot ID: Q9NST1 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Gastric triacylglycerol lipase
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: LIPF
              Uniprot ID: P07098 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lipid phosphate phosphohydrolase 1
              Reactions:
              • a 1,2-diacylglycerol 3-phosphate + H2O = a 1,2-diacyl-sn-glycerol + phosphate [RN:R02239]
              Gene Name: PPAP2A
              Uniprot ID: O14494 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Endothelial lipase
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: LIPG
              Uniprot ID: Q9Y5X9 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Bile salt-activated lipase
              Reactions:
              • a steryl ester + H2O = a sterol + a fatty acid [RN:R02115]
              Gene Name: CEL
              Uniprot ID: P19835 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lipid phosphate phosphohydrolase 3
              Reactions:
              • a 1,2-diacylglycerol 3-phosphate + H2O = a 1,2-diacyl-sn-glycerol + phosphate [RN:R02239]
              Gene Name: PPAP2B
              Uniprot ID: O14495 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Pancreatic lipase-related protein 2
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: PNLIPRP2
              Uniprot ID: P54317 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Succinate-semialdehyde dehydrogenase, mitochondrial
              Reactions:
              • succinate semialdehyde + NAD+ + H2O = succinate + NADH + 2 H+ [RN:R00713]
              Gene Name: ALDH5A1
              Uniprot ID: P51649 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Coproporphyrinogen-III oxidase, mitochondrial
              Reactions:
              • coproporphyrinogen III + O2 + 2 H+ = protoporphyrinogen-IX + 2 CO2 + 2 H2O [RN:R03220]
              Gene Name: CPOX
              Uniprot ID: P36551 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Peptidyl-glycine alpha-amidating monooxygenase
              Reactions:
              • peptidylamidoglycolate = peptidyl amide + glyoxylate [RN:R03874]
              Gene Name: PAM
              Uniprot ID: P19021 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Dopamine beta-hydroxylase
              Reactions:
              • 3,4-dihydroxyphenethylamine + ascorbate + O2 = noradrenaline + dehydroascorbate + H2O [RN:R02535]
              Gene Name: DBH
              Uniprot ID: P09172 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: C-4 methylsterol oxidase
              Reactions:
              • (1) (1a) 4,4-dimethyl-5alpha-cholest-7-en-3beta-ol + NAD(P)H + H+ + O2 = 4beta-hydroxymethyl-4alpha-methyl-5alpha-cholest-7-en-3beta-ol + NAD(P)+ + H2O [RN:R04501 R05736]
              • (2) (1b) 4beta-hydroxymethyl-4alpha-methyl-5alpha-cholest-7-en-3beta-ol + NAD(P)H + H+ + O2 = 3beta-hydroxy-4beta-methyl-5alpha-cholest-7-ene-4alpha-carbaldehyde + NAD(P)+ + 2 H2O [RN:R05733 R05737]
              • (3) (1c) 3beta-hydroxy-4beta-methyl-5alpha-cholest-7-ene-4alpha-carbaldehyde + NAD(P)H + H+ + O2 = 3beta-hydroxy-4beta-methyl-5alpha-cholest-7-ene-4alpha-carboxylate + NAD(P)+ + H2O [RN:R05734 R05738]
              Gene Name: SC4MOL
              Uniprot ID: Q15800 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Sterol-4-alpha-carboxylate 3-dehydrogenase, decarboxylating
              Reactions:
              • 3beta-hydroxy-4beta-methyl-5alpha-cholest-7-ene-4alpha-carboxylate + NAD(P)+ = 4alpha-methyl-5alpha-cholest-7-en-3-one + CO2 + NAD(P)H [RN:R04483 R07149]
              Gene Name: NSDHL
              Uniprot ID: Q15738 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lanosterol 14-alpha demethylase
              Reactions:
              • obtusifoliol + 3 O2 + 3 NADPH + 3 H+ = 4alpha-methyl-5alpha-ergosta-8,14,24(28)-trien-3beta-ol + formate + 3 NADP+ + 4 H2O [RN:R05731]
              Gene Name: CYP51A1
              Uniprot ID: Q16850 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Tyrosine 3-monooxygenase
              Reactions:
              • L-tyrosine + tetrahydrobiopterin + O2 = 3,4-dihydroxy-L-phenylalanine + 4a-hydroxytetrahydrobiopterin [RN:R07212]
              Gene Name: TH
              Uniprot ID: P07101 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Thyroid peroxidase
              Reactions:
              • 2 iodide + H2O2 + 2 H+ = diiodine + 2 H2O [RN:R02810]
              Gene Name: TPO
              Uniprot ID: P07202 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lactoperoxidase
              Reactions:
              • donor + H2O2 = oxidized donor + 2 H2O [RN:R03532]
              Gene Name: LPO
              Uniprot ID: P22079 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Phenylalanine-4-hydroxylase
              Reactions:
              • L-phenylalanine + tetrahydrobiopterin + O2 = L-tyrosine + 4a-hydroxytetrahydrobiopterin [RN:R07211]
              Gene Name: PAH
              Uniprot ID: P00439 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Myeloperoxidase
              Reactions:
              • donor + H2O2 = oxidized donor + 2 H2O [RN:R03532]
              Gene Name: MPO
              Uniprot ID: P05164 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Eosinophil peroxidase
              Reactions:
              • donor + H2O2 = oxidized donor + 2 H2O [RN:R03532]
              Gene Name: EPX
              Uniprot ID: P11678 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Sucrase-isomaltase, intestinal
              Reactions:
              • Hydrolysis of sucrose and maltose by an alpha-D-glucosidase-type action [RN:R00801 R06087] ALL_REAC R00801 R06087(G) > R00802 R06088(G)
              Gene Name: SI
              Uniprot ID: P14410 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: 4-trimethylaminobutyraldehyde dehydrogenase
              Reactions:
              • 4-trimethylammoniobutanal + NAD+ + H2O = 4-trimethylammoniobutanoate + NADH + 2 H+ [RN:R03283]
              Gene Name: ALDH9A1
              Uniprot ID: P49189 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Alpha-aminoadipic semialdehyde dehydrogenase
              Reactions:
              • L-2-aminoadipate 6-semialdehyde + NAD(P)+ + H2O = L-2-aminoadipate + NAD(P)H + H+ [RN:R03102 R03103]
              Gene Name: ALDH7A1
              Uniprot ID: P49419 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Aldehyde dehydrogenase family 1 member A3
              Reactions:
              • an aldehyde + NAD(P)+ + H2O = an acid + NAD(P)H + H+ [RN:R00538 R00634]
              Gene Name: ALDH1A3
              Uniprot ID: P47895 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Aldehyde dehydrogenase, mitochondrial
              Reactions:
              • an aldehyde + NAD+ + H2O = an acid + NADH + H+ [RN:R00538]
              Gene Name: ALDH2
              Uniprot ID: P05091 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Fatty aldehyde dehydrogenase
              Reactions:
              • an aldehyde + NAD+ + H2O = an acid + NADH + H+ [RN:R00538]
              Gene Name: ALDH3A2
              Uniprot ID: P51648 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Aldehyde dehydrogenase X, mitochondrial
              Reactions:
              • an aldehyde + NAD+ + H2O = an acid + NADH + H+ [RN:R00538]
              Gene Name: ALDH1B1
              Uniprot ID: P30837 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Arginase-1
              Reactions:
              • L-arginine + H2O = L-ornithine + urea [RN:R00551]
              Gene Name: ARG1
              Uniprot ID: P05089 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Lipoprotein lipase
              Reactions:
              • triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
              Gene Name: LPL
              Uniprot ID: P06858 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Acyl-CoA desaturase
              Reactions:
              • stearoyl-CoA + 2 ferrocytochrome b5 + O2 + 2 H+ = oleoyl-CoA + 2 ferricytochrome b5 + 2 H2O [RN:R02222]
              Gene Name: SCD
              Uniprot ID: O00767 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Monoglyceride lipase
              Reactions:
              • Hydrolyses glycerol monoesters of long-chain fatty acids ALL_REAC (other) R01351 R01352 REFERENCE 1 [PMID:6776896] AUTHORS Mentlein R, Heiland S, Heymann E. TITLE Simultaneous purification and comparative characterization of six serine hydrolases from rat liver microsomes. JOURNAL Arch. Biochem. Biophys. 200 (1980) 547-59. ORGANISM Rattus norvegicus [GN:rno] REFERENCE 2 [PMID:5916497] AUTHORS Pope JL, McPherson JC, Tidwell HC. TITLE A study of a monoglyceride-hydrolyzing enzyme of intestinal mucosa. JOURNAL J. Biol. Chem. 241 (1966) 2306-10. ORGANISM Rattus norvegicus [GN:rno]
              Gene Name: MGLL
              Uniprot ID: Q99685 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Galactocerebrosidase
              Reactions:
              • D-galactosyl-N-acylsphingosine + H2O = D-galactose + N-acylsphingosine [RN:R03617]
              Gene Name: GALC
              Uniprot ID: P54803 Link_out
              Protein Sequence: FASTA
              Gene Sequence: FASTA
              Name: Arylsulfatase D
              Reactions:
                Gene Name: ARSD
                Uniprot ID: P51689 Link_out
                Protein Sequence: FASTA
                Gene Sequence: FASTA
                Name: Sialidase-2
                Reactions:
                • Hydrolysis of alpha-(2->3)-, alpha-(2->6)-, alpha-(2->8)- glycosidic linkages of terminal sialic acid residues in oligosaccharides, glycoproteins, glycolipids, colominic acid and synthetic substrates ALL_REAC (other) R03491 R04018 R04634 R04650 R05115 R05117 R05996(G) R05998(G) R05999(G) R06012(G) R06147(G) R06253(G) INHIBITOR 2-Deoxy-2,3-dehydro-N-acetylneuraminic acid [CPD:C04580]
                Gene Name: NEU2
                Uniprot ID: Q9Y3R4 Link_out
                Protein Sequence: FASTA
                Gene Sequence: FASTA
                Name: Arylsulfatase A
                Reactions:
                • a cerebroside 3-sulfate + H2O = a cerebroside + sulfate [RN:R04856 R06280]
                Gene Name: ARSA
                Uniprot ID: P15289 Link_out
                Protein Sequence: FASTA
                Gene Sequence: FASTA
                Name: Arylsulfatase B
                Reactions:
                • Hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate [RN:R07823] ALL_REAC R07823(G)
                Gene Name: ARSB
                Uniprot ID: P15848 Link_out
                Protein Sequence: FASTA
                Gene Sequence: FASTA
                Name: Sialidase-4
                Reactions:
                • Hydrolysis of alpha-(2->3)-, alpha-(2->6)-, alpha-(2->8)- glycosidic linkages of terminal sialic acid residues in oligosaccharides, glycoproteins, glycolipids, colominic acid and synthetic substrates ALL_REAC (other) R03491 R04018 R04634 R04650 R05115 R05117 R05996(G) R05998(G) R05999(G) R06012(G) R06147(G) R06253(G) INHIBITOR 2-Deoxy-2,3-dehydro-N-acetylneuraminic acid [CPD:C04580]
                Gene Name: NEU4
                Uniprot ID: Q8WWR8 Link_out
                Protein Sequence: FASTA
                Gene Sequence: FASTA
                Name: Arylsulfatase E
                Reactions:
                  Gene Name: ARSE
                  Uniprot ID: P51690 Link_out
                  Protein Sequence: FASTA
                  Gene Sequence: FASTA
                  Name: Kynureninase
                  Reactions:
                  • L-kynurenine + H2O = anthranilate + L-alanine [RN:R00987]
                  Gene Name: KYNU
                  Uniprot ID: Q16719 Link_out
                  Protein Sequence: FASTA
                  Gene Sequence: FASTA
                  Name: Annexin A3
                  Reactions:
                    Gene Name: ANXA3
                    Uniprot ID: P12429 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: 6-phosphogluconolactonase
                    Reactions:
                    • 6-phospho-D-glucono-1,5-lactone + H2O = 6-phospho-D-gluconate [RN:R02035]
                    Gene Name: PGLS
                    Uniprot ID: O95336 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: GDH/6PGL endoplasmic bifunctional protein
                    Reactions:
                    • 6-phospho-D-glucono-1,5-lactone + H2O = 6-phospho-D-gluconate [RN:R02035]
                    Gene Name: H6PD
                    Uniprot ID: O95479 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Trifunctional purine biosynthetic protein adenosine-3
                    Reactions:
                    • ATP + 5-phospho-D-ribosylamine + glycine = ADP + phosphate + N1-(5-phospho-D-ribosyl)glycinamide [RN:R04144]
                    Gene Name: GART
                    Uniprot ID: P22102 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Bifunctional UDP-N-acetylglucosamine 2-epimerase/N-acetylmannosamine kinase
                    Reactions:
                    • UDP-N-acetyl-D-glucosamine = UDP-N-acetyl-D-mannosamine [RN:R00420]
                    Gene Name: GNE
                    Uniprot ID: Q9Y223 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Sialic acid synthase
                    Reactions:
                    • phosphoenolpyruvate + N-acyl-D-mannosamine 6-phosphate + H2O = N-acylneuraminate 9-phosphate + phosphate [RN:R02769]
                    Gene Name: NANS
                    Uniprot ID: Q9NR45 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: 3'(2'),5'-bisphosphate nucleotidase 1
                    Reactions:
                    • adenosine 3',5'-bisphosphate + H2O = adenosine 5'-phosphate + phosphate [RN:R00188]
                    Gene Name: BPNT1
                    Uniprot ID: O95861 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Uroporphyrinogen-III synthase
                    Reactions:
                    • hydroxymethylbilane = uroporphyrinogen III + H2O [RN:R03165]
                    Gene Name: UROS
                    Uniprot ID: P10746 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Porphobilinogen deaminase
                    Reactions:
                    • 4 porphobilinogen + H2O = hydroxymethylbilane + 4 NH3 [RN:R00084]
                    Gene Name: HMBS
                    Uniprot ID: P08397 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Carbamoyl-phosphate synthase [ammonia], mitochondrial
                    Reactions:
                    • 2 ATP + NH3 + CO2 + H2O = 2 ADP + phosphate + carbamoyl phosphate [RN:R00149]
                    Gene Name: CPS1
                    Uniprot ID: P31327 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Type I inositol-1,4,5-trisphosphate 5-phosphatase
                    Reactions:
                    • (1) D-myo-inositol 1,4,5-trisphosphate + H2O = myo-inositol 1,4-bisphosphate + phosphate [RN:R03394]
                    • (2) 1D-myo-inositol 1,3,4,5-tetrakisphosphate + H2O = 1D-myo-inositol 1,3,4-trisphosphate + phosphate [RN:R03430]
                    Gene Name: INPP5A
                    Uniprot ID: Q14642 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Inositol polyphosphate 1-phosphatase
                    Reactions:
                    • 1D-myo-inositol 1,4-bisphosphate + H2O = 1D-myo-inositol 4-phosphate + phosphate [RN:R03393]
                    Gene Name: INPP1
                    Uniprot ID: P49441 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Phosphatidylinositol 4,5-bisphosphate 5-phosphatase A
                    Reactions:
                    • (1) D-myo-inositol 1,4,5-trisphosphate + H2O = myo-inositol 1,4-bisphosphate + phosphate [RN:R03394]
                    • (2) 1D-myo-inositol 1,3,4,5-tetrakisphosphate + H2O = 1D-myo-inositol 1,3,4-trisphosphate + phosphate [RN:R03430]
                    Gene Name: INPP5J
                    Uniprot ID: Q15735 Link_out
                    Protein Sequence: FASTA
                    Name: Inositol polyphosphate 5-phosphatase K
                    Reactions:
                    • (1) D-myo-inositol 1,4,5-trisphosphate + H2O = myo-inositol 1,4-bisphosphate + phosphate [RN:R03394]
                    • (2) 1D-myo-inositol 1,3,4,5-tetrakisphosphate + H2O = 1D-myo-inositol 1,3,4-trisphosphate + phosphate [RN:R03430]
                    Gene Name: INPP5K
                    Uniprot ID: Q9BT40 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Lactase-phlorizin hydrolase
                    Reactions:
                    • lactose + H2O = D-galactose + D-glucose [RN:R01100 R06114]
                    Gene Name: LCT
                    Uniprot ID: P09848 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Neutral alpha-glucosidase AB
                    Reactions:
                    • Hydrolysis of terminal (1->3)-alpha-D-glucosidic links in (1->3)-alpha-D-glucans ALL_REAC (other) R05980(G) R05981(G)
                    Gene Name: GANAB
                    Uniprot ID: Q14697 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Glycogen debranching enzyme
                    Reactions:
                    • Hydrolysis of (1->6)-alpha-D-glucosidic branch linkages in glycogen phosphorylase limit dextrin ALL_REAC (other) R02109 R06158(G)
                    Gene Name: AGL
                    Uniprot ID: P35573 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Trehalase
                    Reactions:
                    • alpha,alpha-trehalose + H2O = 2 D-glucose [RN:R00010 R06103]
                    Gene Name: TREH
                    Uniprot ID: O43280 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Glucose-6-phosphatase
                    Reactions:
                    • D-glucose 6-phosphate + H2O = D-glucose + phosphate [RN:R00303]
                    Gene Name: G6PC
                    Uniprot ID: P35575 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Peroxisomal bifunctional enzyme
                    Reactions:
                    • (3Z)-dodec-3-enoyl-CoA = (2E)-dodec-2-enoyl-CoA [RN:R04100]
                    Gene Name: EHHADH
                    Uniprot ID: Q08426 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: GDP-mannose 4,6 dehydratase
                    Reactions:
                    • GDP-mannose = GDP-4-dehydro-6-deoxy-D-mannose + H2O [RN:R00888]
                    Gene Name: GMDS
                    Uniprot ID: O60547 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Enoyl-CoA hydratase, mitochondrial
                    Reactions:
                    • (3S)-3-hydroxyacyl-CoA = trans-2(or 3)-enoyl-CoA + H2O [RN:R02685 R07314]
                    Gene Name: ECHS1
                    Uniprot ID: P30084 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Trifunctional enzyme subunit alpha, mitochondrial
                    Reactions:
                    • (3S)-3-hydroxyacyl-CoA = trans-2(or 3)-enoyl-CoA + H2O [RN:R02685 R07314]
                    Gene Name: HADHA
                    Uniprot ID: P40939 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Amiloride-sensitive amine oxidase [copper-containing]
                    Reactions:
                    • histamine + H2O + O2 = (imidazol-4-yl)acetaldehyde + NH3 + H2O2 [RN:R02150]
                    Gene Name: ABP1
                    Uniprot ID: P19801 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Membrane primary amine oxidase
                    Reactions:
                    • RCH2NH2 + H2O + O2 = RCHO + NH3 + H2O2 [RN:R01853]
                    Gene Name: AOC3
                    Uniprot ID: Q16853 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Retina-specific copper amine oxidase
                    Reactions:
                    • RCH2NH2 + H2O + O2 = RCHO + NH3 + H2O2 [RN:R01853]
                    Gene Name: AOC2
                    Uniprot ID: O75106 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Cytochrome P450 4A11
                    Reactions:
                    • octane + reduced rubredoxin + O2 = 1-octanol + oxidized rubredoxin + H2O [RN:R02879]
                    Gene Name: CYP4A11
                    Uniprot ID: Q02928 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: S-adenosylmethionine synthase isoform type-1
                    Reactions:
                    • ATP + L-methionine + H2O = phosphate + diphosphate + S-adenosyl-L-methionine [RN:R00177]
                    Gene Name: MAT1A
                    Uniprot ID: Q00266 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Inosine triphosphate pyrophosphatase
                    Reactions:
                    • a nucleoside triphosphate + H2O = a nucleotide + diphosphate [RN:R01532]
                    Gene Name: ITPA
                    Uniprot ID: Q9BY32 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Deoxyuridine 5'-triphosphate nucleotidohydrolase, mitochondrial
                    Reactions:
                    • dUTP + H2O = dUMP + diphosphate [RN:R02100]
                    Gene Name: DUT
                    Uniprot ID: P33316 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Alpha-N-acetylgalactosaminidase
                    Reactions:
                    • Hydrolysis of terminal non-reducing N-acetyl-D-galactosamine residues in N-acetyl-alpha-D-galactosaminides ALL_REAC (other) R04183 R05966(G)
                    Gene Name: NAGA
                    Uniprot ID: P17050 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Cytochrome P450 11B1, mitochondrial
                    Reactions:
                    • a steroid + reduced adrenal ferredoxin + O2 = an 11beta-hydroxysteroid + oxidized adrenal ferredoxin + H2O [RN:R02726]
                    Gene Name: CYP11B1
                    Uniprot ID: P15538 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Aminopeptidase N
                    Reactions:
                    • Release of an N-terminal amino acid, Xaa!Yaa- from a peptide, amide or arylamide. Xaa is preferably Ala, but may be most amino acids including Pro (slow action). When a terminal hydrophobic residue is followed by a prolyl residue, the two may be released as an intact Xaa-Pro dipeptide ALL_REAC (other) R00899 R04951 COFACTOR Manganese [CPD:C00034]
                    • Zinc [CPD:C00038]
                    Gene Name: ANPEP
                    Uniprot ID: P15144 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Procollagen-lysine,2-oxoglutarate 5-dioxygenase 1
                    Reactions:
                    • L-lysine-[procollagen] + 2-oxoglutarate + O2 = (2S,5R)- 5-hydroxy-L-lysine-[procollagen] + succinate + CO2
                    Gene Name: PLOD1
                    Uniprot ID: Q02809 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Procollagen-lysine,2-oxoglutarate 5-dioxygenase 2
                    Reactions:
                    • L-lysine-[procollagen] + 2-oxoglutarate + O2 = (2S,5R)- 5-hydroxy-L-lysine-[procollagen] + succinate + CO2
                    Gene Name: PLOD2
                    Uniprot ID: O00469 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Procollagen-lysine,2-oxoglutarate 5-dioxygenase 3
                    Reactions:
                    • L-lysine-[procollagen] + 2-oxoglutarate + O2 = (2S,5R)- 5-hydroxy-L-lysine-[procollagen] + succinate + CO2
                    Gene Name: PLOD3
                    Uniprot ID: O60568 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Tryptophan 5-hydroxylase 1
                    Reactions:
                    • L-tryptophan + tetrahydrobiopterin + O2 = 5-hydroxy-L-tryptophan + 4a-hydroxytetrahydrobiopterin [RN:R07213]
                    Gene Name: TPH1
                    Uniprot ID: P17752 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Ferritin, mitochondrial
                    Reactions:
                    • 4 Fe(II) + 4 H+ + O2 = 4 Fe(III) + 2 H2O [RN:R00078]
                    Gene Name: FTMT
                    Uniprot ID: Q8N4E7 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Tryptophan 5-hydroxylase 2
                    Reactions:
                    • L-tryptophan + tetrahydrobiopterin + O2 = 5-hydroxy-L-tryptophan + 4a-hydroxytetrahydrobiopterin [RN:R07213]
                    Gene Name: TPH2
                    Uniprot ID: Q8IWU9 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Beta-Ala-His dipeptidase
                    Reactions:
                    • Preferential hydrolysis of the beta-Ala!His dipeptide (carnosine), and also anserine, Xaa!His dipeptides and other dipeptides including homocarnosine [RN:R01166 R03288] ALL_REAC R01166 R03288 COFACTOR Citrate [CPD:C00158]
                    • Cadmium [CPD:C01413]
                    Gene Name: CNDP1
                    Uniprot ID: Q96KN2 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Peroxisomal multifunctional enzyme type 2
                    Reactions:
                    • (24R,25R)-3alpha,7alpha,12alpha,24-tetrahydroxy-5beta-cholestanoyl- CoA = (24E)-3alpha,7alpha,12alpha-trihydroxy-5beta-cholest-24-enoyl-CoA + H2O [RN:R04813]
                    Gene Name: HSD17B4
                    Uniprot ID: P51659 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Steryl-sulfatase
                    Reactions:
                    • 3beta-hydroxyandrost-5-en-17-one 3-sulfate + H2O = 3beta-hydroxyandrost-5-en-17-one + sulfate [RN:R03404]
                    Gene Name: STS
                    Uniprot ID: P08842 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Liver carboxylesterase 1
                    Reactions:
                    • a carboxylic ester + H2O = an alcohol + a carboxylate [RN:R00630]
                    Gene Name: CES1
                    Uniprot ID: P23141 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Carboxylesterase 2
                    Reactions:
                    • a carboxylic ester + H2O = an alcohol + a carboxylate [RN:R00630]
                    Gene Name: CES2
                    Uniprot ID: O00748 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Cholesterol 7-alpha-monooxygenase
                    Reactions:
                    • cholesterol + NADPH + H+ + O2 = 7alpha-hydroxycholesterol + NADP+ + H2O [RN:R01463]
                    Gene Name: CYP7A1
                    Uniprot ID: P22680 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Acetylcholinesterase
                    Reactions:
                    • acetylcholine + H2O = choline + acetate [RN:R01026]
                    Gene Name: ACHE
                    Uniprot ID: P22303 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Cholinesterase
                    Reactions:
                    • an acylcholine + H2O = choline + a carboxylate [RN:R01029]
                    Gene Name: BCHE
                    Uniprot ID: P06276 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Peptidyl-tRNA hydrolase 2, mitochondrial
                    Reactions:
                    • N-Substituted aminoacyl-tRNA + H2O = N-substituted amino acid + tRNA [RN:R04238]
                    Gene Name: PTRH2
                    Uniprot ID: Q9Y3E5 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Platelet-activating factor acetylhydrolase IB subunit gamma
                    Reactions:
                    • 1-alkyl-2-acetyl-sn-glycero-3-phosphocholine + H2O = 1-alkyl-sn-glycero-3-phosphocholine + acetate [RN:R04452]
                    Gene Name: PAFAH1B3
                    Uniprot ID: Q15102 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Platelet-activating factor acetylhydrolase IB subunit beta
                    Reactions:
                    • 1-alkyl-2-acetyl-sn-glycero-3-phosphocholine + H2O = 1-alkyl-sn-glycero-3-phosphocholine + acetate [RN:R04452]
                    Gene Name: PAFAH1B2
                    Uniprot ID: P68402 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Hormone-sensitive lipase
                    Reactions:
                    • (1) diacylglycerol + H2O = monoacylglycerol + a carboxylate [RN:R05209]
                    • (2) triacylglycerol + H2O = diacylglycerol + a carboxylate [RN:R01369]
                    • (3) monoacylglycerol + H2O = glycerol + a carboxylate [RN:R07293]
                    Gene Name: LIPE
                    Uniprot ID: Q05469 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Group 3 secretory phospholipase A2
                    Reactions:
                    • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
                    Gene Name: PLA2G3
                    Uniprot ID: Q9NZ20 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Platelet-activating factor acetylhydrolase 2, cytoplasmic
                    Reactions:
                    • 1-alkyl-2-acetyl-sn-glycero-3-phosphocholine + H2O = 1-alkyl-sn-glycero-3-phosphocholine + acetate [RN:R04452]
                    Gene Name: PAFAH2
                    Uniprot ID: Q99487 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Sialate O-acetylesterase
                    Reactions:
                    • N-acetyl-O-acetylneuraminate + H2O = N-acetylneuraminate + acetate [RN:R01810]
                    Gene Name: SIAE
                    Uniprot ID: Q9HAT2 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Acyloxyacyl hydrolase
                    Reactions:
                    • 3-(acyloxy)acyl group of bacterial toxin = 3-hydroxyacyl group of bacterial toxin + a fatty acid [RN:R05792]
                    Gene Name: AOAH
                    Uniprot ID: P28039 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Cystathionine gamma-lyase
                    Reactions:
                    • (1) L-cystathionine + H2O = L-cysteine + NH3 + 2-oxobutanoate (overall reaction) [RN:R01001]
                    • (2) (1a) L-cystathionine = L-cysteine + 2-ammoniobut-2-enoate [RN:R08632]
                    • (3) (1b) 2-ammoniobut-2-enoate + H2O = 2-oxobutanoate + NH3 (spontaneous) [RN:R08637]
                    Gene Name: CTH
                    Uniprot ID: P32929 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Aldehyde dehydrogenase family 3 member B2
                    Reactions:
                    • an aldehyde + NAD(P)+ + H2O = an acid + NAD(P)H + H+ [RN:R00538 R00634]
                    Gene Name: ALDH3B2
                    Uniprot ID: P48448 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Aldehyde dehydrogenase family 3 member B1
                    Reactions:
                    • an aldehyde + NAD(P)+ + H2O = an acid + NAD(P)H + H+ [RN:R00538 R00634]
                    Gene Name: ALDH3B1
                    Uniprot ID: P43353 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Dihydropyrimidinase
                    Reactions:
                    • 5,6-dihydrouracil + H2O = 3-ureidopropanoate [RN:R02269]
                    Gene Name: DPYS
                    Uniprot ID: Q14117 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Beta-ureidopropionase
                    Reactions:
                    • N-carbamoyl-beta-alanine + H2O = beta-alanine + CO2 + NH3 [RN:R00905]
                    Gene Name: UPB1
                    Uniprot ID: Q9UBR1 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Biotinidase
                    Reactions:
                    • biotin amide + H2O = biotin + NH3 [RN:R01076]
                    Gene Name: BTD
                    Uniprot ID: P43251 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Bile acid-CoA:amino acid N-acyltransferase
                    Reactions:
                    • palmitoyl-CoA + H2O = CoA + palmitate [RN:R01274]
                    Gene Name: BAAT
                    Uniprot ID: Q14032 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Acylphosphatase-2
                    Reactions:
                    • an acylphosphate + H2O = a carboxylate + phosphate [RN:R00539]
                    Gene Name: ACYP2
                    Uniprot ID: P14621 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Acylphosphatase-1
                    Reactions:
                    • an acylphosphate + H2O = a carboxylate + phosphate [RN:R00539]
                    Gene Name: ACYP1
                    Uniprot ID: P07311 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Aminoacylase-1
                    Reactions:
                    • an N-acyl-L-amino acid + H2O = a carboxylate + an L-amino acid [RN:R01263]
                    Gene Name: ACY1
                    Uniprot ID: Q03154 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Aspartoacylase
                    Reactions:
                    • N-acyl-L-aspartate + H2O = a carboxylate + L-aspartate [RN:R00546]
                    Gene Name: ASPA
                    Uniprot ID: P45381 Link_out
                    Protein Sequence: FASTA
                    Gene Sequence: FASTA
                    Name: Platelet-activating factor acetylhydrolase IB subunit alpha
                    Reactions:
                      Gene Name: PAFAH1B1
                      Uniprot ID: P43034 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Aspartoacylase-2
                      Reactions:
                      • --- []
                      Gene Name: ACY3
                      Uniprot ID: Q96HD9 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Retinal cone rhodopsin-sensitive cGMP 3',5'-cyclic phosphodiesterase subunit gamma
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE6H
                      Uniprot ID: Q13956 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Calcium/calmodulin-dependent 3',5'-cyclic nucleotide phosphodiesterase 1A
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE1A
                      Uniprot ID: P54750 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: High affinity cAMP-specific and IBMX-insensitive 3',5'-cyclic phosphodiesterase 8A
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE8A
                      Uniprot ID: O60658 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Calcium/calmodulin-dependent 3',5'-cyclic nucleotide phosphodiesterase 1B
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE1B
                      Uniprot ID: Q01064 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cGMP-inhibited 3',5'-cyclic phosphodiesterase B
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE3B
                      Uniprot ID: Q13370 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Cone cGMP-specific 3',5'-cyclic phosphodiesterase subunit alpha'
                      Reactions:
                      • guanosine 3',5'-cyclic phosphate + H2O = guanosine 5'-phosphate [RN:R01234]
                      Gene Name: PDE6C
                      Uniprot ID: P51160 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Asparagine synthetase [glutamine-hydrolyzing]
                      Reactions:
                      • (1) ATP + L-aspartate + L-glutamine + H2O = AMP + diphosphate + L-asparagine + L-glutamate [RN:R00578]
                      • (2) (1a) L-glutamine + H2O = L-glutamate + NH3 [RN:R00256]
                      • (3) (1b) ATP + L-aspartate + NH3 = AMP + diphosphate + L-asparagine [RN:R00483]
                      Gene Name: ASNS
                      Uniprot ID: P08243 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: AMP deaminase 3
                      Reactions:
                      • AMP + H2O = IMP + NH3 [RN:R00181]
                      Gene Name: AMPD3
                      Uniprot ID: Q01432 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: AMP deaminase 2
                      Reactions:
                      • AMP + H2O = IMP + NH3 [RN:R00181]
                      Gene Name: AMPD2
                      Uniprot ID: Q01433 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cGMP-inhibited 3',5'-cyclic phosphodiesterase A
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE3A
                      Uniprot ID: Q14432 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cAMP and cAMP-inhibited cGMP 3',5'-cyclic phosphodiesterase 10A
                      Reactions:
                      • guanosine 3',5'-cyclic phosphate + H2O = guanosine 5'-phosphate [RN:R01234]
                      Gene Name: PDE10A
                      Uniprot ID: Q9Y233 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Calcium/calmodulin-dependent 3',5'-cyclic nucleotide phosphodiesterase 1C
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE1C
                      Uniprot ID: Q14123 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cAMP-specific 3',5'-cyclic phosphodiesterase 4B
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE4B
                      Uniprot ID: Q07343 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cAMP-specific 3',5'-cyclic phosphodiesterase 7B
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE7B
                      Uniprot ID: Q9NP56 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Bis(5'-adenosyl)-triphosphatase
                      Reactions:
                      • P1,P3-bis(5'-adenosyl) triphosphate + H2O = ADP + AMP [RN:R00187]
                      Gene Name: FHIT
                      Uniprot ID: P49789 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: High affinity cGMP-specific 3',5'-cyclic phosphodiesterase 9A
                      Reactions:
                      • guanosine 3',5'-cyclic phosphate + H2O = guanosine 5'-phosphate [RN:R01234]
                      Gene Name: PDE9A
                      Uniprot ID: O76083 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cGMP-dependent 3',5'-cyclic phosphodiesterase
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE2A
                      Uniprot ID: O00408 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Bis(5'-nucleosyl)-tetraphosphatase [asymmetrical]
                      Reactions:
                      • P1,P4-bis(5'-guanosyl) tetraphosphate + H2O = GTP + GMP [RN:R01232]
                      Gene Name: NUDT2
                      Uniprot ID: P50583 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Rod cGMP-specific 3',5'-cyclic phosphodiesterase subunit alpha
                      Reactions:
                      • guanosine 3',5'-cyclic phosphate + H2O = guanosine 5'-phosphate [RN:R01234]
                      Gene Name: PDE6A
                      Uniprot ID: P16499 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: ADP-sugar pyrophosphatase
                      Reactions:
                      • ADP-ribose + H2O = AMP + D-ribose 5-phosphate [RN:R01054]
                      Gene Name: NUDT5
                      Uniprot ID: Q9UKK9 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: High affinity cAMP-specific and IBMX-insensitive 3',5'-cyclic phosphodiesterase 8B
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE8B
                      Uniprot ID: O95263 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cAMP-specific 3',5'-cyclic phosphodiesterase 4C
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE4C
                      Uniprot ID: Q08493 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Rod cGMP-specific 3',5'-cyclic phosphodiesterase subunit beta
                      Reactions:
                      • guanosine 3',5'-cyclic phosphate + H2O = guanosine 5'-phosphate [RN:R01234]
                      Gene Name: PDE6B
                      Uniprot ID: P35913 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: cAMP-specific 3',5'-cyclic phosphodiesterase 4D
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE4D
                      Uniprot ID: Q08499 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Retinal rod rhodopsin-sensitive cGMP 3',5'-cyclic phosphodiesterase subunit gamma
                      Reactions:
                      • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                      Gene Name: PDE6G
                      Uniprot ID: P18545 Link_out
                      Protein Sequence: FASTA
                      Gene Sequence: FASTA
                      Name: Retinal rod rhodopsin-sensitive cGMP 3',5'-cyclic phosphodiesterase subunit delta
                      Reactions:
                        Gene Name: PDE6D
                        Uniprot ID: O43924 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: cAMP-specific 3',5'-cyclic phosphodiesterase 4A
                        Reactions:
                        • nucleoside 3',5'-cyclic phosphate + H2O = nucleoside 5'-phosphate [RN:R03259]
                        Gene Name: PDE4A
                        Uniprot ID: P27815 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Selenide, water dikinase 1
                        Reactions:
                        • ATP + selenide + H2O = AMP + selenophosphate + phosphate [RN:R03595]
                        Gene Name: SEPHS1
                        Uniprot ID: P49903 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: cGMP-specific 3',5'-cyclic phosphodiesterase
                        Reactions:
                        • guanosine 3',5'-cyclic phosphate + H2O = guanosine 5'-phosphate [RN:R01234]
                        Gene Name: PDE5A
                        Uniprot ID: O76074 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: AMP deaminase 1
                        Reactions:
                        • AMP + H2O = IMP + NH3 [RN:R00181]
                        Gene Name: AMPD1
                        Uniprot ID: P23109 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Selenide, water dikinase 2
                        Reactions:
                        • ATP + selenide + H2O = AMP + selenophosphate + phosphate [RN:R03595]
                        Gene Name: SEPHS2
                        Uniprot ID: Q99611 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Putative adenosylhomocysteinase 3
                        Reactions:
                        • S-adenosyl-L-homocysteine + H2O = L-homocysteine + adenosine [RN:R00192]
                        Gene Name: AHCYL2
                        Uniprot ID: Q96HN2 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Adenosylhomocysteinase
                        Reactions:
                        • S-adenosyl-L-homocysteine + H2O = L-homocysteine + adenosine [RN:R00192]
                        Gene Name: AHCY
                        Uniprot ID: P23526 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Putative adenosylhomocysteinase 2
                        Reactions:
                        • S-adenosyl-L-homocysteine + H2O = L-homocysteine + adenosine [RN:R00192]
                        Gene Name: AHCYL1
                        Uniprot ID: O43865 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Adenosine deaminase
                        Reactions:
                        • adenosine + H2O = inosine + NH3 [RN:R01560]
                        Gene Name: ADA
                        Uniprot ID: P00813 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutamate dehydrogenase 2, mitochondrial
                        Reactions:
                        • L-glutamate + H2O + NAD(P)+ = 2-oxoglutarate + NH3 + NAD(P)H + H+ [RN:R00243 R00248]
                        Gene Name: GLUD2
                        Uniprot ID: P49448 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Protein-arginine deiminase type-6
                        Reactions:
                        • protein L-arginine + H2O = protein L-citrulline + NH3 [RN:R02621]
                        Gene Name: PADI6
                        Uniprot ID: Q6TGC4 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: L-serine dehydratase/L-threonine deaminase
                        Reactions:
                        • L-threonine = 2-oxobutanoate + NH3 [RN:R00996]
                        Gene Name: SDS
                        Uniprot ID: P20132 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Protein-arginine deiminase type-4
                        Reactions:
                        • protein L-arginine + H2O = protein L-citrulline + NH3 [RN:R02621]
                        Gene Name: PADI4
                        Uniprot ID: Q9UM07 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Pyridoxine-5'-phosphate oxidase
                        Reactions:
                        • (1) pyridoxamine 5'-phosphate + H2O + O2 = pyridoxal 5'-phosphate + NH3 + H2O2 [RN:R00277]
                        • (2) pyridoxine 5'-phosphate + O2 = pyridoxal 5'-phosphate + H2O2 [RN:R00278]
                        Gene Name: PNPO
                        Uniprot ID: Q9NVS9 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutaminase liver isoform, mitochondrial
                        Reactions:
                        • L-glutamine + H2O = L-glutamate + NH3 [RN:R00256]
                        Gene Name: GLS2
                        Uniprot ID: Q9UI32 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: CTP synthase 1
                        Reactions:
                        • ATP + UTP + NH3 = ADP + phosphate + CTP [RN:R00571]
                        Gene Name: CTPS
                        Uniprot ID: P17812 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Protein-arginine deiminase type-3
                        Reactions:
                        • protein L-arginine + H2O = protein L-citrulline + NH3 [RN:R02621]
                        Gene Name: PADI3
                        Uniprot ID: Q9ULW8 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutaminase kidney isoform, mitochondrial
                        Reactions:
                        • L-glutamine + H2O = L-glutamate + NH3 [RN:R00256]
                        Gene Name: GLS
                        Uniprot ID: O94925 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Protein-arginine deiminase type-2
                        Reactions:
                        • protein L-arginine + H2O = protein L-citrulline + NH3 [RN:R02621]
                        Gene Name: PADI2
                        Uniprot ID: Q9Y2J8 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Protein-arginine deiminase type-1
                        Reactions:
                        • protein L-arginine + H2O = protein L-citrulline + NH3 [RN:R02621]
                        Gene Name: PADI1
                        Uniprot ID: Q9ULC6 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Aminomethyltransferase, mitochondrial
                        Reactions:
                        • [protein]-S8-aminomethyldihydrolipoyllysine + tetrahydrofolate = [protein]-dihydrolipoyllysine + 5,10-methylenetetrahydrofolate + NH3 [RN:R04125]
                        Gene Name: AMT
                        Uniprot ID: P48728 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Guanine deaminase
                        Reactions:
                        • guanine + H2O = xanthine + NH3 [RN:R01676]
                        Gene Name: GDA
                        Uniprot ID: Q9Y2T3 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutamate dehydrogenase 1, mitochondrial
                        Reactions:
                        • L-glutamate + H2O + NAD(P)+ = 2-oxoglutarate + NH3 + NAD(P)H + H+ [RN:R00243 R00248]
                        Gene Name: GLUD1
                        Uniprot ID: P00367 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Protein-lysine 6-oxidase
                        Reactions:
                        • peptidyl-L-lysyl-peptide + O2 + H2O = peptidyl-allysyl-peptide + NH3 + H2O2 [RN:R04239]
                        Gene Name: LOX
                        Uniprot ID: P28300 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Fumarylacetoacetase
                        Reactions:
                        • 4-fumarylacetoacetate + H2O = acetoacetate + fumarate [RN:R01364]
                        Gene Name: FAH
                        Uniprot ID: P16930 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alpha-galactosidase A
                        Reactions:
                        • Hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids ALL_REAC (other) R01101 R01103 R01104 R01194 R01329 R02926 R03618 R03634 R04019 R04470 R05549 R05961(G) R06070(G) R06091(G) R06093(G) R06094(G) R06096(G) R06142(G) R06152(G)
                        Gene Name: GLA
                        Uniprot ID: P06280 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cholesterol side-chain cleavage enzyme, mitochondrial
                        Reactions:
                        • cholesterol + reduced adrenal ferredoxin + O2 = pregnenolone + 4-methylpentanal + oxidized adrenal ferredoxin + H2O [RN:R02724]
                        Gene Name: CYP11A1
                        Uniprot ID: P05108 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Aconitate hydratase, mitochondrial
                        Reactions:
                        • (1) citrate = isocitrate [RN:R01324]
                        • (2) (1a) citrate = cis-aconitate + H2O [RN:R01325]
                        • (3) (1b) cis-aconitate + H2O = isocitrate [RN:R01900]
                        Gene Name: ACO2
                        Uniprot ID: Q99798 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cytoplasmic aconitate hydratase
                        Reactions:
                        • (1) citrate = isocitrate [RN:R01324]
                        • (2) (1a) citrate = cis-aconitate + H2O [RN:R01325]
                        • (3) (1b) cis-aconitate + H2O = isocitrate [RN:R01900]
                        Gene Name: ACO1
                        Uniprot ID: P21399 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Gamma-glutamyltranspeptidase 1
                        Reactions:
                        • (5-L-glutamyl)-peptide + an amino acid = peptide + 5-L-glutamyl amino acid [RN:R04159]
                        Gene Name: GGT1
                        Uniprot ID: P19440 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: N(G),N(G)-dimethylarginine dimethylaminohydrolase 2
                        Reactions:
                        • Nomega,Nomega'-dimethyl-L-arginine + H2O = dimethylamine + L-citrulline [RN:R02513]
                        Gene Name: DDAH2
                        Uniprot ID: O95865 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Sphingomyelin phosphodiesterase
                        Reactions:
                        • sphingomyelin + H2O = N-acylsphingosine + choline phosphate [RN:R02541]
                        Gene Name: SMPD1
                        Uniprot ID: P17405 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cystathionine beta-synthase
                        Reactions:
                        • L-serine + L-homocysteine = L-cystathionine + H2O [RN:R01290]
                        Gene Name: CBS
                        Uniprot ID: P35520 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alcohol dehydrogenase class-3
                        Reactions:
                        • S-(hydroxymethyl)glutathione + NAD(P)+ = S-formylglutathione + NAD(P)H + H+ [RN:R06983 R07140]
                        Gene Name: ADH5
                        Uniprot ID: P11766 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alcohol dehydrogenase 1B
                        Reactions:
                        • an alcohol + NAD+ = an aldehyde or ketone + NADH + H+ [RN:R07326 R07327]
                        Gene Name: ADH1B
                        Uniprot ID: P00325 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alcohol dehydrogenase class 4 mu/sigma chain
                        Reactions:
                        • an alcohol + NAD+ = an aldehyde or ketone + NADH + H+ [RN:R07326 R07327]
                        Gene Name: ADH7
                        Uniprot ID: P40394 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alcohol dehydrogenase 1A
                        Reactions:
                        • an alcohol + NAD+ = an aldehyde or ketone + NADH + H+ [RN:R07326 R07327]
                        Gene Name: ADH1A
                        Uniprot ID: P07327 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alcohol dehydrogenase 6
                        Reactions:
                        • an alcohol + NAD+ = an aldehyde or ketone + NADH + H+ [RN:R07326 R07327]
                        Gene Name: ADH6
                        Uniprot ID: P28332 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alcohol dehydrogenase 1C
                        Reactions:
                        • an alcohol + NAD+ = an aldehyde or ketone + NADH + H+ [RN:R07326 R07327]
                        Gene Name: ADH1C
                        Uniprot ID: P00326 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Serine hydroxymethyltransferase, mitochondrial
                        Reactions:
                        • 5,10-methylenetetrahydrofolate + glycine + H2O = tetrahydrofolate + L-serine [RN:R00945]
                        Gene Name: SHMT2
                        Uniprot ID: P34897 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Sarcosine dehydrogenase, mitochondrial
                        Reactions:
                        • sarcosine + acceptor + H2O = glycine + formaldehyde + reduced acceptor [RN:R00611]
                        Gene Name: SARDH
                        Uniprot ID: Q9UL12 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Serine hydroxymethyltransferase, cytosolic
                        Reactions:
                        • 5,10-methylenetetrahydrofolate + glycine + H2O = tetrahydrofolate + L-serine [RN:R00945]
                        Gene Name: SHMT1
                        Uniprot ID: P34896 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 3
                        Reactions:
                        • beta-D-fructose 2,6-bisphosphate + H2O = D-fructose 6-phosphate + phosphate [RN:R00763]
                        Gene Name: PFKFB3
                        Uniprot ID: Q16875 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 4
                        Reactions:
                        • beta-D-fructose 2,6-bisphosphate + H2O = D-fructose 6-phosphate + phosphate [RN:R00763]
                        Gene Name: PFKFB4
                        Uniprot ID: Q16877 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 1
                        Reactions:
                        • beta-D-fructose 2,6-bisphosphate + H2O = D-fructose 6-phosphate + phosphate [RN:R00763]
                        Gene Name: PFKFB1
                        Uniprot ID: P16118 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Fructose-1,6-bisphosphatase isozyme 2
                        Reactions:
                        • D-fructose 1,6-bisphosphate + H2O = D-fructose 6-phosphate + phosphate [RN:R00762]
                        Gene Name: FBP2
                        Uniprot ID: O00757 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Fructose-1,6-bisphosphatase 1
                        Reactions:
                        • D-fructose 1,6-bisphosphate + H2O = D-fructose 6-phosphate + phosphate [RN:R00762]
                        Gene Name: FBP1
                        Uniprot ID: P09467 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 6-phosphofructo-2-kinase/fructose-2,6-biphosphatase 2
                        Reactions:
                        • beta-D-fructose 2,6-bisphosphate + H2O = D-fructose 6-phosphate + phosphate [RN:R00763]
                        Gene Name: PFKFB2
                        Uniprot ID: O60825 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase Mu 2
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTM2
                        Uniprot ID: P28161 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione peroxidase 7
                        Reactions:
                        • 2 glutathione + H2O2 = glutathione disulfide + 2 H2O [RN:R00274]
                        Gene Name: GPX7
                        Uniprot ID: Q96SL4 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Epididymal secretory glutathione peroxidase
                        Reactions:
                        • 2 glutathione + H2O2 = glutathione disulfide + 2 H2O [RN:R00274]
                        Gene Name: GPX5
                        Uniprot ID: O75715 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase Mu 1
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTM1
                        Uniprot ID: P09488 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Hydroxyacylglutathione hydrolase, mitochondrial
                        Reactions:
                        • S-(2-hydroxyacyl)glutathione + H2O = glutathione + a 2-hydroxy carboxylate [RN:R04090]
                        Gene Name: HAGH
                        Uniprot ID: Q16775 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Microsomal glutathione S-transferase 3
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: MGST3
                        Uniprot ID: O14880 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase Mu 3
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTM3
                        Uniprot ID: P21266 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase A1
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTA1
                        Uniprot ID: P08263 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Maleylacetoacetate isomerase
                        Reactions:
                        • 4-maleylacetoacetate = 4-fumarylacetoacetate [RN:R03181]
                        Gene Name: GSTZ1
                        Uniprot ID: O43708 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase Mu 5
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTM5
                        Uniprot ID: P46439 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Microsomal glutathione S-transferase 2
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: MGST2
                        Uniprot ID: Q99735 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase omega-1
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTO1
                        Uniprot ID: P78417 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase A5
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTA5
                        Uniprot ID: Q7RTV2 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase A2
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTA2
                        Uniprot ID: P09210 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione peroxidase 6
                        Reactions:
                        • 2 glutathione + H2O2 = glutathione disulfide + 2 H2O [RN:R00274]
                        Gene Name: GPX6
                        Uniprot ID: P59796 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase A3
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTA3
                        Uniprot ID: Q16772 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase A4
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTA4
                        Uniprot ID: O15217 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione peroxidase 1
                        Reactions:
                        • 2 glutathione + H2O2 = glutathione disulfide + 2 H2O [RN:R00274]
                        Gene Name: GPX1
                        Uniprot ID: P07203 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Phospholipid hydroperoxide glutathione peroxidase, mitochondrial
                        Reactions:
                        • 2 glutathione + a lipid hydroperoxide = glutathione disulfide + lipid + 2 H2O [RN:R03167]
                        Gene Name: GPX4
                        Uniprot ID: P36969 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione peroxidase 3
                        Reactions:
                        • 2 glutathione + H2O2 = glutathione disulfide + 2 H2O [RN:R00274]
                        Gene Name: GPX3
                        Uniprot ID: P22352 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase omega-2
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTO2
                        Uniprot ID: Q9H4Y5 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase theta-1
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTT1
                        Uniprot ID: P30711 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione peroxidase 2
                        Reactions:
                        • 2 glutathione + H2O2 = glutathione disulfide + 2 H2O [RN:R00274]
                        Gene Name: GPX2
                        Uniprot ID: P18283 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Glutathione S-transferase P
                        Reactions:
                        • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                        Gene Name: GSTP1
                        Uniprot ID: P09211 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Beta-glucuronidase
                        Reactions:
                        • a beta-D-glucuronoside + H2O = D-glucuronate + an alcohol [RN:R01478]
                        Gene Name: GUSB
                        Uniprot ID: P08236 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Inositol oxygenase
                        Reactions:
                        • myo-inositol + O2 = D-glucuronate + H2O [RN:R01184]
                        Gene Name: MIOX
                        Uniprot ID: Q9UGB7 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Beta-galactosidase
                        Reactions:
                        • Hydrolysis of terminal non-reducing beta-D-galactose residues in beta-D-galactosides ALL_REAC (other) R01100 R01105 R01678 R03355 R04633 R04783 R05112 R05994(G) R06010(G) R06098(G) R06099(G) R06114(G) R06144(G) R06202(G) R07807(G)
                        Gene Name: GLB1
                        Uniprot ID: P16278 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 3-keto-steroid reductase
                        Reactions:
                        • 4alpha-methyl-5alpha-cholest-7-en-3beta-ol + NADP+ = 4alpha-methyl-5alpha-cholest-7-en-3-one + NADPH + H+ [RN:R05691]
                        Gene Name: HSD17B7
                        Uniprot ID: P56937 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 5-oxoprolinase
                        Reactions:
                        • ATP + 5-oxo-L-proline + 2 H2O = ADP + phosphate + L-glutamate [RN:R00251]
                        Gene Name: OPLAH
                        Uniprot ID: O14841 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Inositol monophosphatase 1
                        Reactions:
                        • myo-inositol phosphate + H2O = myo-inositol + phosphate [RN:R07343]
                        Gene Name: IMPA1
                        Uniprot ID: P29218 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cytosol aminopeptidase
                        Reactions:
                        • Release of N-terminal proline from a peptide ALL_REAC (other) R00135 COFACTOR Manganese [CPD:C00034]
                        Gene Name: LAP3
                        Uniprot ID: P28838 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alpha-mannosidase 2
                        Reactions:
                        • Hydrolysis of the terminal (1->3)- and (1->6)-linked alpha-D-mannose residues in the mannosyl-oligosaccharide Man5(GlcNAc)3 ALL_REAC (other) R05984(G)
                        Gene Name: MAN2A1
                        Uniprot ID: Q16706 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Mannosyl-oligosaccharide 1,2-alpha-mannosidase IB
                        Reactions:
                        • Hydrolysis of the terminal (1->2)-linked alpha-D-mannose residues in the oligo-mannose oligosaccharide Man9(GlcNAc)2 ALL_REAC (other) R05982(G) R06722(G)
                        Gene Name: MAN1A2
                        Uniprot ID: O60476 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Endoplasmic reticulum mannosyl-oligosaccharide 1,2-alpha-mannosidase
                        Reactions:
                        • Hydrolysis of the terminal (1->2)-linked alpha-D-mannose residues in the oligo-mannose oligosaccharide Man9(GlcNAc)2 ALL_REAC (other) R05982(G) R06722(G)
                        Gene Name: MAN1B1
                        Uniprot ID: Q9UKM7 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Mannosyl-oligosaccharide 1,2-alpha-mannosidase IA
                        Reactions:
                        • Hydrolysis of the terminal (1->2)-linked alpha-D-mannose residues in the oligo-mannose oligosaccharide Man9(GlcNAc)2 ALL_REAC (other) R05982(G) R06722(G)
                        Gene Name: MAN1A1
                        Uniprot ID: P33908 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Beta-hexosaminidase subunit beta
                        Reactions:
                        • Hydrolysis of terminal non-reducing N-acetyl-D-hexosamine residues in N-acetyl-beta-D-hexosaminides ALL_REAC (other) R00022 R03492 R04184 R04586 R05963(G) R06001(G) R06004(G) R06141(G) R07809(G) R07810(G)
                        Gene Name: HEXB
                        Uniprot ID: P07686 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Beta-hexosaminidase subunit alpha
                        Reactions:
                        • Hydrolysis of terminal non-reducing N-acetyl-D-hexosamine residues in N-acetyl-beta-D-hexosaminides ALL_REAC (other) R00022 R03492 R04184 R04586 R05963(G) R06001(G) R06004(G) R06141(G) R07809(G) R07810(G)
                        Gene Name: HEXA
                        Uniprot ID: P06865 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Tissue alpha-L-fucosidase
                        Reactions:
                        • an alpha-L-fucoside + H2O = L-fucose + an alcohol [RN:R03162]
                        Gene Name: FUCA1
                        Uniprot ID: P04066 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Plasma alpha-L-fucosidase
                        Reactions:
                        • an alpha-L-fucoside + H2O = L-fucose + an alcohol [RN:R03162]
                        Gene Name: FUCA2
                        Uniprot ID: Q9BTY2 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Ectonucleoside triphosphate diphosphohydrolase 6
                        Reactions:
                        • a nucleoside diphosphate + H2O = a nucleotide + phosphate [RN:R00329]
                        Gene Name: ENTPD6
                        Uniprot ID: O75354 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Ectonucleoside triphosphate diphosphohydrolase 5
                        Reactions:
                        • a nucleoside diphosphate + H2O = a nucleotide + phosphate [RN:R00329]
                        Gene Name: ENTPD5
                        Uniprot ID: O75356 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Inosine-5'-monophosphate dehydrogenase 2
                        Reactions:
                        • inosine 5'-phosphate + NAD+ + H2O = xanthosine 5'-phosphate + NADH + H+ [RN:R01130]
                        Gene Name: IMPDH2
                        Uniprot ID: P12268 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Bifunctional purine biosynthesis protein PURH
                        Reactions:
                        • IMP + H2O = 5-formamido-1-(5-phospho-D-ribosyl)imidazole-4-carboxamide [RN:R01127]
                        Gene Name: ATIC
                        Uniprot ID: P31939 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Phosphoserine phosphatase
                        Reactions:
                        • O-phospho-L(or D)-serine + H2O = L(or D)-serine + phosphate [RN:R00582 R02853]
                        Gene Name: PSPH
                        Uniprot ID: P78330 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: dTDP-D-glucose 4,6-dehydratase
                        Reactions:
                        • dTDP-glucose = dTDP-4-dehydro-6-deoxy-D-glucose + H2O [RN:R06513]
                        Gene Name: TGDS
                        Uniprot ID: O95455 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: UDP-glucose 6-dehydrogenase
                        Reactions:
                        • UDP-glucose + 2 NAD+ + H2O = UDP-glucuronate + 2 NADH + 2 H+ [RN:R00286]
                        Gene Name: UGDH
                        Uniprot ID: O60701 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Urocanate hydratase
                        Reactions:
                        • 3-(5-oxo-4,5-dihydro-3H-imidazol-4-yl)propanoate = urocanate + H2O [RN:R02914]
                        Gene Name: UROC1
                        Uniprot ID: Q96N76 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: ADP-ribosyl cyclase 2
                        Reactions:
                        • NAD+ + H2O = ADP-ribose + nicotinamide [RN:R00102]
                        Gene Name: BST1
                        Uniprot ID: Q10588 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: ADP-ribosyl cyclase 1
                        Reactions:
                        • NAD+ + H2O = ADP-ribose + nicotinamide [RN:R00102]
                        Gene Name: CD38
                        Uniprot ID: P28907 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: C-1-tetrahydrofolate synthase, cytoplasmic
                        Reactions:
                        • ATP + formate + tetrahydrofolate = ADP + phosphate + 10-formyltetrahydrofolate [RN:R00943]
                        Gene Name: MTHFD1
                        Uniprot ID: P11586 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Nitric oxide synthase, inducible
                        Reactions:
                        • L-arginine + n NADPH + n H+ + m O2 = citrulline + nitric oxide + n NADP+ [RN:R00557]
                        Gene Name: NOS2
                        Uniprot ID: P35228 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 10-formyltetrahydrofolate dehydrogenase
                        Reactions:
                        • 10-formyltetrahydrofolate + NADP+ + H2O = tetrahydrofolate + CO2 + NADPH + H+ [RN:R00941]
                        Gene Name: ALDH1L1
                        Uniprot ID: O75891 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: GTP cyclohydrolase 1
                        Reactions:
                        • GTP + H2O = formate + 7,8-dihydroneopterin 3'-triphosphate [RN:R00424]
                        Gene Name: GCH1
                        Uniprot ID: P30793 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Arachidonate 5-lipoxygenase
                        Reactions:
                        • (1) arachidonate + O2 = (5S,6S,7E,9E,11Z,14Z)-5,6-epoxyicosa-7,9,11,14-tetraenoate + H2O (overall reaction) [RN:R08527]
                        • (2) (1a) arachidonate + O2 = (5S,6E,8Z,11Z,14Z)-5-hydroperoxyicosa-6,8,11,14-tetraenoate [RN:R01595]
                        • (3) (1b) (5S,6E,8Z,11Z,14Z)-5-hydroperoxyicosa-6,8,11,14-tetraenoate = (5S,6S,7E,9E,11Z,14Z)-5,6-epoxyicosa-7,9,11,14-tetraenoate + H2O [RN:R03058]
                        Gene Name: ALOX5
                        Uniprot ID: P09917 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Prostaglandin G/H synthase 2
                        Reactions:
                        • arachidonate + AH2 + 2 O2 = prostaglandin H2 + A + H2O [RN:R01599]
                        Gene Name: PTGS2
                        Uniprot ID: P35354 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Prostaglandin G/H synthase 1
                        Reactions:
                        • arachidonate + AH2 + 2 O2 = prostaglandin H2 + A + H2O [RN:R01599]
                        Gene Name: PTGS1
                        Uniprot ID: P23219 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Methylglutaconyl-CoA hydratase, mitochondrial
                        Reactions:
                        • (S)-3-hydroxy-3-methylglutaryl-CoA = trans-3-methylglutaconyl-CoA + H2O [RN:R02085]
                        Gene Name: AUH
                        Uniprot ID: Q13825 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Leukotriene-B(4) omega-hydroxylase 1
                        Reactions:
                        • (6Z,8E,10E,14Z)-(5S,12R)-5,12-dihydroxyicosa-6,8,10,14-tetraenoate + NADPH + H+ + O2 = (6Z,8E,10E,14Z)-(5S,12R)-5,12,20-trihydroxyicosa-6,8,10,14- tetraenoate + NADP+ + H2O [RN:R03866]
                        Gene Name: CYP4F2
                        Uniprot ID: P78329 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Leukotriene-B(4) omega-hydroxylase 2
                        Reactions:
                        • (6Z,8E,10E,14Z)-(5S,12R)-5,12-dihydroxyicosa-6,8,10,14-tetraenoate + NADPH + H+ + O2 = (6Z,8E,10E,14Z)-(5S,12R)-5,12,20-trihydroxyicosa-6,8,10,14- tetraenoate + NADP+ + H2O [RN:R03866]
                        Gene Name: CYP4F3
                        Uniprot ID: Q08477 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Leukotriene A-4 hydrolase
                        Reactions:
                        • (7E,9E,11Z,14Z)-(5S,6S)-5,6-epoxyicosa-7,9,11,14-tetraenoate + H2O = (6Z,8E,10E,14Z)-(5S,12R)-5,12-dihydroxyicosa-6,8,10,14-tetraenoate [RN:R03057]
                        Gene Name: LTA4H
                        Uniprot ID: P09960 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cytochrome P450 3A4
                        Reactions:
                        • (1) taurochenodeoxycholate + NADPH + H+ + O2 = taurohyocholate + NADP+ + H2O [RN:R07205]
                        • (2) lithocholate + NADPH + H+ + O2 = hyodeoxycholate + NADP+ + H2O [RN:R07206]
                        Gene Name: CYP3A4
                        Uniprot ID: P08684 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Protoporphyrinogen oxidase
                        Reactions:
                        • protoporphyrinogen IX + 3 O2 = protoporphyrin IX + 3 H2O2 [RN:R03222]
                        Gene Name: PPOX
                        Uniprot ID: P50336 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Acidic mammalian chitinase
                        Reactions:
                        • Random hydrolysis of N-acetyl-beta-D-glucosaminide (1->4)-beta-linkages in chitin and chitodextrins ALL_REAC (other) R01206 R02334 R06081(G) R06082(G) INHIBITOR Allosamidine [CPD:C05346]
                        Gene Name: CHIA
                        Uniprot ID: Q9BZP6 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: N-acetylglucosamine-1-phosphodiester alpha-N-acetylglucosaminidase
                        Reactions:
                        • glycoprotein N-acetyl-D-glucosaminyl-phospho-D-mannose + H2O = N-acetyl-D-glucosamine + glycoprotein phospho-D-mannose [RN:R04373]
                        Gene Name: NAGPA
                        Uniprot ID: Q9UK23 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Chitotriosidase-1
                        Reactions:
                        • Random hydrolysis of N-acetyl-beta-D-glucosaminide (1->4)-beta-linkages in chitin and chitodextrins ALL_REAC (other) R01206 R02334 R06081(G) R06082(G) INHIBITOR Allosamidine [CPD:C05346]
                        Gene Name: CHIT1
                        Uniprot ID: Q13231 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Arginase-2, mitochondrial
                        Reactions:
                        • L-arginine + H2O = L-ornithine + urea [RN:R00551]
                        Gene Name: ARG2
                        Uniprot ID: P78540 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cytochrome P450 2C9
                        Reactions:
                        • (R)-limonene + NADPH + H+ + O2 = (+)-trans-carveol + NADP+ + H2O [RN:R06119]
                        Gene Name: CYP2C9
                        Uniprot ID: P11712 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Sterol 26-hydroxylase, mitochondrial
                        Reactions:
                        • 5beta-cholestane-3alpha,7alpha,12alpha-triol + NADPH + H+ + O2 = (25R)-5beta-cholestane-3alpha,7alpha,12alpha,26-tetraol + NADP+ + H2O [RN:R04807]
                        Gene Name: CYP27A1
                        Uniprot ID: Q02318 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cytochrome P450 2C19
                        Reactions:
                        • (R)-limonene + NADPH + H+ + O2 = (+)-trans-carveol + NADP+ + H2O [RN:R06119]
                        Gene Name: CYP2C19
                        Uniprot ID: P33261 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: 25-hydroxyvitamin D-1 alpha hydroxylase, mitochondrial
                        Reactions:
                        • calcidiol + NADPH + H+ + O2 = calcitriol + NADP+ + H2O [RN:R03610]
                        Gene Name: CYP27B1
                        Uniprot ID: O15528 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Steroid 17-alpha-hydroxylase/17,20 lyase
                        Reactions:
                        • a steroid + AH2 + O2 = a 17alpha-hydroxysteroid + A + H2O [RN:R02131]
                        Gene Name: CYP17A1
                        Uniprot ID: P05093 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Cytosolic acyl coenzyme A thioester hydrolase
                        Reactions:
                        • palmitoyl-CoA + H2O = CoA + palmitate [RN:R01274]
                        Gene Name: ACOT7
                        Uniprot ID: O00154 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Acyl-coenzyme A thioesterase 2, mitochondrial
                        Reactions:
                        • palmitoyl-CoA + H2O = CoA + palmitate [RN:R01274]
                        Gene Name: ACOT2
                        Uniprot ID: P49753 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Acyl-coenzyme A thioesterase 4
                        Reactions:
                        • palmitoyl-CoA + H2O = CoA + palmitate [RN:R01274]
                        Gene Name: ACOT4
                        Uniprot ID: Q8N9L9 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Acyl-coenzyme A thioesterase 8
                        Reactions:
                        • choloyl-CoA + H2O = cholate + CoA [RN:R07296]
                        Gene Name: ACOT8
                        Uniprot ID: O14734 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Palmitoyl-protein thioesterase 1
                        Reactions:
                        • palmitoyl[protein] + H2O = palmitate + protein [RN:R01705]
                        Gene Name: PPT1
                        Uniprot ID: P50897 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Lysosomal thioesterase PPT2
                        Reactions:
                        • --- []
                        Gene Name: PPT2
                        Uniprot ID: Q9UMR5 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Sulfite oxidase, mitochondrial
                        Reactions:
                        • sulfite + O2 + H2O = sulfate + H2O2 [RN:R00533]
                        Gene Name: SUOX
                        Uniprot ID: P51687 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Inorganic pyrophosphatase
                        Reactions:
                        • diphosphate + H2O = 2 phosphate [RN:R00004]
                        Gene Name: PPA1
                        Uniprot ID: Q15181 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: mRNA-capping enzyme
                        Reactions:
                        • a 5'-phosphopolynucleotide + H2O = a polynucleotide + phosphate [RN:R02249]
                        Gene Name: RNGTT
                        Uniprot ID: O60942 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Acid ceramidase
                        Reactions:
                        • N-acylsphingosine + H2O = a carboxylate + sphingosine [RN:R01493]
                        Gene Name: ASAH1
                        Uniprot ID: Q13510 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Beta-enolase
                        Reactions:
                        • 2-phospho-D-glycerate = phosphoenolpyruvate + H2O [RN:R00658]
                        Gene Name: ENO3
                        Uniprot ID: P13929 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Gamma-enolase
                        Reactions:
                        • 2-phospho-D-glycerate = phosphoenolpyruvate + H2O [RN:R00658]
                        Gene Name: ENO2
                        Uniprot ID: P09104 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Alpha-enolase
                        Reactions:
                        • 2-phospho-D-glycerate = phosphoenolpyruvate + H2O [RN:R00658]
                        Gene Name: ENO1
                        Uniprot ID: P06733 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Ectonucleotide pyrophosphatase/phosphodiesterase family member 7
                        Reactions:
                        • sphingomyelin + H2O = N-acylsphingosine + choline phosphate [RN:R02541]
                        Gene Name: ENPP7
                        Uniprot ID: Q6UWV6 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Sphingomyelin phosphodiesterase 2
                        Reactions:
                        • sphingomyelin + H2O = N-acylsphingosine + choline phosphate [RN:R02541]
                        Gene Name: SMPD2
                        Uniprot ID: O60906 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Uridine diphosphate glucose pyrophosphatase
                        Reactions:
                        • UDP-sugar + H2O = UMP + alpha-D-aldose 1-phosphate [RN:R03986]
                        Gene Name: NUDT14
                        Uniprot ID: O95848 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Peptide deformylase, mitochondrial
                        Reactions:
                        • formyl-L-methionyl peptide + H2O = formate + methionyl peptide [RN:R05635]
                        Gene Name: PDF
                        Uniprot ID: Q9HBH1 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Inositol monophosphatase 2
                        Reactions:
                        • myo-inositol phosphate + H2O = myo-inositol + phosphate [RN:R07343]
                        Gene Name: IMPA2
                        Uniprot ID: O14732 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Probable phospholipid-transporting ATPase IG
                        Reactions:
                        • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                        Gene Name: ATP11C
                        Uniprot ID: Q8NB49 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Probable phospholipid-transporting ATPase IH
                        Reactions:
                        • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                        Gene Name: ATP11A
                        Uniprot ID: P98196 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Plasma membrane calcium-transporting ATPase 3
                        Reactions:
                        • ATP + H2O + Ca2+cis = ADP + phosphate + Ca2+trans [RN:R00086]
                        Gene Name: ATP2B3
                        Uniprot ID: Q16720 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: Katanin p60 ATPase-containing subunit A1
                        Reactions:
                        • ATP + H2O = ADP + phosphate [RN:R00086]
                        Gene Name: KATNA1
                        Uniprot ID: O75449 Link_out
                        Protein Sequence: FASTA
                        Gene Sequence: FASTA
                        Name: V-type proton ATPase subunit G 3
                        Reactions:
                          Gene Name: ATP6V1G3
                          Uniprot ID: Q96LB4 Link_out
                          Protein Sequence: FASTA
                          Gene Sequence: FASTA
                          Name: Probable phospholipid-transporting ATPase VA
                          Reactions:
                          • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                          Gene Name: ATP10A
                          Uniprot ID: O60312 Link_out
                          Protein Sequence: FASTA
                          Gene Sequence: FASTA
                          Name: V-type proton ATPase subunit G 1
                          Reactions:
                            Gene Name: ATP6V1G1
                            Uniprot ID: O75348 Link_out
                            Protein Sequence: FASTA
                            Gene Sequence: FASTA
                            Name: Probable phospholipid-transporting ATPase IC
                            Reactions:
                            • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                            Gene Name: ATP8B1
                            Uniprot ID: O43520 Link_out
                            Protein Sequence: FASTA
                            Gene Sequence: FASTA
                            Name: Sodium/potassium-transporting ATPase subunit beta-3
                            Reactions:
                              Gene Name: ATP1B3
                              Uniprot ID: P54709 Link_out
                              Protein Sequence: FASTA
                              Gene Sequence: FASTA
                              Name: Plasma membrane calcium-transporting ATPase 1
                              Reactions:
                              • ATP + H2O + Ca2+cis = ADP + phosphate + Ca2+trans [RN:R00086]
                              Gene Name: ATP2B1
                              Uniprot ID: P20020 Link_out
                              Protein Sequence: FASTA
                              Gene Sequence: FASTA
                              Name: ATP synthase subunit epsilon, mitochondrial
                              Reactions:
                                Gene Name: ATP5E
                                Uniprot ID: P56381 Link_out
                                Protein Sequence: FASTA
                                Gene Sequence: FASTA
                                Name: ATP synthase subunit delta, mitochondrial
                                Reactions:
                                • --- []
                                Gene Name: ATP5D
                                Uniprot ID: P30049 Link_out
                                Protein Sequence: FASTA
                                Gene Sequence: FASTA
                                Name: Probable phospholipid-transporting ATPase IIA
                                Reactions:
                                • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                Gene Name: ATP9A
                                Uniprot ID: O75110 Link_out
                                Protein Sequence: FASTA
                                Gene Sequence: FASTA
                                Name: Sodium/potassium-transporting ATPase subunit beta-2
                                Reactions:
                                  Gene Name: ATP1B2
                                  Uniprot ID: P14415 Link_out
                                  Protein Sequence: FASTA
                                  Gene Sequence: FASTA
                                  Name: Plasma membrane calcium-transporting ATPase 2
                                  Reactions:
                                  • ATP + H2O + Ca2+cis = ADP + phosphate + Ca2+trans [RN:R00086]
                                  Gene Name: ATP2B2
                                  Uniprot ID: Q01814 Link_out
                                  Protein Sequence: FASTA
                                  Gene Sequence: FASTA
                                  Name: Sodium/potassium-transporting ATPase subunit beta-1
                                  Reactions:
                                    Gene Name: ATP1B1
                                    Uniprot ID: P05026 Link_out
                                    Protein Sequence: FASTA
                                    Gene Sequence: FASTA
                                    Name: Probable phospholipid-transporting ATPase VD
                                    Reactions:
                                    • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                    Gene Name: ATP10D
                                    Uniprot ID: Q9P241 Link_out
                                    Protein Sequence: FASTA
                                    Gene Sequence: FASTA
                                    Name: Sarcoplasmic/endoplasmic reticulum calcium ATPase 3
                                    Reactions:
                                    • ATP + H2O + Ca2+cis = ADP + phosphate + Ca2+trans [RN:R00086]
                                    Gene Name: ATP2A3
                                    Uniprot ID: Q93084 Link_out
                                    Protein Sequence: FASTA
                                    Gene Sequence: FASTA
                                    Name: V-type proton ATPase subunit C 1
                                    Reactions:
                                    • --- []
                                    Gene Name: ATP6V1C1
                                    Uniprot ID: P21283 Link_out
                                    Protein Sequence: FASTA
                                    Gene Sequence: FASTA
                                    Name: V-type proton ATPase subunit G 2
                                    Reactions:
                                      Gene Name: ATP6V1G2
                                      Uniprot ID: O95670 Link_out
                                      Protein Sequence: FASTA
                                      Gene Sequence: FASTA
                                      Name: ATP synthase subunit O, mitochondrial
                                      Reactions:
                                        Gene Name: ATP5O
                                        Uniprot ID: P48047 Link_out
                                        Protein Sequence: FASTA
                                        Gene Sequence: FASTA
                                        Name: ATP synthase-coupling factor 6, mitochondrial
                                        Reactions:
                                          Gene Name: ATP5J
                                          Uniprot ID: P18859 Link_out
                                          Protein Sequence: FASTA
                                          Gene Sequence: FASTA
                                          Name: Bifunctional polynucleotide phosphatase/kinase
                                          Reactions:
                                          • a 3'-phosphopolynucleotide + H2O = a polynucleotide + phosphate [RN:R02248]
                                          Gene Name: PNKP
                                          Uniprot ID: Q96T60 Link_out
                                          Protein Sequence: FASTA
                                          Gene Sequence: FASTA
                                          Name: V-type proton ATPase subunit B, kidney isoform
                                          Reactions:
                                            Gene Name: ATP6V1B1
                                            Uniprot ID: P15313 Link_out
                                            Protein Sequence: FASTA
                                            Gene Sequence: FASTA
                                            Name: Potassium-transporting ATPase alpha chain 2
                                            Reactions:
                                            • ATP + H2O + H+in + K+out = ADP + phosphate + H+out + K+in [RN:R00086]
                                            Gene Name: ATP12A
                                            Uniprot ID: P54707 Link_out
                                            Protein Sequence: FASTA
                                            Gene Sequence: FASTA
                                            Name: V-type proton ATPase 116 kDa subunit a isoform 4
                                            Reactions:
                                            • --- []
                                            Gene Name: ATP6V0A4
                                            Uniprot ID: Q9HBG4 Link_out
                                            Protein Sequence: FASTA
                                            Gene Sequence: FASTA
                                            Name: Protein ATP1B4
                                            Reactions:
                                              Gene Name: ATP1B4
                                              Uniprot ID: Q9UN42 Link_out
                                              Protein Sequence: FASTA
                                              Gene Sequence: FASTA
                                              Name: ATP synthase protein 8
                                              Reactions:
                                                Gene Name: MT-ATP8
                                                Uniprot ID: P03928 Link_out
                                                Protein Sequence: FASTA
                                                Gene Sequence: FASTA
                                                Name: ATP synthase subunit e, mitochondrial
                                                Reactions:
                                                  Gene Name: ATP5I
                                                  Uniprot ID: P56385 Link_out
                                                  Protein Sequence: FASTA
                                                  Gene Sequence: FASTA
                                                  Name: V-type proton ATPase catalytic subunit A
                                                  Reactions:
                                                  • ATP + H2O + H+in = ADP + phosphate + H+out [RN:R00086]
                                                  Gene Name: ATP6V1A
                                                  Uniprot ID: P38606 Link_out
                                                  Protein Sequence: FASTA
                                                  Gene Sequence: FASTA
                                                  Name: ATP synthase subunit gamma, mitochondrial
                                                  Reactions:
                                                    Gene Name: ATP5C1
                                                    Uniprot ID: P36542 Link_out
                                                    Protein Sequence: FASTA
                                                    Gene Sequence: FASTA
                                                    Name: Plasma membrane calcium-transporting ATPase 4
                                                    Reactions:
                                                    • ATP + H2O + Ca2+cis = ADP + phosphate + Ca2+trans [RN:R00086]
                                                    Gene Name: ATP2B4
                                                    Uniprot ID: P23634 Link_out
                                                    Protein Sequence: FASTA
                                                    Gene Sequence: FASTA
                                                    Name: V-type proton ATPase subunit d 1
                                                    Reactions:
                                                      Gene Name: ATP6V0D1
                                                      Uniprot ID: P61421 Link_out
                                                      Protein Sequence: FASTA
                                                      Gene Sequence: FASTA
                                                      Name: Probable phospholipid-transporting ATPase IA
                                                      Reactions:
                                                      • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                                      Gene Name: ATP8A1
                                                      Uniprot ID: Q9Y2Q0 Link_out
                                                      Protein Sequence: FASTA
                                                      Gene Sequence: FASTA
                                                      Name: Sodium/potassium-transporting ATPase subunit alpha-1
                                                      Reactions:
                                                      • ATP + H2O + Na+in + K+out = ADP + phosphate + Na+out + K+in [RN:R00086]
                                                      Gene Name: ATP1A1
                                                      Uniprot ID: P05023 Link_out
                                                      Protein Sequence: FASTA
                                                      Gene Sequence: FASTA
                                                      Name: Calcium-transporting ATPase type 2C member 1
                                                      Reactions:
                                                      • ATP + H2O + Ca2+cis = ADP + phosphate + Ca2+trans [RN:R00086]
                                                      Gene Name: ATP2C1
                                                      Uniprot ID: P98194 Link_out
                                                      Protein Sequence: FASTA
                                                      Gene Sequence: FASTA
                                                      Name: V-type proton ATPase subunit B, brain isoform
                                                      Reactions:
                                                      • --- []
                                                      Gene Name: ATP6V1B2
                                                      Uniprot ID: P21281 Link_out
                                                      Protein Sequence: FASTA
                                                      Gene Sequence: FASTA
                                                      Name: Sodium/potassium-transporting ATPase subunit alpha-3
                                                      Reactions:
                                                      • ATP + H2O + Na+in + K+out = ADP + phosphate + Na+out + K+in [RN:R00086]
                                                      Gene Name: ATP1A3
                                                      Uniprot ID: P13637 Link_out
                                                      Protein Sequence: FASTA
                                                      Gene Sequence: FASTA
                                                      Name: ATP synthase subunit b, mitochondrial
                                                      Reactions:
                                                        Gene Name: ATP5F1
                                                        Uniprot ID: P24539 Link_out
                                                        Protein Sequence: FASTA
                                                        Gene Sequence: FASTA
                                                        Name: Vesicle-fusing ATPase
                                                        Reactions:
                                                        • ATP + H2O = ADP + phosphate [RN:R00086]
                                                        Gene Name: NSF
                                                        Uniprot ID: P46459 Link_out
                                                        Protein Sequence: FASTA
                                                        Gene Sequence: FASTA
                                                        Name: Potassium-transporting ATPase subunit beta
                                                        Reactions:
                                                          Gene Name: ATP4B
                                                          Uniprot ID: P51164 Link_out
                                                          Protein Sequence: FASTA
                                                          Gene Sequence: FASTA
                                                          Name: ATP synthase subunit alpha, mitochondrial
                                                          Reactions:
                                                            Gene Name: ATP5A1
                                                            Uniprot ID: P25705 Link_out
                                                            Protein Sequence: FASTA
                                                            Gene Sequence: FASTA
                                                            Name: Probable phospholipid-transporting ATPase IIB
                                                            Reactions:
                                                            • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                                            Gene Name: ATP9B
                                                            Uniprot ID: O43861 Link_out
                                                            Protein Sequence: FASTA
                                                            Gene Sequence: FASTA
                                                            Name: Potassium-transporting ATPase alpha chain 1
                                                            Reactions:
                                                            • ATP + H2O + H+in + K+out = ADP + phosphate + H+out + K+in [RN:R00086]
                                                            Gene Name: ATP4A
                                                            Uniprot ID: P20648 Link_out
                                                            Protein Sequence: FASTA
                                                            Gene Sequence: FASTA
                                                            Name: Probable phospholipid-transporting ATPase IM
                                                            Reactions:
                                                            • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                                            Gene Name: ATP8B4
                                                            Uniprot ID: Q8TF62 Link_out
                                                            Protein Sequence: FASTA
                                                            Gene Sequence: FASTA
                                                            Name: Ectonucleoside triphosphate diphosphohydrolase 2
                                                            Reactions:
                                                            • --- []
                                                            Gene Name: ENTPD2
                                                            Uniprot ID: Q9Y5L3 Link_out
                                                            Protein Sequence: FASTA
                                                            Gene Sequence: FASTA
                                                            Name: V-type proton ATPase 16 kDa proteolipid subunit
                                                            Reactions:
                                                              Gene Name: ATP6V0C
                                                              Uniprot ID: P27449 Link_out
                                                              Protein Sequence: FASTA
                                                              Gene Sequence: FASTA
                                                              Name: Probable phospholipid-transporting ATPase IF
                                                              Reactions:
                                                              • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                                              Gene Name: ATP11B
                                                              Uniprot ID: Q9Y2G3 Link_out
                                                              Protein Sequence: FASTA
                                                              Gene Sequence: FASTA
                                                              Name: V-type proton ATPase subunit e 1
                                                              Reactions:
                                                                Gene Name: ATP6V0E1
                                                                Uniprot ID: O15342 Link_out
                                                                Protein Sequence: FASTA
                                                                Gene Sequence: FASTA
                                                                Name: Probable phospholipid-transporting ATPase IK
                                                                Reactions:
                                                                • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                                                Gene Name: ATP8B3
                                                                Uniprot ID: O60423 Link_out
                                                                Protein Sequence: FASTA
                                                                Gene Sequence: FASTA
                                                                Name: ATP synthase subunit d, mitochondrial
                                                                Reactions:
                                                                  Gene Name: ATP5H
                                                                  Uniprot ID: O75947 Link_out
                                                                  Protein Sequence: FASTA
                                                                  Gene Sequence: FASTA
                                                                  Name: ATP synthase subunit f, mitochondrial
                                                                  Reactions:
                                                                    Gene Name: ATP5J2
                                                                    Uniprot ID: P56134 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Sodium/potassium-transporting ATPase subunit alpha-2
                                                                    Reactions:
                                                                    • ATP + H2O + Na+in + K+out = ADP + phosphate + Na+out + K+in [RN:R00086]
                                                                    Gene Name: ATP1A2
                                                                    Uniprot ID: P50993 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2E1
                                                                    Reactions:
                                                                    • --- []
                                                                    Gene Name: CYP2E1
                                                                    Uniprot ID: P05181 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 3A43
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP3A43
                                                                    Uniprot ID: Q9HB55 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 1B1
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP1B1
                                                                    Uniprot ID: Q16678 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2C18
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2C18
                                                                    Uniprot ID: P33260 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2F1
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2F1
                                                                    Uniprot ID: P24903 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 4X1
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP4X1
                                                                    Uniprot ID: Q8N118 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2B6
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2B6
                                                                    Uniprot ID: P20813 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 3A5
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP3A5
                                                                    Uniprot ID: P20815 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2A13
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2A13
                                                                    Uniprot ID: Q16696 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 3A7
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP3A7
                                                                    Uniprot ID: P24462 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 4B1
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP4B1
                                                                    Uniprot ID: P13584 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 4Z1
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP4Z1
                                                                    Uniprot ID: Q86W10 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 1A2
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP1A2
                                                                    Uniprot ID: P05177 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 19A1
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP19A1
                                                                    Uniprot ID: P11511 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2C8
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2C8
                                                                    Uniprot ID: P10632 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2S1
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2S1
                                                                    Uniprot ID: Q96SQ9 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2J2
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2J2
                                                                    Uniprot ID: P51589 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2A7
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2A7
                                                                    Uniprot ID: P20853 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome P450 2A6
                                                                    Reactions:
                                                                    • RH + reduced flavoprotein + O2 = ROH + oxidized flavoprotein + H2O [RN:R04122]
                                                                    Gene Name: CYP2A6
                                                                    Uniprot ID: P11509 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Inositol polyphosphate 5-phosphatase OCRL-1
                                                                    Reactions:
                                                                    • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1-phosphatidyl-1D-myo-inositol 4-phosphate + phosphate [RN:R04404]
                                                                    Gene Name: OCRL
                                                                    Uniprot ID: Q01968 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Phosphatidylinositol-3,4,5-trisphosphate 3-phosphatase and dual-specificity protein phosphatase PTEN
                                                                    Reactions:
                                                                    • phosphatidylinositol 3,4,5-trisphosphate + H2O = phosphatidylinositol 4,5-bisphosphate + phosphate [RN:R04513]
                                                                    Gene Name: PTEN
                                                                    Uniprot ID: P60484 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Synaptojanin-2
                                                                    Reactions:
                                                                    • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1-phosphatidyl-1D-myo-inositol 4-phosphate + phosphate [RN:R04404]
                                                                    Gene Name: SYNJ2
                                                                    Uniprot ID: O15056 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: 72 kDa inositol polyphosphate 5-phosphatase
                                                                    Reactions:
                                                                    • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1-phosphatidyl-1D-myo-inositol 4-phosphate + phosphate [RN:R04404]
                                                                    Gene Name: INPP5E
                                                                    Uniprot ID: Q9NRR6 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Synaptojanin-1
                                                                    Reactions:
                                                                    • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1-phosphatidyl-1D-myo-inositol 4-phosphate + phosphate [RN:R04404]
                                                                    Gene Name: SYNJ1
                                                                    Uniprot ID: O43426 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Thiamine-triphosphatase
                                                                    Reactions:
                                                                    • thiamine triphosphate + H2O = thiamine diphosphate + phosphate [RN:R00618]
                                                                    Gene Name: THTPA
                                                                    Uniprot ID: Q9BU02 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Catalase
                                                                    Reactions:
                                                                    • 2 H2O2 = O2 + 2 H2O [RN:R00009]
                                                                    Gene Name: CAT
                                                                    Uniprot ID: P04040 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Phosphatidylinositol-glycan-specific phospholipase D
                                                                    Reactions:
                                                                    • 6-(alpha-D-glucosaminyl)-1-phosphatidyl-1D-myo-inositol + H2O = 6-(alpha-D-glucosaminyl)-1D-myo-inositol + 3-sn-phosphatidate [RN:R06623]
                                                                    Gene Name: GPLD1
                                                                    Uniprot ID: P80108 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Dolichyldiphosphatase 1
                                                                    Reactions:
                                                                    • dolichyl diphosphate + H2O = dolichyl phosphate + phosphate [RN:R01004]
                                                                    Gene Name: DOLPP1
                                                                    Uniprot ID: Q86YN1 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Alpha-L-iduronidase
                                                                    Reactions:
                                                                    • Hydrolysis of unsulfated alpha-L-iduronosidic linkages in dermatan sulfate ALL_REAC (other) R07813(G) R07822(G) REFERENCE 1 [PMID:4993544] AUTHORS Matalon R, Cifonelli JA, Dorfman A. TITLE L-iduronidase in cultured human fibroblasts and liver. JOURNAL Biochem. Biophys. Res. Commun. 42 (1971) 340-5. ORGANISM Homo sapiens [GN:hsa] REFERENCE 2 [PMID:30407] AUTHORS Rome LH, Garvin AJ, Neufeld EF. TITLE Human kidney alpha-L-iduronidase: purification and characterization. JOURNAL Arch. Biochem. Biophys. 189 (1978) 344-53. ORGANISM Homo sapiens [GN:hsa] REFERENCE 3 AUTHORS Srivastava, R.M., Hudson, N., Seymour, F.R. and Weissman, B. TITLE Preparation of (aryl alpha-L-idopyranosid)uronic acids. JOURNAL Carbohydr. Res. 60 (1978) 315-326.
                                                                    Gene Name: IDUA
                                                                    Uniprot ID: P35475 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Iduronate 2-sulfatase
                                                                    Reactions:
                                                                    • Hydrolysis of the 2-sulfate groups of the L-iduronate 2-sulfate units of dermatan sulfate, heparan sulfate and heparin [RN:R07812 R07821] ALL_REAC R07812(G) R07821(G) REFERENCE 1 [PMID:6816283] AUTHORS Archer IM, Harper PS, Wusteman FS. TITLE Multiple forms of iduronate 2-sulphate sulphatase in human tissues and body fluids. JOURNAL Biochim. Biophys. Acta. 708 (1982) 134-40. ORGANISM Homo sapiens [GN:hsa] REFERENCE 2 [PMID:4269173] AUTHORS Bach G, Eisenberg F Jr, Cantz M, Neufeld EF. TITLE The defect in the Hunter syndrome: deficiency of sulfoiduronate sulfatase. JOURNAL Proc. Natl. Acad. Sci. U. S. A. 70 (1973) 2134-8. ORGANISM Homo sapiens [GN:hsa] REFERENCE 3 [PMID:6945876] AUTHORS Di Natale P, Ronsisvalle L. TITLE Identification and partial characterization of two enzyme forms of iduronate sulfatase from human placenta. JOURNAL Biochim. Biophys. Acta. 661 (1981) 106-11. ORGANISM Homo sapiens [GN:hsa] REFERENCE 4 [PMID:6950934] AUTHORS Yutaka T, Fluharty AL, Stevens RL, Kihara H. TITLE Purification and some properties of human liver iduronate sulfatase. JOURNAL J. Biochem. (Tokyo). 91 (1982) 433-41. ORGANISM Homo sapiens [GN:hsa]
                                                                    Gene Name: IDS
                                                                    Uniprot ID: P22304 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Alpha-N-acetylglucosaminidase
                                                                    Reactions:
                                                                    • Hydrolysis of terminal non-reducing N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides ALL_REAC (other) R07816(G)
                                                                    Gene Name: NAGLU
                                                                    Uniprot ID: P54802 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: N-acetylglucosamine-6-sulfatase
                                                                    Reactions:
                                                                    • Hydrolysis of the 6-sulfate groups of the N-acetyl-D-glucosamine 6-sulfate units of heparan sulfate and keratan sulfate [RN:R07808 R07819] ALL_REAC R07808(G) R07819(G)
                                                                    Gene Name: GNS
                                                                    Uniprot ID: P15586 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: 25-hydroxycholesterol 7-alpha-hydroxylase
                                                                    Reactions:
                                                                    • (1) cholest-5-ene-3beta,25-diol + NADPH + H+ + O2 = cholest-5-ene-3beta,7alpha,25-triol + NADP+ + H2O [RN:R07209]
                                                                    • (2) cholest-5-ene-3beta,27-diol + NADPH + H+ + O2 = cholest-5-ene-3beta,7alpha,27-triol + NADP+ + H2O [RN:R07372]
                                                                    Gene Name: CYP7B1
                                                                    Uniprot ID: O75881 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Cytochrome c oxidase subunit 1
                                                                    Reactions:
                                                                    • 4 ferrocytochrome c + O2 + 4 H+ = 4 ferricytochrome c + 2 H2O [RN:R00081]
                                                                    Gene Name: MT-CO1
                                                                    Uniprot ID: P00395 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Serine/threonine-protein phosphatase PP1-beta catalytic subunit
                                                                    Reactions:
                                                                    • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                    Gene Name: PPP1CB
                                                                    Uniprot ID: P62140 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Epoxide hydrolase 2
                                                                    Reactions:
                                                                    • an epoxide + H2O = a glycol [RN:R02822]
                                                                    Gene Name: EPHX2
                                                                    Uniprot ID: P34913 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Epoxide hydrolase 1
                                                                    Reactions:
                                                                    • cis-stilbene oxide + H2O = (+)-(1R,2R)-1,2-diphenylethane-1,2-diol [RN:R07627]
                                                                    Gene Name: EPHX1
                                                                    Uniprot ID: P07099 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Glucosylceramidase
                                                                    Reactions:
                                                                    • D-glucosyl-N-acylsphingosine + H2O = D-glucose + N-acylsphingosine [RN:R01498]
                                                                    Gene Name: GBA
                                                                    Uniprot ID: P04062 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Type II inositol-1,4,5-trisphosphate 5-phosphatase
                                                                    Reactions:
                                                                    • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1-phosphatidyl-1D-myo-inositol 4-phosphate + phosphate [RN:R04404]
                                                                    Gene Name: INPP5B
                                                                    Uniprot ID: P32019 Link_out
                                                                    Protein Sequence: FASTA
                                                                    Gene Sequence: FASTA
                                                                    Name: Elongation factor 1-alpha 1
                                                                    Reactions:
                                                                      Gene Name: EEF1A1
                                                                      Uniprot ID: P68104 Link_out
                                                                      Protein Sequence: FASTA
                                                                      Gene Sequence: FASTA
                                                                      Name: Elongation factor 1-alpha 2
                                                                      Reactions:
                                                                        Gene Name: EEF1A2
                                                                        Uniprot ID: Q05639 Link_out
                                                                        Protein Sequence: FASTA
                                                                        Gene Sequence: FASTA
                                                                        Name: Laforin
                                                                        Reactions:
                                                                        • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                        Gene Name: EPM2A
                                                                        Uniprot ID: O95278 Link_out
                                                                        Protein Sequence: FASTA
                                                                        Gene Sequence: FASTA
                                                                        Name: Serine/threonine-protein phosphatase PP1-gamma catalytic subunit
                                                                        Reactions:
                                                                        • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                        Gene Name: PPP1CC
                                                                        Uniprot ID: P36873 Link_out
                                                                        Protein Sequence: FASTA
                                                                        Gene Sequence: FASTA
                                                                        Name: Pantetheinase
                                                                        Reactions:
                                                                        • (R)-pantetheine + H2O = (R)-pantothenate + 2-aminoethanethiol [RN:R02973]
                                                                        Gene Name: VNN1
                                                                        Uniprot ID: O95497 Link_out
                                                                        Protein Sequence: FASTA
                                                                        Gene Sequence: FASTA
                                                                        Name: Proline dehydrogenase, mitochondrial
                                                                        Reactions:
                                                                        • L-proline + acceptor = (S)-1-pyrroline-5-carboxylate + reduced acceptor [RN:R01253]
                                                                        Gene Name: PRODH
                                                                        Uniprot ID: O43272 Link_out
                                                                        Protein Sequence: FASTA
                                                                        Gene Sequence: FASTA
                                                                        Name: Peptidoglycan recognition protein 1
                                                                        Reactions:
                                                                          Gene Name: PGLYRP1
                                                                          Uniprot ID: O75594 Link_out
                                                                          Protein Sequence: FASTA
                                                                          Gene Sequence: FASTA
                                                                          Name: Carbonic anhydrase 1
                                                                          Reactions:
                                                                          • H2CO3 = CO2 + H2O [RN:R00132]
                                                                          Gene Name: CA1
                                                                          Uniprot ID: P00915 Link_out
                                                                          Protein Sequence: FASTA
                                                                          Gene Sequence: FASTA
                                                                          Name: Carbonic anhydrase 2
                                                                          Reactions:
                                                                          • H2CO3 = CO2 + H2O [RN:R00132]
                                                                          Gene Name: CA2
                                                                          Uniprot ID: P00918 Link_out
                                                                          Protein Sequence: FASTA
                                                                          Gene Sequence: FASTA
                                                                          Name: Alpha-amylase 1
                                                                          Reactions:
                                                                          • Endohydrolysis of (1->4)-alpha-D-glucosidic linkages in polysaccharides containing three or more (1->4)-alpha-linked D-glucose units ALL_REAC (other) R02108 R06209(G)
                                                                          Gene Name: AMY1A
                                                                          Uniprot ID: P04745 Link_out
                                                                          Protein Sequence: FASTA
                                                                          Gene Sequence: FASTA
                                                                          Name: Pancreatic alpha-amylase
                                                                          Reactions:
                                                                          • Endohydrolysis of (1->4)-alpha-D-glucosidic linkages in polysaccharides containing three or more (1->4)-alpha-linked D-glucose units ALL_REAC (other) R02108 R06209(G)
                                                                          Gene Name: AMY2A
                                                                          Uniprot ID: P04746 Link_out
                                                                          Protein Sequence: FASTA
                                                                          Gene Sequence: FASTA
                                                                          Name: Natriuretic peptides B
                                                                          Reactions:
                                                                            Gene Name: NPPB
                                                                            Uniprot ID: P16860 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Alpha-amylase 2B
                                                                            Reactions:
                                                                            • Endohydrolysis of (1->4)-alpha-D-glucosidic linkages in polysaccharides containing three or more (1->4)-alpha-linked D-glucose units ALL_REAC (other) R02108 R06209(G)
                                                                            Gene Name: AMY2B
                                                                            Uniprot ID: P19961 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: N-acetylgalactosamine-6-sulfatase
                                                                            Reactions:
                                                                            • Hydrolysis of the 6-sulfate groups of the N-acetyl-D-galactosamine 6-sulfate units of chondroitin sulfate and of the D-galactose 6-sulfate units of keratan sulfate [RN:R07806] ALL_REAC R07806(G) REFERENCE 1 [PMID:6939689] AUTHORS Epstein EH Jr, Leventhal ME. TITLE Steroid sulfatase of human leukocytes and epidermis and the diagnosis of recessive X-linked ichthyosis. JOURNAL J. Clin. Invest. 67 (1981) 1257-62. ORGANISM Homo sapiens [GN:hsa] REFERENCE 2 [PMID:6213226] AUTHORS Glossl J, Kresse H. TITLE Impaired degradation of keratan sulphate by Morquio A fibroblasts. JOURNAL Biochem. J. 203 (1982) 335-8. ORGANISM Homo sapiens [GN:hsa] REFERENCE 3 [PMID:7213753] AUTHORS Lim CT, Horwitz AL. TITLE Purification and properties of human N-acetylgalactosamine-6-sulfate sulfatase. JOURNAL Biochim. Biophys. Acta. 657 (1981) 344-55. ORGANISM Homo sapiens [GN:hsa] REFERENCE 4 [PMID:6814909] AUTHORS Sorensen SH, Noren O, Sjostrom H, Danielsen EM. TITLE Amphiphilic pig intestinal microvillus maltase/glucoamylase. Structure and specificity. JOURNAL Eur. J. Biochem. 126 (1982) 559-68. ORGANISM Sus scofa [GN:ssc] REFERENCE 5 [PMID:6809361] AUTHORS Yutaka T, Okada S, Kato T, Inui K, Yabuuhi H. TITLE Galactose 6-sulfate sulfatase activity in Morquio syndrome. JOURNAL Clin. Chim. Acta. 122 (1982) 169-80. ORGANISM shark
                                                                            Gene Name: GALNS
                                                                            Uniprot ID: P34059 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Vitamin K epoxide reductase complex subunit 1
                                                                            Reactions:
                                                                            • 2-methyl-3-phytyl-1,4-naphthoquinone + oxidized dithiothreitol = 2,3-epoxy-2,3-dihydro-2-methyl-3-phytyl-1,4-naphthoquinone + 1,4-dithiothreitol [RN:R03511]
                                                                            Gene Name: VKORC1
                                                                            Uniprot ID: Q9BQB6 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Cytochrome c oxidase subunit 7A1, mitochondrial
                                                                            Reactions:
                                                                            • --- []
                                                                            Gene Name: COX7A1
                                                                            Uniprot ID: P24310 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Carbonic anhydrase 5A, mitochondrial
                                                                            Reactions:
                                                                            • H2CO3 = CO2 + H2O [RN:R00132]
                                                                            Gene Name: CA5A
                                                                            Uniprot ID: P35218 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: 2',3'-cyclic-nucleotide 3'-phosphodiesterase
                                                                            Reactions:
                                                                            • nucleoside 2',3'-cyclic phosphate + H2O = nucleoside 2'-phosphate [RN:R03422]
                                                                            Gene Name: CNP
                                                                            Uniprot ID: P09543 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Ubiquitin carboxyl-terminal hydrolase CYLD
                                                                            Reactions:
                                                                            • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                            Gene Name: CYLD
                                                                            Uniprot ID: Q9NQC7 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Tyrosine-protein phosphatase non-receptor type 6
                                                                            Reactions:
                                                                            • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                            Gene Name: PTPN6
                                                                            Uniprot ID: P29350 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Peroxiredoxin-5, mitochondrial
                                                                            Reactions:
                                                                            • 2 R'-SH + ROOH = R'-S-S-R' + H2O + ROH [RN:R07180]
                                                                            Gene Name: PRDX5
                                                                            Uniprot ID: P30044 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Carbonic anhydrase 3
                                                                            Reactions:
                                                                            • H2CO3 = CO2 + H2O [RN:R00132]
                                                                            Gene Name: CA3
                                                                            Uniprot ID: P07451 Link_out
                                                                            Protein Sequence: FASTA
                                                                            Gene Sequence: FASTA
                                                                            Name: Aquaporin-3
                                                                            Reactions:
                                                                              Gene Name: AQP3
                                                                              Uniprot ID: Q92482 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Receptor-type tyrosine-protein phosphatase C
                                                                              Reactions:
                                                                              • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                              Gene Name: PTPRC
                                                                              Uniprot ID: P08575 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Kynurenine 3-monooxygenase
                                                                              Reactions:
                                                                              • L-kynurenine + NADPH + H+ + O2 = 3-hydroxy-L-kynurenine + NADP+ + H2O [RN:R01960]
                                                                              Gene Name: KMO
                                                                              Uniprot ID: O15229 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Probable peptidyl-tRNA hydrolase
                                                                              Reactions:
                                                                              • N-Substituted aminoacyl-tRNA + H2O = N-substituted amino acid + tRNA [RN:R04238]
                                                                              Gene Name: PTRH1
                                                                              Uniprot ID: Q86Y79 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Agmatinase, mitochondrial
                                                                              Reactions:
                                                                              • agmatine + H2O = putrescine + urea [RN:R01157]
                                                                              Gene Name: AGMAT
                                                                              Uniprot ID: Q9BSE5 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Receptor-type tyrosine-protein phosphatase alpha
                                                                              Reactions:
                                                                              • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                              Gene Name: PTPRA
                                                                              Uniprot ID: P18433 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Myotubularin
                                                                              Reactions:
                                                                              • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                              Gene Name: MTM1
                                                                              Uniprot ID: Q13496 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Dual specificity protein phosphatase 2
                                                                              Reactions:
                                                                              • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                              Gene Name: DUSP2
                                                                              Uniprot ID: Q05923 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Pterin-4-alpha-carbinolamine dehydratase
                                                                              Reactions:
                                                                              • (6R)-6-(L-erythro-1,2-dihydroxypropyl)-5,6,7,8-tetrahydro-4a- hydroxypterin = (6R)-6-(L-erythro-1,2-dihydroxypropyl)-7,8-dihydro-6H-pterin + H2O [RN:R04734]
                                                                              Gene Name: PCBD1
                                                                              Uniprot ID: P61457 Link_out
                                                                              Protein Sequence: FASTA
                                                                              Gene Sequence: FASTA
                                                                              Name: Aquaporin-2
                                                                              Reactions:
                                                                                Gene Name: AQP2
                                                                                Uniprot ID: P41181 Link_out
                                                                                Protein Sequence: FASTA
                                                                                Gene Sequence: FASTA
                                                                                Name: Elongation factor 2
                                                                                Reactions:
                                                                                  Gene Name: EEF2
                                                                                  Uniprot ID: P13639 Link_out
                                                                                  Protein Sequence: FASTA
                                                                                  Gene Sequence: FASTA
                                                                                  Name: Peroxiredoxin-1
                                                                                  Reactions:
                                                                                  • 2 R'-SH + ROOH = R'-S-S-R' + H2O + ROH [RN:R07180]
                                                                                  Gene Name: PRDX1
                                                                                  Uniprot ID: Q06830 Link_out
                                                                                  Protein Sequence: FASTA
                                                                                  Gene Sequence: FASTA
                                                                                  Name: V-type proton ATPase 116 kDa subunit a isoform 2
                                                                                  Reactions:
                                                                                    Gene Name: ATP6V0A2
                                                                                    Uniprot ID: Q9Y487 Link_out
                                                                                    Protein Sequence: FASTA
                                                                                    Gene Sequence: FASTA
                                                                                    Name: Peroxiredoxin-2
                                                                                    Reactions:
                                                                                    • 2 R'-SH + ROOH = R'-S-S-R' + H2O + ROH [RN:R07180]
                                                                                    Gene Name: PRDX2
                                                                                    Uniprot ID: P32119 Link_out
                                                                                    Protein Sequence: FASTA
                                                                                    Gene Sequence: FASTA
                                                                                    Name: Carbonic anhydrase 5B, mitochondrial
                                                                                    Reactions:
                                                                                    • H2CO3 = CO2 + H2O [RN:R00132]
                                                                                    Gene Name: CA5B
                                                                                    Uniprot ID: Q9Y2D0 Link_out
                                                                                    Protein Sequence: FASTA
                                                                                    Gene Sequence: FASTA
                                                                                    Name: Cytochrome c oxidase subunit 7A2, mitochondrial
                                                                                    Reactions:
                                                                                      Gene Name: COX7A2
                                                                                      Uniprot ID: P14406 Link_out
                                                                                      Protein Sequence: FASTA
                                                                                      Gene Sequence: FASTA
                                                                                      Name: Myotubularin-related protein 3
                                                                                      Reactions:
                                                                                      • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                      Gene Name: MTMR3
                                                                                      Uniprot ID: Q13615 Link_out
                                                                                      Protein Sequence: FASTA
                                                                                      Gene Sequence: FASTA
                                                                                      Name: Cholesterol 25-hydroxylase
                                                                                      Reactions:
                                                                                      • cholesterol + AH2 + O2 = 25-hydroxycholesterol + A + H2O [RN:R07218]
                                                                                      Gene Name: CH25H
                                                                                      Uniprot ID: O95992 Link_out
                                                                                      Protein Sequence: FASTA
                                                                                      Gene Sequence: FASTA
                                                                                      Name: AID
                                                                                      Reactions:
                                                                                        Gene Name: AID
                                                                                        Uniprot ID: Q546Y9 Link_out
                                                                                        Protein Sequence: FASTA
                                                                                        Gene Sequence: FASTA
                                                                                        Name: Cytosolic beta-glucosidase
                                                                                        Reactions:
                                                                                        • Hydrolysis of terminal, non-reducing beta-D-glucosyl residues with release of beta-D-glucose ALL_REAC (other) R00026 R02887 R03527 R04949 R04998 R06077(G) R06092(G)
                                                                                        Gene Name: GBA3
                                                                                        Uniprot ID: Q9H227 Link_out
                                                                                        Protein Sequence: FASTA
                                                                                        Gene Sequence: FASTA
                                                                                        Name: Thioredoxin-dependent peroxide reductase, mitochondrial
                                                                                        Reactions:
                                                                                        • 2 R'-SH + ROOH = R'-S-S-R' + H2O + ROH [RN:R07180]
                                                                                        Gene Name: PRDX3
                                                                                        Uniprot ID: P30048 Link_out
                                                                                        Protein Sequence: FASTA
                                                                                        Gene Sequence: FASTA
                                                                                        Name: Maltase-glucoamylase, intestinal
                                                                                        Reactions:
                                                                                        • Hydrolysis of terminal, non-reducing (1->4)-linked alpha-D-glucose residues with release of D-glucose ALL_REAC (other) R00028 R00801 R00802 R06084(G) R06087(G) R06088(G) INHIBITOR Castanospermine [CPD:C02256]
                                                                                        Gene Name: MGAM
                                                                                        Uniprot ID: O43451 Link_out
                                                                                        Protein Sequence: FASTA
                                                                                        Gene Sequence: FASTA
                                                                                        Name: Carbonic anhydrase 12
                                                                                        Reactions:
                                                                                        • H2CO3 = CO2 + H2O [RN:R00132]
                                                                                        Gene Name: CA12
                                                                                        Uniprot ID: O43570 Link_out
                                                                                        Protein Sequence: FASTA
                                                                                        Gene Sequence: FASTA
                                                                                        Name: Phosphoethanolamine/phosphocholine phosphatase
                                                                                        Reactions:
                                                                                        • (1) O-phosphoethanolamine + H2O = ethanolamine + phosphate [RN:R06870]
                                                                                        • (2) phosphocholine + H2O = choline + phosphate [RN:R06871]
                                                                                        Gene Name: PHOSPHO1
                                                                                        Uniprot ID: Q8TCT1 Link_out
                                                                                        Protein Sequence: FASTA
                                                                                        Gene Sequence: FASTA
                                                                                        Name: ATP synthase lipid-binding protein, mitochondrial
                                                                                        Reactions:
                                                                                          Gene Name: ATP5G3
                                                                                          Uniprot ID: P48201 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Carbonic anhydrase 4
                                                                                          Reactions:
                                                                                          • H2CO3 = CO2 + H2O [RN:R00132]
                                                                                          Gene Name: CA4
                                                                                          Uniprot ID: P22748 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Sodium/potassium-transporting ATPase subunit alpha-4
                                                                                          Reactions:
                                                                                          • ATP + H2O + Na+in + K+out = ADP + phosphate + Na+out + K+in [RN:R00086]
                                                                                          Gene Name: ATP1A4
                                                                                          Uniprot ID: Q13733 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Cytochrome c oxidase subunit 6A2, mitochondrial
                                                                                          Reactions:
                                                                                          • --- []
                                                                                          Gene Name: COX6A2
                                                                                          Uniprot ID: Q02221 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Cytochrome c oxidase subunit 7B, mitochondrial
                                                                                          Reactions:
                                                                                          • --- []
                                                                                          Gene Name: COX7B
                                                                                          Uniprot ID: P24311 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Cytochrome c oxidase subunit 7C, mitochondrial
                                                                                          Reactions:
                                                                                          • --- []
                                                                                          Gene Name: COX7C
                                                                                          Uniprot ID: P15954 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Cytochrome c oxidase subunit 5B, mitochondrial
                                                                                          Reactions:
                                                                                          • --- []
                                                                                          Gene Name: COX5B
                                                                                          Uniprot ID: P10606 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Carbonic anhydrase 9
                                                                                          Reactions:
                                                                                          • H2CO3 = CO2 + H2O [RN:R00132]
                                                                                          Gene Name: CA9
                                                                                          Uniprot ID: Q16790 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Cytochrome c oxidase subunit 6B1
                                                                                          Reactions:
                                                                                          • --- []
                                                                                          Gene Name: COX6B1
                                                                                          Uniprot ID: P14854 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Cytosolic 5'-nucleotidase 3
                                                                                          Reactions:
                                                                                          • a 5'-ribonucleotide + H2O = a ribonucleoside + phosphate [RN:R07297]
                                                                                          Gene Name: NT5C3
                                                                                          Uniprot ID: Q9H0P0 Link_out
                                                                                          Protein Sequence: FASTA
                                                                                          Gene Sequence: FASTA
                                                                                          Name: Cytochrome c oxidase subunit 7B2, mitochondrial
                                                                                          Reactions:
                                                                                            Gene Name: COX7B2
                                                                                            Uniprot ID: Q8TF08 Link_out
                                                                                            Protein Sequence: FASTA
                                                                                            Gene Sequence: FASTA
                                                                                            Name: Cytochrome c oxidase subunit 4 isoform 1, mitochondrial
                                                                                            Reactions:
                                                                                            • --- []
                                                                                            Gene Name: COX4I1
                                                                                            Uniprot ID: P13073 Link_out
                                                                                            Protein Sequence: FASTA
                                                                                            Gene Sequence: FASTA
                                                                                            Name: ENTPD4 protein
                                                                                            Reactions:
                                                                                              Gene Name: ENTPD4
                                                                                              Uniprot ID: Q8NE73 Link_out
                                                                                              Protein Sequence: FASTA
                                                                                              Gene Sequence: FASTA
                                                                                              Name: Cytochrome c oxidase subunit 6B2
                                                                                              Reactions:
                                                                                                Gene Name: COX6B2
                                                                                                Uniprot ID: Q6YFQ2 Link_out
                                                                                                Protein Sequence: FASTA
                                                                                                Gene Sequence: FASTA
                                                                                                Name: Glutamine-dependent NAD(+) synthetase
                                                                                                Reactions:
                                                                                                • ATP + deamido-NAD+ + L-glutamine + H2O = AMP + diphosphate + NAD+ + L-glutamate [RN:R00257]
                                                                                                Gene Name: NADSYN1
                                                                                                Uniprot ID: Q6IA69 Link_out
                                                                                                Protein Sequence: FASTA
                                                                                                Gene Sequence: FASTA
                                                                                                Name: Carbonic anhydrase 13
                                                                                                Reactions:
                                                                                                • H2CO3 = CO2 + H2O [RN:R00132]
                                                                                                Gene Name: CA13
                                                                                                Uniprot ID: Q8N1Q1 Link_out
                                                                                                Protein Sequence: FASTA
                                                                                                Gene Sequence: FASTA
                                                                                                Name: Phosphatidylinositol-3,4,5-trisphosphate 5-phosphatase 2
                                                                                                Reactions:
                                                                                                  Gene Name: INPPL1
                                                                                                  Uniprot ID: O15357 Link_out
                                                                                                  Protein Sequence: FASTA
                                                                                                  Gene Sequence: FASTA
                                                                                                  Name: ATP synthase lipid-binding protein, mitochondrial
                                                                                                  Reactions:
                                                                                                    Gene Name: ATP5G1
                                                                                                    Uniprot ID: P05496 Link_out
                                                                                                    Protein Sequence: FASTA
                                                                                                    Gene Sequence: FASTA
                                                                                                    Name: Cytochrome c oxidase subunit 8A, mitochondrial
                                                                                                    Reactions:
                                                                                                    • --- []
                                                                                                    Gene Name: COX8A
                                                                                                    Uniprot ID: P10176 Link_out
                                                                                                    Protein Sequence: FASTA
                                                                                                    Gene Sequence: FASTA
                                                                                                    Name: Type II inositol-3,4-bisphosphate 4-phosphatase
                                                                                                    Reactions:
                                                                                                    • 1-phosphatidyl-myo-inositol 3,4-bisphosphate + H2O = 1-phosphatidyl-1D-myo-inositol 3-phosphate + phosphate [RN:R07299]
                                                                                                    Gene Name: INPP4B
                                                                                                    Uniprot ID: O15327 Link_out
                                                                                                    Protein Sequence: FASTA
                                                                                                    Gene Sequence: FASTA
                                                                                                    Name: Cytochrome c oxidase subunit 6C
                                                                                                    Reactions:
                                                                                                    • --- []
                                                                                                    Gene Name: COX6C
                                                                                                    Uniprot ID: P09669 Link_out
                                                                                                    Protein Sequence: FASTA
                                                                                                    Gene Sequence: FASTA
                                                                                                    Name: Cytochrome c oxidase subunit 7A-related protein, mitochondrial
                                                                                                    Reactions:
                                                                                                      Gene Name: COX7A2L
                                                                                                      Uniprot ID: O14548 Link_out
                                                                                                      Protein Sequence: FASTA
                                                                                                      Gene Sequence: FASTA
                                                                                                      Name: CAD protein
                                                                                                      Reactions:
                                                                                                      • (1) 2 ATP + L-glutamine + HCO3- + H2O = 2 ADP + phosphate + L-glutamate + carbamoyl phosphate [RN:R00575]
                                                                                                      • (2) L-glutamine + H2O = L-glutamate + NH3 [RN:R00256]
                                                                                                      • (3) 2 ATP + HCO3- = 2 ADP + phosphate + carbamoyl phosphate [RN:R07641]
                                                                                                      Gene Name: CAD
                                                                                                      Uniprot ID: P27708 Link_out
                                                                                                      Protein Sequence: FASTA
                                                                                                      Gene Sequence: FASTA
                                                                                                      Name: Cytochrome c oxidase subunit 8C, mitochondrial
                                                                                                      Reactions:
                                                                                                        Gene Name: COX8C
                                                                                                        Uniprot ID: Q7Z4L0 Link_out
                                                                                                        Protein Sequence: FASTA
                                                                                                        Gene Sequence: FASTA
                                                                                                        Name: L-asparaginase
                                                                                                        Reactions:
                                                                                                        • L-asparagine + H2O = L-aspartate + NH3 [RN:R00485]
                                                                                                        Gene Name: ASRGL1
                                                                                                        Uniprot ID: Q7L266 Link_out
                                                                                                        Protein Sequence: FASTA
                                                                                                        Gene Sequence: FASTA
                                                                                                        Name: Putative N-acetylglucosamine-6-phosphate deacetylase
                                                                                                        Reactions:
                                                                                                        • N-acetyl-D-glucosamine 6-phosphate + H2O = D-glucosamine 6-phosphate + acetate [RN:R02059]
                                                                                                        Gene Name: AMDHD2
                                                                                                        Uniprot ID: Q9Y303 Link_out
                                                                                                        Protein Sequence: FASTA
                                                                                                        Gene Sequence: FASTA
                                                                                                        Name: Pyridoxal phosphate phosphatase
                                                                                                        Reactions:
                                                                                                        • pyridoxal 5'-phosphate + H2O = pyridoxal + phosphate [RN:R00173]
                                                                                                        Gene Name: PDXP
                                                                                                        Uniprot ID: Q96GD0 Link_out
                                                                                                        Protein Sequence: FASTA
                                                                                                        Gene Sequence: FASTA
                                                                                                        Name: Methionine adenosyltransferase 2 subunit beta
                                                                                                        Reactions:
                                                                                                          Gene Name: MAT2B
                                                                                                          Uniprot ID: Q9NZL9 Link_out
                                                                                                          Protein Sequence: FASTA
                                                                                                          Gene Sequence: FASTA
                                                                                                          Name: V-type proton ATPase subunit H
                                                                                                          Reactions:
                                                                                                            Gene Name: ATP6V1H
                                                                                                            Uniprot ID: Q9UI12 Link_out
                                                                                                            Protein Sequence: FASTA
                                                                                                            Gene Sequence: FASTA
                                                                                                            Name: V-type proton ATPase subunit D
                                                                                                            Reactions:
                                                                                                              Gene Name: ATP6V1D
                                                                                                              Uniprot ID: Q9Y5K8 Link_out
                                                                                                              Protein Sequence: FASTA
                                                                                                              Gene Sequence: FASTA
                                                                                                              Name: V-type proton ATPase subunit d 2
                                                                                                              Reactions:
                                                                                                                Gene Name: ATP6V0D2
                                                                                                                Uniprot ID: Q8N8Y2 Link_out
                                                                                                                Protein Sequence: FASTA
                                                                                                                Gene Sequence: FASTA
                                                                                                                Name: V-type proton ATPase subunit E 2
                                                                                                                Reactions:
                                                                                                                  Gene Name: ATP6V1E2
                                                                                                                  Uniprot ID: Q96A05 Link_out
                                                                                                                  Protein Sequence: FASTA
                                                                                                                  Gene Sequence: FASTA
                                                                                                                  Name: V-type proton ATPase subunit C 2
                                                                                                                  Reactions:
                                                                                                                    Gene Name: ATP6V1C2
                                                                                                                    Uniprot ID: Q8NEY4 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: CTP synthase 2
                                                                                                                    Reactions:
                                                                                                                    • ATP + UTP + NH3 = ADP + phosphate + CTP [RN:R00571]
                                                                                                                    Gene Name: CTPS2
                                                                                                                    Uniprot ID: Q9NRF8 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Dual 3',5'-cyclic-AMP and -GMP phosphodiesterase 11A
                                                                                                                    Reactions:
                                                                                                                    • guanosine 3',5'-cyclic phosphate + H2O = guanosine 5'-phosphate [RN:R01234]
                                                                                                                    Gene Name: PDE11A
                                                                                                                    Uniprot ID: Q9HCR9 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Phosphoglycolate phosphatase
                                                                                                                    Reactions:
                                                                                                                    • 2-phosphoglycolate + H2O = glycolate + phosphate [RN:R01334]
                                                                                                                    Gene Name: PGP
                                                                                                                    Uniprot ID: A6NDG6 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: 1-phosphatidylinositol-4,5-bisphosphate phosphodiesterase delta-4
                                                                                                                    Reactions:
                                                                                                                    • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1D-myo-inositol 1,4,5-trisphosphate + diacylglycerol
                                                                                                                    Gene Name: PLCD4
                                                                                                                    Uniprot ID: Q9BRC7 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: 1-phosphatidylinositol-4,5-bisphosphate phosphodiesterase delta-3
                                                                                                                    Reactions:
                                                                                                                    • 1-phosphatidyl-1D-myo-inositol 4,5-bisphosphate + H2O = 1D-myo-inositol 1,4,5-trisphosphate + diacylglycerol
                                                                                                                    Gene Name: PLCD3
                                                                                                                    Uniprot ID: Q8N3E9 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial
                                                                                                                    Reactions:
                                                                                                                    • 3-hydroxy-2-methylpropanoyl-CoA + H2O = CoA + 3-hydroxy-2-methylpropanoate [RN:R03352]
                                                                                                                    Gene Name: HIBCH
                                                                                                                    Uniprot ID: Q6NVY1 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Carbonic anhydrase 7
                                                                                                                    Reactions:
                                                                                                                    • H2CO3 = CO2 + H2O [RN:R00132]
                                                                                                                    Gene Name: CA7
                                                                                                                    Uniprot ID: P43166 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Cholesterol 24-hydroxylase
                                                                                                                    Reactions:
                                                                                                                    • cholesterol + NADPH + H+ + O2 = (24S)-24-hydroxycholesterol + NADP+ + H2O [RN:R07207]
                                                                                                                    Gene Name: CYP46A1
                                                                                                                    Uniprot ID: Q9Y6A2 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Inorganic pyrophosphatase 2, mitochondrial
                                                                                                                    Reactions:
                                                                                                                    • diphosphate + H2O = 2 phosphate [RN:R00004]
                                                                                                                    Gene Name: PPA2
                                                                                                                    Uniprot ID: Q9H2U2 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Glucose-6-phosphatase 2
                                                                                                                    Reactions:
                                                                                                                    • D-glucose 6-phosphate + H2O = D-glucose + phosphate [RN:R00303]
                                                                                                                    Gene Name: G6PC2
                                                                                                                    Uniprot ID: Q9NQR9 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Mannosyl-oligosaccharide 1,2-alpha-mannosidase IC
                                                                                                                    Reactions:
                                                                                                                    • Hydrolysis of the terminal (1->2)-linked alpha-D-mannose residues in the oligo-mannose oligosaccharide Man9(GlcNAc)2 ALL_REAC (other) R05982(G) R06722(G)
                                                                                                                    Gene Name: MAN1C1
                                                                                                                    Uniprot ID: Q9NR34 Link_out
                                                                                                                    Protein Sequence: FASTA
                                                                                                                    Gene Sequence: FASTA
                                                                                                                    Name: Hydroxyacylglutathione hydrolase-like protein
                                                                                                                    Reactions:
                                                                                                                      Gene Name: HAGHL
                                                                                                                      Uniprot ID: Q6PII5 Link_out
                                                                                                                      Protein Sequence: FASTA
                                                                                                                      Gene Sequence: FASTA
                                                                                                                      Name: Neutral alpha-glucosidase C
                                                                                                                      Reactions:
                                                                                                                      • Hydrolysis of terminal, non-reducing (1->4)-linked alpha-D-glucose residues with release of D-glucose ALL_REAC (other) R00028 R00801 R00802 R06084(G) R06087(G) R06088(G) INHIBITOR Castanospermine [CPD:C02256]
                                                                                                                      Gene Name: GANC
                                                                                                                      Uniprot ID: Q8TET4 Link_out
                                                                                                                      Protein Sequence: FASTA
                                                                                                                      Gene Sequence: FASTA
                                                                                                                      Name: Type I inositol-3,4-bisphosphate 4-phosphatase
                                                                                                                      Reactions:
                                                                                                                      • 1-phosphatidyl-myo-inositol 3,4-bisphosphate + H2O = 1-phosphatidyl-1D-myo-inositol 3-phosphate + phosphate [RN:R07299]
                                                                                                                      Gene Name: INPP4A
                                                                                                                      Uniprot ID: Q96PE3 Link_out
                                                                                                                      Protein Sequence: FASTA
                                                                                                                      Gene Sequence: FASTA
                                                                                                                      Name: Sphingomyelin phosphodiesterase 3
                                                                                                                      Reactions:
                                                                                                                      • sphingomyelin + H2O = N-acylsphingosine + choline phosphate [RN:R02541]
                                                                                                                      Gene Name: SMPD3
                                                                                                                      Uniprot ID: Q9NY59 Link_out
                                                                                                                      Protein Sequence: FASTA
                                                                                                                      Gene Sequence: FASTA
                                                                                                                      Name: Cytochrome c oxidase subunit 2
                                                                                                                      Reactions:
                                                                                                                        Gene Name: MT-CO2
                                                                                                                        Uniprot ID: P00403 Link_out
                                                                                                                        Protein Sequence: FASTA
                                                                                                                        Gene Sequence: FASTA
                                                                                                                        Name: Cytochrome c oxidase subunit 6A1, mitochondrial
                                                                                                                        Reactions:
                                                                                                                          Gene Name: COX6A1
                                                                                                                          Uniprot ID: P12074 Link_out
                                                                                                                          Protein Sequence: FASTA
                                                                                                                          Gene Sequence: FASTA
                                                                                                                          Name: Cytochrome c oxidase subunit 4 isoform 2, mitochondrial
                                                                                                                          Reactions:
                                                                                                                            Gene Name: COX4I2
                                                                                                                            Uniprot ID: Q96KJ9 Link_out
                                                                                                                            Protein Sequence: FASTA
                                                                                                                            Gene Sequence: FASTA
                                                                                                                            Name: Cytochrome P450 4A22
                                                                                                                            Reactions:
                                                                                                                            • octane + reduced rubredoxin + O2 = 1-octanol + oxidized rubredoxin + H2O [RN:R02879]
                                                                                                                            Gene Name: CYP4A22
                                                                                                                            Uniprot ID: Q5TCH4 Link_out
                                                                                                                            Protein Sequence: FASTA
                                                                                                                            Gene Sequence: FASTA
                                                                                                                            Name: Stearoyl-CoA desaturase 5
                                                                                                                            Reactions:
                                                                                                                            • stearoyl-CoA + 2 ferrocytochrome b5 + O2 + 2 H+ = oleoyl-CoA + 2 ferricytochrome b5 + 2 H2O [RN:R02222]
                                                                                                                            Gene Name: SCD5
                                                                                                                            Uniprot ID: Q86SK9 Link_out
                                                                                                                            Protein Sequence: FASTA
                                                                                                                            Gene Sequence: FASTA
                                                                                                                            Name: Probable phospholipid-transporting ATPase ID
                                                                                                                            Reactions:
                                                                                                                            • ATP + H2O + phospholipidin = ADP + phosphate + phospholipidout [RN:R00086]
                                                                                                                            Gene Name: ATP8B2
                                                                                                                            Uniprot ID: P98198 Link_out
                                                                                                                            Protein Sequence: FASTA
                                                                                                                            Gene Sequence: FASTA
                                                                                                                            Name: Lysophosphatidic acid phosphatase type 6
                                                                                                                            Reactions:
                                                                                                                            • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
                                                                                                                            Gene Name: ACP6
                                                                                                                            Uniprot ID: Q9NPH0 Link_out
                                                                                                                            Protein Sequence: FASTA
                                                                                                                            Gene Sequence: FASTA
                                                                                                                            Name: N-acylneuraminate-9-phosphatase
                                                                                                                            Reactions:
                                                                                                                            • N-acylneuraminate 9-phosphate + H2O = N-acylneuraminate + phosphate [RN:R02597]
                                                                                                                            Gene Name: NANP
                                                                                                                            Uniprot ID: Q8TBE9 Link_out
                                                                                                                            Protein Sequence: FASTA
                                                                                                                            Gene Sequence: FASTA
                                                                                                                            Name: Gamma-glutamyltransferase 6
                                                                                                                            Reactions:
                                                                                                                            • (5-L-glutamyl)-peptide + an amino acid = peptide + 5-L-glutamyl amino acid [RN:R04159]
                                                                                                                            Gene Name: GGT6
                                                                                                                            Uniprot ID: Q6P531 Link_out
                                                                                                                            Protein Sequence: FASTA
                                                                                                                            Gene Sequence: FASTA
                                                                                                                            Name: Putative uncharacterized protein DKFZp686B0215
                                                                                                                            Reactions:
                                                                                                                              Gene Name: DKFZp686B0215
                                                                                                                              Uniprot ID: Q5HYI4 Link_out
                                                                                                                              Protein Sequence: FASTA
                                                                                                                              Gene Sequence: FASTA
                                                                                                                              Name: Fumarate hydratase
                                                                                                                              Reactions:
                                                                                                                                Gene Name: FH
                                                                                                                                Uniprot ID: B1ANK7 Link_out
                                                                                                                                Protein Sequence: FASTA
                                                                                                                                Gene Sequence: FASTA
                                                                                                                                Name: Monofunctional C1-tetrahydrofolate synthase, mitochondrial
                                                                                                                                Reactions:
                                                                                                                                • ATP + formate + tetrahydrofolate = ADP + phosphate + 10-formyltetrahydrofolate [RN:R00943]
                                                                                                                                Gene Name: MTHFD1L
                                                                                                                                Uniprot ID: Q6UB35 Link_out
                                                                                                                                Protein Sequence: FASTA
                                                                                                                                Gene Sequence: FASTA
                                                                                                                                Name: Methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase
                                                                                                                                Reactions:
                                                                                                                                  Gene Name: MTHFD2
                                                                                                                                  Uniprot ID: Q7Z650 Link_out
                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                  Name: Glycerophosphodiester phosphodiesterase 1
                                                                                                                                  Reactions:
                                                                                                                                  • 1-(sn-glycero-3-phospho)-1D-myo-inositol + H2O = myo-inositol + sn-glycerol 3-phosphate [RN:R01193]
                                                                                                                                  Gene Name: GDE1
                                                                                                                                  Uniprot ID: Q9NZC3 Link_out
                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                  Name: Probable arylformamidase
                                                                                                                                  Reactions:
                                                                                                                                  • N-formyl-L-kynurenine + H2O = formate + L-kynurenine [RN:R01959]
                                                                                                                                  Gene Name: AFMID
                                                                                                                                  Uniprot ID: Q63HM1 Link_out
                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                  Name: Multiple inositol polyphosphate phosphatase 1
                                                                                                                                  Reactions:
                                                                                                                                  • myo-inositol hexakisphosphate + H2O = myo-inositol pentakisphosphate (mixed isomers) + phosphate [RN:R07584]
                                                                                                                                  Gene Name: MINPP1
                                                                                                                                  Uniprot ID: Q9UNW1 Link_out
                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                  Name: Protein-tyrosine phosphatase mitochondrial 1
                                                                                                                                  Reactions:
                                                                                                                                  • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                  Gene Name: PTPMT1
                                                                                                                                  Uniprot ID: Q8WUK0 Link_out
                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                  Name: Acyl-CoA synthetase family member 4
                                                                                                                                  Reactions:
                                                                                                                                    Gene Name: AASDH
                                                                                                                                    Uniprot ID: Q4L235 Link_out
                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                    Name: Aminoadipate-semialdehyde synthase
                                                                                                                                    Reactions:
                                                                                                                                      Gene Name: AASS
                                                                                                                                      Uniprot ID: A4D0W4 Link_out
                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                      Name: Peroxisomal NADH pyrophosphatase NUDT12
                                                                                                                                      Reactions:
                                                                                                                                      • NAD+ + H2O = AMP + NMN [RN:R00103]
                                                                                                                                      Gene Name: NUDT12
                                                                                                                                      Uniprot ID: Q9BQG2 Link_out
                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                      Name: Ribonucleoside-diphosphate reductase subunit M2 B
                                                                                                                                      Reactions:
                                                                                                                                      • 2'-deoxyribonucleoside diphosphate + thioredoxin disulfide + H2O = ribonucleoside diphosphate + thioredoxin [RN:R04294]
                                                                                                                                      Gene Name: RRM2B
                                                                                                                                      Uniprot ID: Q7LG56 Link_out
                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                      Name: Inosine-5'-monophosphate dehydrogenase
                                                                                                                                      Reactions:
                                                                                                                                      • inosine 5'-phosphate + NAD+ + H2O = xanthosine 5'-phosphate + NADH + H+ [RN:R01130]
                                                                                                                                      Gene Name: IMPDH1
                                                                                                                                      Uniprot ID: A4D0Z6 Link_out
                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                      Name: Cytochrome P450, family 1, subfamily A, polypeptide 1
                                                                                                                                      Reactions:
                                                                                                                                        Gene Name: CYP1A1
                                                                                                                                        Uniprot ID: A0N0X8 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Ectonucleoside triphosphate diphosphohydrolase 8
                                                                                                                                        Reactions:
                                                                                                                                        • ATP + 2 H2O = AMP + 2 phosphate [RN:R00085]
                                                                                                                                        Gene Name: ENTPD8
                                                                                                                                        Uniprot ID: Q5MY95 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Serine/threonine-protein phosphatase 2B catalytic subunit alpha isoform
                                                                                                                                        Reactions:
                                                                                                                                        • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                        Gene Name: PPP3CA
                                                                                                                                        Uniprot ID: Q08209 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Serine/threonine-protein phosphatase 2B catalytic subunit beta isoform
                                                                                                                                        Reactions:
                                                                                                                                        • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                        Gene Name: PPP3CB
                                                                                                                                        Uniprot ID: P16298 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Serine/threonine-protein phosphatase 2B catalytic subunit gamma isoform
                                                                                                                                        Reactions:
                                                                                                                                        • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                        Gene Name: PPP3CC
                                                                                                                                        Uniprot ID: P48454 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Serine/threonine-protein phosphatase with EF-hands 1
                                                                                                                                        Reactions:
                                                                                                                                        • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                        Gene Name: PPEF1
                                                                                                                                        Uniprot ID: O14829 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Serine/threonine-protein phosphatase with EF-hands 2
                                                                                                                                        Reactions:
                                                                                                                                        • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                        Gene Name: PPEF2
                                                                                                                                        Uniprot ID: O14830 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Protein tyrosine phosphatase type IVA 3
                                                                                                                                        Reactions:
                                                                                                                                        • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                        Gene Name: PTP4A3
                                                                                                                                        Uniprot ID: O75365 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Protein prune homolog
                                                                                                                                        Reactions:
                                                                                                                                        • diphosphate + H2O = 2 phosphate [RN:R00004]
                                                                                                                                        Gene Name: PRUNE
                                                                                                                                        Uniprot ID: Q86TP1 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Tyrosine-protein phosphatase non-receptor type 7
                                                                                                                                        Reactions:
                                                                                                                                        • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                        Gene Name: PTPN7
                                                                                                                                        Uniprot ID: P35236 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Prenylcysteine oxidase 1
                                                                                                                                        Reactions:
                                                                                                                                        • an S-prenyl-L-cysteine + O2 + H2O = a prenal + L-cysteine + H2O2 [RN:R07360]
                                                                                                                                        Gene Name: PCYOX1
                                                                                                                                        Uniprot ID: Q9UHG3 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 2, mitochondrial
                                                                                                                                        Reactions:
                                                                                                                                        • [pyruvate dehydrogenase (acetyl-transferring)] phosphate + H2O = [pyruvate dehydrogenase (acetyl-transferring)] + phosphate [RN:R03450]
                                                                                                                                        Gene Name: PDP2
                                                                                                                                        Uniprot ID: Q9P2J9 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Sulfhydryl oxidase 1
                                                                                                                                        Reactions:
                                                                                                                                        • 4 R'C(R)SH + O2 = 2 R'C(R)S-S(R)CR' + 2 H2O [RN:R00057]
                                                                                                                                        Gene Name: QSOX1
                                                                                                                                        Uniprot ID: O00391 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Sulfhydryl oxidase 2
                                                                                                                                        Reactions:
                                                                                                                                        • 4 R'C(R)SH + O2 = 2 R'C(R)S-S(R)CR' + 2 H2O [RN:R00057]
                                                                                                                                        Gene Name: QSOX2
                                                                                                                                        Uniprot ID: Q6ZRP7 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Dynamin-1-like protein
                                                                                                                                        Reactions:
                                                                                                                                        • GTP + H2O = GDP + phosphate [RN:R00335]
                                                                                                                                        Gene Name: DNM1L
                                                                                                                                        Uniprot ID: O00429 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Dynamin-1
                                                                                                                                        Reactions:
                                                                                                                                        • GTP + H2O = GDP + phosphate [RN:R00335]
                                                                                                                                        Gene Name: DNM1
                                                                                                                                        Uniprot ID: Q05193 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Dynamin-2
                                                                                                                                        Reactions:
                                                                                                                                        • GTP + H2O = GDP + phosphate [RN:R00335]
                                                                                                                                        Gene Name: DNM2
                                                                                                                                        Uniprot ID: P50570 Link_out
                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                        Name: Elongation factor G, mitochondrial
                                                                                                                                        Reactions:
                                                                                                                                          Gene Name: GFM1
                                                                                                                                          Uniprot ID: Q96RP9 Link_out
                                                                                                                                          Protein Sequence: FASTA
                                                                                                                                          Gene Sequence: FASTA
                                                                                                                                          Name: Ribosome-releasing factor 2, mitochondrial
                                                                                                                                          Reactions:
                                                                                                                                            Gene Name: GFM2
                                                                                                                                            Uniprot ID: Q969S9 Link_out
                                                                                                                                            Protein Sequence: FASTA
                                                                                                                                            Gene Sequence: FASTA
                                                                                                                                            Name: Elongation factor Tu, mitochondrial
                                                                                                                                            Reactions:
                                                                                                                                              Gene Name: TUFM
                                                                                                                                              Uniprot ID: P49411 Link_out
                                                                                                                                              Protein Sequence: FASTA
                                                                                                                                              Gene Sequence: FASTA
                                                                                                                                              Name: Elongation factor Tu GTP-binding domain-containing protein 1
                                                                                                                                              Reactions:
                                                                                                                                                Gene Name: EFTUD1
                                                                                                                                                Uniprot ID: Q7Z2Z2 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Ferritin heavy chain
                                                                                                                                                Reactions:
                                                                                                                                                • 4 Fe(II) + 4 H+ + O2 = 4 Fe(III) + 2 H2O [RN:R00078]
                                                                                                                                                Gene Name: FTH1
                                                                                                                                                Uniprot ID: P02794 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Probable imidazolonepropionase
                                                                                                                                                Reactions:
                                                                                                                                                • (S)-3-(5-oxo-4,5-dihydro-3H-imidazol-4-yl)propanoate + H2O = N-formimidoyl-L-glutamate + H+ [RN:R02288]
                                                                                                                                                Gene Name: AMDHD1
                                                                                                                                                Uniprot ID: Q96NU7 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Serine/threonine-protein phosphatase PP1-alpha catalytic subunit
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPP1CA
                                                                                                                                                Uniprot ID: P62136 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Serine/threonine-protein phosphatase 2A catalytic subunit beta isoform
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPP2CB
                                                                                                                                                Uniprot ID: P62714 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Serine/threonine-protein phosphatase 4 catalytic subunit
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPP4C
                                                                                                                                                Uniprot ID: P60510 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Serine/threonine-protein phosphatase 5
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPP5C
                                                                                                                                                Uniprot ID: P53041 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Serine/threonine-protein phosphatase 6 catalytic subunit
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPP6C
                                                                                                                                                Uniprot ID: O00743 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Enolase-phosphatase E1
                                                                                                                                                Reactions:
                                                                                                                                                • (1) 5-(methylthio)-2,3-dioxopentyl phosphate + H2O = 1,2-dihydroxy-5-(methylthio)pent-1-en-3-one + phosphate (overall reaction) [RN:R07395]
                                                                                                                                                • (2) (1a) 5-(methylthio)-2,3-dioxopentyl phosphate = 2-hydroxy-5-(methylthio)-3-oxopent-1-enyl phosphate (probably spontaneous) [RN:R07393]
                                                                                                                                                • (3) (1b) 2-hydroxy-5-(methylthio)-3-oxopent-1-enyl phosphate + H2O = 1,2-dihydroxy-5-(methylthio)pent-1-en-3-one + phosphate [RN:R07394]
                                                                                                                                                Gene Name: ENOPH1
                                                                                                                                                Uniprot ID: Q9UHY7 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Eyes absent homolog 1
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: EYA1
                                                                                                                                                Uniprot ID: Q99502 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Eyes absent homolog 2
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: EYA2
                                                                                                                                                Uniprot ID: O00167 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Eyes absent homolog 3
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: EYA3
                                                                                                                                                Uniprot ID: Q99504 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Sphingomyelin phosphodiesterase 4
                                                                                                                                                Reactions:
                                                                                                                                                • sphingomyelin + H2O = N-acylsphingosine + choline phosphate [RN:R02541]
                                                                                                                                                Gene Name: SMPD4
                                                                                                                                                Uniprot ID: Q9NXE4 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Diphosphoinositol polyphosphate phosphohydrolase 3-beta
                                                                                                                                                Reactions:
                                                                                                                                                • diphospho-myo-inositol polyphosphate + H2O = myo-inositol polyphosphate + phosphate [RN:R05777]
                                                                                                                                                Gene Name: NUDT11
                                                                                                                                                Uniprot ID: Q96G61 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Diphosphoinositol polyphosphate phosphohydrolase 1
                                                                                                                                                Reactions:
                                                                                                                                                • diphospho-myo-inositol polyphosphate + H2O = myo-inositol polyphosphate + phosphate [RN:R05777]
                                                                                                                                                Gene Name: NUDT3
                                                                                                                                                Uniprot ID: O95989 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Diphosphoinositol polyphosphate phosphohydrolase 2
                                                                                                                                                Reactions:
                                                                                                                                                • diphospho-myo-inositol polyphosphate + H2O = myo-inositol polyphosphate + phosphate [RN:R05777]
                                                                                                                                                Gene Name: NUDT4
                                                                                                                                                Uniprot ID: Q9NZJ9 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: [Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 1, mitochondrial
                                                                                                                                                Reactions:
                                                                                                                                                • [pyruvate dehydrogenase (acetyl-transferring)] phosphate + H2O = [pyruvate dehydrogenase (acetyl-transferring)] + phosphate [RN:R03450]
                                                                                                                                                Gene Name: PDP1
                                                                                                                                                Uniprot ID: Q9P0J1 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein phosphatase 1A
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPM1A
                                                                                                                                                Uniprot ID: P35813 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein phosphatase 1B
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPM1B
                                                                                                                                                Uniprot ID: O75688 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein phosphatase 1D
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPM1D
                                                                                                                                                Uniprot ID: O15297 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein phosphatase 1E
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPM1E
                                                                                                                                                Uniprot ID: Q8WY54 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein phosphatase 1F
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPM1F
                                                                                                                                                Uniprot ID: P49593 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein phosphatase 1G
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPM1G
                                                                                                                                                Uniprot ID: O15355 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein phosphatase 1M
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PPM1M
                                                                                                                                                Uniprot ID: Q96MI6 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Ubiquitin-like domain-containing CTD phosphatase 1
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: UBLCP1
                                                                                                                                                Uniprot ID: Q8WVY7 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 18
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP18
                                                                                                                                                Uniprot ID: Q8NEJ0 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: PH domain leucine-rich repeat-containing protein phosphatase 2
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PHLPP2
                                                                                                                                                Uniprot ID: Q6ZVD8 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: PH domain leucine-rich repeat-containing protein phosphatase 1
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: PHLPP1
                                                                                                                                                Uniprot ID: O60346 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase CDC14A
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: CDC14A
                                                                                                                                                Uniprot ID: Q9UNH5 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase CDC14B
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: CDC14B
                                                                                                                                                Uniprot ID: O60729 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Cyclin-dependent kinase inhibitor 3
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: CDKN3
                                                                                                                                                Uniprot ID: Q16667 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: RNA polymerase II subunit A C-terminal domain phosphatase
                                                                                                                                                Reactions:
                                                                                                                                                • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                Gene Name: CTDP1
                                                                                                                                                Uniprot ID: Q9Y5B0 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 10
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP10
                                                                                                                                                Uniprot ID: Q9Y6W6 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 12
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP12
                                                                                                                                                Uniprot ID: Q9UNI6 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 13
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP13
                                                                                                                                                Uniprot ID: Q9UII6 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 16
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP16
                                                                                                                                                Uniprot ID: Q9BY84 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 19
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP19
                                                                                                                                                Uniprot ID: Q8WTR2 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 1
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP1
                                                                                                                                                Uniprot ID: P28562 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 3
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP3
                                                                                                                                                Uniprot ID: P51452 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 4
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP4
                                                                                                                                                Uniprot ID: Q13115 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 5
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP5
                                                                                                                                                Uniprot ID: Q16690 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 6
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP6
                                                                                                                                                Uniprot ID: Q16828 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 7
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP7
                                                                                                                                                Uniprot ID: Q16829 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Dual specificity protein phosphatase 8
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: DUSP8
                                                                                                                                                Uniprot ID: Q13202 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: M-phase inducer phosphatase 1
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: CDC25A
                                                                                                                                                Uniprot ID: P30304 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: M-phase inducer phosphatase 3
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: CDC25C
                                                                                                                                                Uniprot ID: P30307 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 11
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN11
                                                                                                                                                Uniprot ID: Q06124 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 14
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN14
                                                                                                                                                Uniprot ID: Q15678 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 18
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN18
                                                                                                                                                Uniprot ID: Q99952 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 21
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN21
                                                                                                                                                Uniprot ID: Q16825 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 22
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN22
                                                                                                                                                Uniprot ID: Q9Y2R2 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 2
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN2
                                                                                                                                                Uniprot ID: P17706 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 3
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN3
                                                                                                                                                Uniprot ID: P26045 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 4
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN4
                                                                                                                                                Uniprot ID: P29074 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Tyrosine-protein phosphatase non-receptor type 9
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPN9
                                                                                                                                                Uniprot ID: P43378 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase N2
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRN2
                                                                                                                                                Uniprot ID: Q92932 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase epsilon
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRE
                                                                                                                                                Uniprot ID: P23469 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase F
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRF
                                                                                                                                                Uniprot ID: P10586 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase gamma
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRG
                                                                                                                                                Uniprot ID: P23470 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase eta
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRJ
                                                                                                                                                Uniprot ID: Q12913 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase kappa
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRK
                                                                                                                                                Uniprot ID: Q15262 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase O
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRO
                                                                                                                                                Uniprot ID: Q16827 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase R
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRR
                                                                                                                                                Uniprot ID: Q15256 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase U
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRU
                                                                                                                                                Uniprot ID: Q92729 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Receptor-type tyrosine-protein phosphatase zeta
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTPRZ1
                                                                                                                                                Uniprot ID: P23471 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein tyrosine phosphatase type IVA 1
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTP4A1
                                                                                                                                                Uniprot ID: Q93096 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Protein tyrosine phosphatase type IVA 2
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: PTP4A2
                                                                                                                                                Uniprot ID: Q12974 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Putative tyrosine-protein phosphatase TPTE
                                                                                                                                                Reactions:
                                                                                                                                                • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                Gene Name: TPTE
                                                                                                                                                Uniprot ID: P56180 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Cytosolic phospholipase A2 beta
                                                                                                                                                Reactions:
                                                                                                                                                • phosphatidylcholine + H2O = 1-acylglycerophosphocholine + a carboxylate [RN:R01313]
                                                                                                                                                Gene Name: PLA2G4B
                                                                                                                                                Uniprot ID: P0C869 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Alkaline ceramidase 2
                                                                                                                                                Reactions:
                                                                                                                                                • N-acylsphingosine + H2O = a carboxylate + sphingosine [RN:R01493]
                                                                                                                                                Gene Name: ACER2
                                                                                                                                                Uniprot ID: Q5QJU3 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Deoxyhypusine hydroxylase
                                                                                                                                                Reactions:
                                                                                                                                                • protein N6-(4-aminobutyl)-L-lysine + AH2 + O2 = protein N6-[(R)-4-amino-2-hydroxybutyl]-L-lysine + A + H2O [RN:R04437]
                                                                                                                                                Gene Name: DOHH
                                                                                                                                                Uniprot ID: Q9BU89 Link_out
                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                Name: Cytochrome P450, family 21, subfamily A, polypeptide 2
                                                                                                                                                Reactions:
                                                                                                                                                  Gene Name: CYP21A2
                                                                                                                                                  Uniprot ID: Q08AG9 Link_out
                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                  Name: Glucosamine-6-phosphate isomerase 2
                                                                                                                                                  Reactions:
                                                                                                                                                  • D-glucosamine 6-phosphate + H2O = D-fructose 6-phosphate + NH3 [RN:R00765]
                                                                                                                                                  Gene Name: GNPDA2
                                                                                                                                                  Uniprot ID: Q8TDQ7 Link_out
                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                  Name: Cytochrome P450 2D6
                                                                                                                                                  Reactions:
                                                                                                                                                    Gene Name: CYP2D6
                                                                                                                                                    Uniprot ID: Q6NWU0 Link_out
                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                    Name: GGT7 protein
                                                                                                                                                    Reactions:
                                                                                                                                                      Gene Name: GGT7
                                                                                                                                                      Uniprot ID: A0PJJ9 Link_out
                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                      Name: Gamma-glutamyltransferase 5
                                                                                                                                                      Reactions:
                                                                                                                                                        Gene Name: GGT5
                                                                                                                                                        Uniprot ID: P36269 Link_out
                                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                                        Name: Phospholipase D1 variant
                                                                                                                                                        Reactions:
                                                                                                                                                          Gene Name: Not Available
                                                                                                                                                          Uniprot ID: Q59EA4 Link_out
                                                                                                                                                          Protein Sequence: FASTA
                                                                                                                                                          Gene Sequence: FASTA
                                                                                                                                                          Name: Glutathione S-transferase kappa 1
                                                                                                                                                          Reactions:
                                                                                                                                                            Gene Name: LOC51064
                                                                                                                                                            Uniprot ID: Q6FII1 Link_out
                                                                                                                                                            Protein Sequence: FASTA
                                                                                                                                                            Gene Sequence: FASTA
                                                                                                                                                            Name: Peptidoglycan recognition protein 3
                                                                                                                                                            Reactions:
                                                                                                                                                              Gene Name: PGLYRP3
                                                                                                                                                              Uniprot ID: Q96LB9 Link_out
                                                                                                                                                              Protein Sequence: FASTA
                                                                                                                                                              Gene Sequence: FASTA
                                                                                                                                                              Name: Peptidoglycan recognition protein 4 (PGLYRP4 protein)
                                                                                                                                                              Reactions:
                                                                                                                                                                Gene Name: PGLYRP4
                                                                                                                                                                Uniprot ID: Q96LB8 Link_out
                                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                                Name: Hyaluronidase-1
                                                                                                                                                                Reactions:
                                                                                                                                                                • Random hydrolysis of (1->4)-linkages between N-acetyl-beta-D-glucosamine and D-glucuronate residues in hyaluronate ALL_REAC (other) R07824(G) R07825(G)
                                                                                                                                                                Gene Name: HYAL1
                                                                                                                                                                Uniprot ID: Q12794 Link_out
                                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                                Name: Sperm adhesion molecule 1 (PH-20 hyaluronidase, zona pellucida binding)
                                                                                                                                                                Reactions:
                                                                                                                                                                  Gene Name: SPAM1
                                                                                                                                                                  Uniprot ID: P38567 Link_out
                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                  Name: Hyaluronidase-2
                                                                                                                                                                  Reactions:
                                                                                                                                                                  • Random hydrolysis of (1->4)-linkages between N-acetyl-beta-D-glucosamine and D-glucuronate residues in hyaluronate ALL_REAC (other) R07824(G) R07825(G)
                                                                                                                                                                  Gene Name: HYAL2
                                                                                                                                                                  Uniprot ID: Q12891 Link_out
                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                  Name: NEU1 protein
                                                                                                                                                                  Reactions:
                                                                                                                                                                    Gene Name: NEU1
                                                                                                                                                                    Uniprot ID: Q5JQI0 Link_out
                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                    Name: Testicular acid phosphatase
                                                                                                                                                                    Reactions:
                                                                                                                                                                    • a phosphate monoester + H2O = an alcohol + phosphate [RN:R00626]
                                                                                                                                                                    Gene Name: ACPT
                                                                                                                                                                    Uniprot ID: Q9BZG2 Link_out
                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                    Name: Dual specificity protein phosphatase 14
                                                                                                                                                                    Reactions:
                                                                                                                                                                    • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                                    Gene Name: DUSP14
                                                                                                                                                                    Uniprot ID: O95147 Link_out
                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                    Name: Putative uncharacterized protein DUSP15
                                                                                                                                                                    Reactions:
                                                                                                                                                                      Gene Name: DUSP15
                                                                                                                                                                      Uniprot ID: Q9H1R2 Link_out
                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                      Name: Serine/threonine-protein phosphatase 2A regulatory subunit B'' subunit beta
                                                                                                                                                                      Reactions:
                                                                                                                                                                        Gene Name: PPP2R3B
                                                                                                                                                                        Uniprot ID: Q9Y5P8 Link_out
                                                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                                                        Name: Carboxy-terminal domain RNA polymerase II polypeptide A small phosphatase 1
                                                                                                                                                                        Reactions:
                                                                                                                                                                        • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                                        Gene Name: CTDSP1
                                                                                                                                                                        Uniprot ID: Q9GZU7 Link_out
                                                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                                                        Name: Dual specificity protein phosphatase 21
                                                                                                                                                                        Reactions:
                                                                                                                                                                        • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                                        Gene Name: DUSP21
                                                                                                                                                                        Uniprot ID: Q9H596 Link_out
                                                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                                                        Name: Putative uncharacterized protein DKFZp686I0955
                                                                                                                                                                        Reactions:
                                                                                                                                                                          Gene Name: DKFZp686I0955
                                                                                                                                                                          Uniprot ID: Q5HYC3 Link_out
                                                                                                                                                                          Protein Sequence: FASTA
                                                                                                                                                                          Gene Sequence: FASTA
                                                                                                                                                                          Name: T-cell, immune regulator 1, ATPase, H+ transporting, lysosomal V0 subunit A3 (T-cell, immune regulator 1, ATPase, H+ transporting, lysosomal V0 subunit A3, isoform CRA_c)
                                                                                                                                                                          Reactions:
                                                                                                                                                                            Gene Name: TCIRG1
                                                                                                                                                                            Uniprot ID: Q13488 Link_out
                                                                                                                                                                            Protein Sequence: FASTA
                                                                                                                                                                            Gene Sequence: FASTA
                                                                                                                                                                            Name: V-type proton ATPase subunit e 2
                                                                                                                                                                            Reactions:
                                                                                                                                                                              Gene Name: ATP6V0E2
                                                                                                                                                                              Uniprot ID: Q8NHE4 Link_out
                                                                                                                                                                              Protein Sequence: FASTA
                                                                                                                                                                              Gene Sequence: FASTA
                                                                                                                                                                              Name: Putative uncharacterized protein ATP6V1E1
                                                                                                                                                                              Reactions:
                                                                                                                                                                                Gene Name: ATP6V1E1
                                                                                                                                                                                Uniprot ID: P36543 Link_out
                                                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                                                Name: Vacuolar-type H(+)-ATPase
                                                                                                                                                                                Reactions:
                                                                                                                                                                                  Gene Name: Not Available
                                                                                                                                                                                  Uniprot ID: Q53X12 Link_out
                                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                                  Name: ATPase, H+ transporting, lysosomal accessory protein 1 (ATPase, H+ transporting, lysosomal accessory protein 1, isoform CRA_d) (cDNA FLJ78461, highly similar to Homo sapiens ATPase, H+ transporting, lysosomal accessory protein 1 (ATP6AP1), mRNA) (Fragment
                                                                                                                                                                                  Reactions:
                                                                                                                                                                                    Gene Name: ATP6AP1
                                                                                                                                                                                    Uniprot ID: Q15904 Link_out
                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                    Name: ATPase, H+ transporting, lysosomal 14kDa, V1 subunit F
                                                                                                                                                                                    Reactions:
                                                                                                                                                                                      Gene Name: ATP6V1F
                                                                                                                                                                                      Uniprot ID: A4D1K0 Link_out
                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                      Name: CP protein
                                                                                                                                                                                      Reactions:
                                                                                                                                                                                        Gene Name: CP
                                                                                                                                                                                        Uniprot ID: A5PL27 Link_out
                                                                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                                                                        Name: Carbonic anhydrase 6
                                                                                                                                                                                        Reactions:
                                                                                                                                                                                        • H2CO3 = CO2 + H2O [RN:R00132]
                                                                                                                                                                                        Gene Name: CA6
                                                                                                                                                                                        Uniprot ID: P23280 Link_out
                                                                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                                                                        Name: Protein tyrosine phosphatase domain-containing protein 1
                                                                                                                                                                                        Reactions:
                                                                                                                                                                                          Gene Name: PTPDC1
                                                                                                                                                                                          Uniprot ID: A2A3K4 Link_out
                                                                                                                                                                                          Protein Sequence: FASTA
                                                                                                                                                                                          Gene Sequence: FASTA
                                                                                                                                                                                          Name: Protein tyrosine phosphatase receptor type D
                                                                                                                                                                                          Reactions:
                                                                                                                                                                                            Gene Name: PTPRD
                                                                                                                                                                                            Uniprot ID: Q2HXI4 Link_out
                                                                                                                                                                                            Protein Sequence: FASTA
                                                                                                                                                                                            Gene Sequence: FASTA
                                                                                                                                                                                            Name: Receptor-type tyrosine-protein phosphatase H
                                                                                                                                                                                            Reactions:
                                                                                                                                                                                            • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                                                            Gene Name: PTPRH
                                                                                                                                                                                            Uniprot ID: Q9HD43 Link_out
                                                                                                                                                                                            Protein Sequence: FASTA
                                                                                                                                                                                            Gene Sequence: FASTA
                                                                                                                                                                                            Name: PTPRM protein
                                                                                                                                                                                            Reactions:
                                                                                                                                                                                              Gene Name: PTPRM
                                                                                                                                                                                              Uniprot ID: A7MBN1 Link_out
                                                                                                                                                                                              Protein Sequence: FASTA
                                                                                                                                                                                              Gene Sequence: FASTA
                                                                                                                                                                                              Name: Receptor-type tyrosine-protein phosphatase-like N
                                                                                                                                                                                              Reactions:
                                                                                                                                                                                                Gene Name: PTPRN
                                                                                                                                                                                                Uniprot ID: Q16849 Link_out
                                                                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                                                                Name: Protein tyrosine phosphatase, receptor type, sigma isoform 3 variant
                                                                                                                                                                                                Reactions:
                                                                                                                                                                                                  Gene Name: Not Available
                                                                                                                                                                                                  Uniprot ID: Q59FX6 Link_out
                                                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                                                  Name: Carboxylesterase 7
                                                                                                                                                                                                  Reactions:
                                                                                                                                                                                                  • a carboxylic ester + H2O = an alcohol + a carboxylate [RN:R00630]
                                                                                                                                                                                                  Gene Name: CES7
                                                                                                                                                                                                  Uniprot ID: Q6NT32 Link_out
                                                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                                                  Name: Peroxiredoxin-4
                                                                                                                                                                                                  Reactions:
                                                                                                                                                                                                  • 2 R'-SH + ROOH = R'-S-S-R' + H2O + ROH [RN:R07180]
                                                                                                                                                                                                  Gene Name: PRDX4
                                                                                                                                                                                                  Uniprot ID: Q13162 Link_out
                                                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                                                  Name: Carboxymethylenebutenolidase homolog
                                                                                                                                                                                                  Reactions:
                                                                                                                                                                                                    Gene Name: CMBL
                                                                                                                                                                                                    Uniprot ID: Q96DG6 Link_out
                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                    Name: Ubiquitin carboxyl-terminal hydrolase 16
                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                    • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                    Gene Name: USP16
                                                                                                                                                                                                    Uniprot ID: Q9Y5T5 Link_out
                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                    Name: STAM-binding protein
                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                      Gene Name: STAMBP
                                                                                                                                                                                                      Uniprot ID: O95630 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • ubiquitin C-terminal thioester + H2O = ubiquitin + a thiol [RN:R02418]
                                                                                                                                                                                                      Gene Name: Em:AC008079.1
                                                                                                                                                                                                      Uniprot ID: Q53Y90 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 51
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP51
                                                                                                                                                                                                      Uniprot ID: Q70EK9 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 33
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP33
                                                                                                                                                                                                      Uniprot ID: Q8TEY7 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 22
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP22
                                                                                                                                                                                                      Uniprot ID: Q9UPT9 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 47
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP47
                                                                                                                                                                                                      Uniprot ID: Q96K76 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 40
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP40
                                                                                                                                                                                                      Uniprot ID: Q9NVE5 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 35
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP35
                                                                                                                                                                                                      Uniprot ID: Q9P2H5 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 36
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP36
                                                                                                                                                                                                      Uniprot ID: Q9P275 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 29
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP29
                                                                                                                                                                                                      Uniprot ID: Q9HBJ7 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 46
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP46
                                                                                                                                                                                                      Uniprot ID: P62068 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • ubiquitin C-terminal thioester + H2O = ubiquitin + a thiol [RN:R02418]
                                                                                                                                                                                                      Gene Name: USP4
                                                                                                                                                                                                      Uniprot ID: Q08AK7 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 1
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP1
                                                                                                                                                                                                      Uniprot ID: O94782 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 7
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP7
                                                                                                                                                                                                      Uniprot ID: Q93009 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 5
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP5
                                                                                                                                                                                                      Uniprot ID: P45974 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Probable ubiquitin carboxyl-terminal hydrolase FAF-X
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP9X
                                                                                                                                                                                                      Uniprot ID: Q93008 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Probable ubiquitin carboxyl-terminal hydrolase FAF-Y
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP9Y
                                                                                                                                                                                                      Uniprot ID: O00507 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 26
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP26
                                                                                                                                                                                                      Uniprot ID: Q9BXU7 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • ubiquitin C-terminal thioester + H2O = ubiquitin + a thiol [RN:R02418]
                                                                                                                                                                                                      Gene Name: USP42
                                                                                                                                                                                                      Uniprot ID: Q9H9J4 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 32
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP32
                                                                                                                                                                                                      Uniprot ID: Q8NFA0 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 30
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP30
                                                                                                                                                                                                      Uniprot ID: Q70CQ3 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 13
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP13
                                                                                                                                                                                                      Uniprot ID: Q92995 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • ubiquitin C-terminal thioester + H2O = ubiquitin + a thiol [RN:R02418]
                                                                                                                                                                                                      Gene Name: USP14
                                                                                                                                                                                                      Uniprot ID: A6NJA2 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 6
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP6
                                                                                                                                                                                                      Uniprot ID: P35125 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 10
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP10
                                                                                                                                                                                                      Uniprot ID: Q14694 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 8
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP8
                                                                                                                                                                                                      Uniprot ID: P40818 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 15
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP15
                                                                                                                                                                                                      Uniprot ID: Q9Y4E8 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Ubiquitin carboxyl-terminal hydrolase 3
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                      Gene Name: USP3
                                                                                                                                                                                                      Uniprot ID: Q9Y6I4 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Lysozyme-like protein 1
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • Hydrolysis of (1->4)-beta-linkages between N-acetylmuramic acid and N-acetyl-D-glucosamine residues in a peptidoglycan and between N-acetyl-D-glucosamine residues in chitodextrins
                                                                                                                                                                                                      Gene Name: LYZL1
                                                                                                                                                                                                      Uniprot ID: Q6UWQ5 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: Pterin-4-alpha-carbinolamine dehydratase 2
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                      • (6R)-6-(L-erythro-1,2-dihydroxypropyl)-5,6,7,8-tetrahydro-4a- hydroxypterin = (6R)-6-(L-erythro-1,2-dihydroxypropyl)-7,8-dihydro-6H-pterin + H2O [RN:R04734]
                                                                                                                                                                                                      Gene Name: PCBD2
                                                                                                                                                                                                      Uniprot ID: Q9H0N5 Link_out
                                                                                                                                                                                                      Protein Sequence: FASTA
                                                                                                                                                                                                      Gene Sequence: FASTA
                                                                                                                                                                                                      Name: NOS1 mutant
                                                                                                                                                                                                      Reactions:
                                                                                                                                                                                                        Gene Name: NOS1
                                                                                                                                                                                                        Uniprot ID: B3VK56 Link_out
                                                                                                                                                                                                        Protein Sequence: FASTA
                                                                                                                                                                                                        Gene Sequence: FASTA
                                                                                                                                                                                                        Name: Putative uncharacterized protein ACP1
                                                                                                                                                                                                        Reactions:
                                                                                                                                                                                                          Gene Name: ACP1
                                                                                                                                                                                                          Uniprot ID: B5MCC7 Link_out
                                                                                                                                                                                                          Protein Sequence: FASTA
                                                                                                                                                                                                          Gene Sequence: FASTA
                                                                                                                                                                                                          Name: Serine/threonine-protein phosphatase
                                                                                                                                                                                                          Reactions:
                                                                                                                                                                                                          • a phosphoprotein + H2O = a protein + phosphate [RN:R00164]
                                                                                                                                                                                                          Gene Name: PPP2CA
                                                                                                                                                                                                          Uniprot ID: B3KUN1 Link_out
                                                                                                                                                                                                          Protein Sequence: FASTA
                                                                                                                                                                                                          Gene Sequence: FASTA
                                                                                                                                                                                                          Name: [Protein ADP-ribosylarginine] hydrolase
                                                                                                                                                                                                          Reactions:
                                                                                                                                                                                                          • (1) protein-Nomega-(ADP-D-ribosyl)-L-arginine + H2O = ADP-ribose + protein-L-arginine [RN:R07626]
                                                                                                                                                                                                          • (2) Nomega-(ADP-D-ribosyl)-L-arginine + H2O = ADP-ribose + L-arginine [RN:R01886]
                                                                                                                                                                                                          Gene Name: ADPRH
                                                                                                                                                                                                          Uniprot ID: P54922 Link_out
                                                                                                                                                                                                          Protein Sequence: FASTA
                                                                                                                                                                                                          Gene Sequence: FASTA
                                                                                                                                                                                                          Name: Aquaporin-1
                                                                                                                                                                                                          Reactions:
                                                                                                                                                                                                            Gene Name: AQP1
                                                                                                                                                                                                            Uniprot ID: P29972 Link_out
                                                                                                                                                                                                            Protein Sequence: FASTA
                                                                                                                                                                                                            Gene Sequence: FASTA
                                                                                                                                                                                                            Name: Aquaporin-4
                                                                                                                                                                                                            Reactions:
                                                                                                                                                                                                              Gene Name: AQP4
                                                                                                                                                                                                              Uniprot ID: P55087 Link_out
                                                                                                                                                                                                              Protein Sequence: FASTA
                                                                                                                                                                                                              Gene Sequence: FASTA
                                                                                                                                                                                                              Name: Aquaporin-10
                                                                                                                                                                                                              Reactions:
                                                                                                                                                                                                                Gene Name: AQP10
                                                                                                                                                                                                                Uniprot ID: Q96PS8 Link_out
                                                                                                                                                                                                                Protein Sequence: FASTA
                                                                                                                                                                                                                Gene Sequence: FASTA
                                                                                                                                                                                                                Name: Carbonic anhydrase-related protein
                                                                                                                                                                                                                Reactions:
                                                                                                                                                                                                                  Gene Name: CA8
                                                                                                                                                                                                                  Uniprot ID: P35219 Link_out
                                                                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                                                                  Name: Ubiquitin carboxyl-terminal hydrolase 11
                                                                                                                                                                                                                  Reactions:
                                                                                                                                                                                                                  • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                  Gene Name: USP11
                                                                                                                                                                                                                  Uniprot ID: P51784 Link_out
                                                                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                                                                  Name: Ubiquitin carboxyl-terminal hydrolase 38
                                                                                                                                                                                                                  Reactions:
                                                                                                                                                                                                                  • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                  Gene Name: USP38
                                                                                                                                                                                                                  Uniprot ID: Q8NB14 Link_out
                                                                                                                                                                                                                  Protein Sequence: FASTA
                                                                                                                                                                                                                  Gene Sequence: FASTA
                                                                                                                                                                                                                  Name: L-aminoadipate-semialdehyde dehydrogenase-phosphopantetheinyl transferase
                                                                                                                                                                                                                  Reactions:
                                                                                                                                                                                                                    Gene Name: AASDHPPT
                                                                                                                                                                                                                    Uniprot ID: Q9NRN7 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Ubiquitin carboxyl-terminal hydrolase 21
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                    Gene Name: USP21
                                                                                                                                                                                                                    Uniprot ID: Q9UK80 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Ubiquitin carboxyl-terminal hydrolase 37
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                    Gene Name: USP37
                                                                                                                                                                                                                    Uniprot ID: Q86T82 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Tyrosine-protein phosphatase non-receptor type 23
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • protein tyrosine phosphate + H2O = protein tyrosine + phosphate [RN:R02585]
                                                                                                                                                                                                                    Gene Name: PTPN23
                                                                                                                                                                                                                    Uniprot ID: Q9H3S7 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Ubiquitin carboxyl-terminal hydrolase 2
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                    Gene Name: USP2
                                                                                                                                                                                                                    Uniprot ID: O75604 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Ubiquitin carboxyl-terminal hydrolase 28
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                    Gene Name: USP28
                                                                                                                                                                                                                    Uniprot ID: Q96RU2 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Glutathione S-transferase theta-2
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • RX + glutathione = HX + R-S-glutathione [RN:R03522 R08511 R08512]
                                                                                                                                                                                                                    Gene Name: GSTT2
                                                                                                                                                                                                                    Uniprot ID: P0CG29 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Ubiquitin carboxyl-terminal hydrolase 20
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                    Gene Name: USP20
                                                                                                                                                                                                                    Uniprot ID: Q9Y2K6 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: S-acyl fatty acid synthase thioesterase, medium chain
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • an oleoyl-[acyl-carrier protein] + H2O = an [acyl-carrier protein] + oleate [RN:R02814]
                                                                                                                                                                                                                    Gene Name: OLAH
                                                                                                                                                                                                                    Uniprot ID: Q9NV23 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Ubiquitin carboxyl-terminal hydrolase 25
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • Thiol-dependent hydrolysis of ester, thioester, amide, peptide and isopeptide bonds formed by the C-terminal Gly of ubiquitin (a 76-residue protein attached to proteins as an intracellular targeting signal)
                                                                                                                                                                                                                    Gene Name: USP25
                                                                                                                                                                                                                    Uniprot ID: Q9UHP3 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Transporters
                                                                                                                                                                                                                    Name: Copper-transporting ATPase 2
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • ATP + H2O + Cu2+in = ADP + phosphate + Cu2+out [RN:R00086]
                                                                                                                                                                                                                    Gene Name: ATP7B
                                                                                                                                                                                                                    Uniprot ID: P35670 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA
                                                                                                                                                                                                                    Name: Copper-transporting ATPase 1
                                                                                                                                                                                                                    Reactions:
                                                                                                                                                                                                                    • ATP + H2O + Cu2+in = ADP + phosphate + Cu2+out [RN:R00086]
                                                                                                                                                                                                                    Gene Name: ATP7A
                                                                                                                                                                                                                    Uniprot ID: Q04656 Link_out
                                                                                                                                                                                                                    Protein Sequence: FASTA
                                                                                                                                                                                                                    Gene Sequence: FASTA