| Record Information |
| Version |
3.5 |
| Creation Date |
2006-05-22 08:17:46 -0600 |
| Update Date |
2013-05-29 13:35:25 -0600 |
| HMDB ID |
HMDB02287 |
| Secondary Accession Numbers |
None |
| Metabolite Identification |
| Common Name |
Homocysteine thiolactone |
| Description |
Elevated level of the nonprotein amino acid homocysteine (Hcy) is a risk factor for cardiovascular diseases, neurodegenerative diseases, and neural tube defects. Metabolic conversion of Hcy to a chemically reactive metabolite, Hcy-thiolactone, catalyzed by methionyl-tRNA synthetase is the first step in a pathway that contributes to Hcy toxicity in humans. (PMID 16702349 ). The only known source of Hcy in the human body is dietary protein methionine; subsequent examinations of individual dietary amino acids have led to the conclusion that methionine, ingested in excess, is the most toxic amino acid. (Harper AE, Benevenga NJ, Wohlheuter RM. Effects of ingestion of disproportionate amounts of amino acids. Physiol Rev. 1970;50: 428 - 58; Benevenga NJ, Steele RD. Adverse effects of excessive consumption of amino acids. Annu Rev Nutr. 1984; 4:157-81). Animals fed high-protein or high-methionine diets for 2 years developed hyperhomocysteinemia and evidence of vascular disease (Fau D, Preret J, Hadjiisky P. Effects of ingestion of high protein or excess methionine diets by rats for two years. J Nutr. 1988; 118:128-33). |
| Structure |
Download:
MOL |
SDF |
SMILES |
InChI
Display:
2D Structure |
3D Structure
|
| Synonyms |
- ( -)-3-Amino-2-thiolanon
- ( -)-3-Aminotetrahydro-2-thiophenon
- (+-)-3-Aminodihydro-2(3H)-thiophenone
- 3-Aminodihydro-2(3H)-thiophenone
- DL-3-Aminotetrahydro-2-thiophenone
- DL-Homocysteine thiolactone
- L-Homocysteine thiolactone
|
| Chemical Formula |
C4H7NOS |
| Average Molecular Weight |
117.169 |
| Monoisotopic Molecular Weight |
117.024834541 |
| IUPAC Name |
3-aminothiolan-2-one |
| Traditional IUPAC Name |
3-aminothiolan-2-one |
| CAS Registry Number |
3622-59-1 |
| SMILES |
NC1CCSC1=O |
| InChI Identifier |
InChI=1S/C4H7NOS/c5-3-1-2-7-4(3)6/h3H,1-2,5H2 |
| InChI Key |
KIWQWJKWBHZMDT-UHFFFAOYSA-N |
| Chemical Taxonomy |
| Kingdom |
Organic Compounds |
| Super Class |
Aliphatic Heteromonocyclic Compounds |
| Class |
Thiolanes |
| Sub Class |
N/A |
| Other Descriptors |
|
| Substituents |
- Primary Aliphatic Amine (Alkylamine)
- Thiocarboxylic Acid Ester
- Thiolactone
|
| Direct Parent |
Thiolanes |
| Ontology |
| Status |
Detected and Quantified |
| Origin |
|
| Biofunction |
- Protein synthesis, amino acid biosynthesis
|
| Application |
Not Available
|
| Cellular locations |
Not Available
|
| Physical Properties |
| State |
Solid |
| Experimental Properties |
| Property |
Value |
Reference |
| Melting Point |
Not Available |
Not Available |
| Boiling Point |
Not Available |
Not Available |
| Water Solubility |
Not Available |
Not Available |
| LogP |
Not Available |
Not Available |
|
| Predicted Properties |
|
| Spectra |
|
Not Available
|
| Biological Properties |
| Cellular Locations |
Not Available
|
| Biofluid Locations |
|
| Tissue Location |
Not Available
|
| Pathways |
Not Available
|
| Normal Concentrations |
|
| Blood |
Detected and Quantified |
|
0.00282 +/- 0.00613 uM |
Adult (>18 years old) |
Both |
Normal
|
|
|
| Abnormal Concentrations |
|
Not Available |
| Associated Disorders and Diseases |
| Disease References |
None |
| Associated OMIM IDs |
None |
| External Links |
| DrugBank ID |
Not Available |
| DrugBank Metabolite ID |
Not Available |
| Phenol Explorer Compound ID |
Not Available |
| Phenol Explorer Metabolite ID |
Not Available |
| FoodDB ID |
FDB022949 |
| KNApSAcK ID |
Not Available |
| Chemspider ID |
96881  |
| KEGG Compound ID |
Not Available |
| BioCyc ID |
Not Available |
| BiGG ID |
Not Available |
| Wikipedia Link |
Not Available |
| NuGOwiki Link |
HMDB02287  |
| Metagene Link |
HMDB02287  |
| METLIN ID |
6594  |
| PubChem Compound |
107712  |
| PDB ID |
Not Available |
| ChEBI ID |
Not Available |
| References |
| Synthesis Reference |
Takehara, Jun; Ichikawa, Shuji; Iwane, Hiroshi. Preparation of DL-homocysteine thiolactone inorganic acid salts. Jpn. Kokai Tokkyo Koho (1998), 4 pp. |
| Material Safety Data Sheet (MSDS) |
Not Available
|
| General References |
- Ricci G, Santoro L, Achilli M, Matarese RM, Nardini M, Cavallini D: Similarity of the oxidation products of L-cystathionine by L-amino acid oxidase to those excreted by cystathioninuric patients. J Biol Chem. 1983 Sep 10;258(17):10511-7.
Pubmed: 6885789
- Jakubowski H: Homocysteine thiolactone: metabolic origin and protein homocysteinylation in humans. J Nutr. 2000 Feb;130(2S Suppl):377S-381S.
Pubmed: 10721911
- Jakubowski H: Protein homocysteinylation: possible mechanism underlying pathological consequences of elevated homocysteine levels. FASEB J. 1999 Dec;13(15):2277-83.
Pubmed: 10593875
- Kerkeni M, Addad F, Chauffert M, Chuniaud L, Miled A, Trivin F, Maaroufi K: Hyperhomocysteinemia, paraoxonase activity and risk of coronary artery disease. Clin Biochem. 2006 Aug;39(8):821-5. Epub 2006 Jun 7.
Pubmed: 16875684
- Chwatko G, Jakubowski H: The determination of homocysteine-thiolactone in human plasma. Anal Biochem. 2005 Feb 15;337(2):271-7.
Pubmed: 15691507
- Jakubowski H: Pathophysiological consequences of homocysteine excess. J Nutr. 2006 Jun;136(6 Suppl):1741S-1749S.
Pubmed: 16702349
|