| Record Information |
| Version |
3.5 |
| Creation Date |
2007-05-22 11:34:16 -0600 |
| Update Date |
2013-05-29 13:42:59 -0600 |
| HMDB ID |
HMDB06210 |
| Secondary Accession Numbers |
None |
| Metabolite Identification |
| Common Name |
Heptadecanoyl carnitine |
| Description |
Heptadecanoyl carnitine is an acylcarnitine. Numerous disorders have been described that lead to disturbances in energy production and in intermediary metabolism in the organism which are characterized by the production and excretion of unusual acylcarnitines. A mutation in the gene coding for carnitine-acylcarnitine translocase or the OCTN2 transporter aetiologically causes a carnitine deficiency that results in poor intestinal absorption of dietary L-carnitine, its impaired reabsorption by the kidney and, consequently, in increased urinary loss of L-carnitine. Determination of the qualitative pattern of acylcarnitines can be of diagnostic and therapeutic importance. The betaine structure of carnitine requires special analytical procedures for recording. The ionic nature of L-carnitine causes a high water solubility which decreases with increasing chain length of the ester group in the acylcarnitines. Therefore, the distribution of L-carnitine and acylcarnitines in various organs is defined by their function and their physico-chemical properties as well. High performance liquid chromatography (HPLC) permits screening for free and total carnitine, as well as complete quantitative acylcarnitine determination, including the long-chain acylcarnitine profile. (PMID: 17508264 , Monatshefte fuer Chemie (2005), 136(8), 1279-1291., Int J Mass Spectrom. 1999;188:39-52.). |
| Structure |
Download:
MOL |
SDF |
SMILES |
InChI
Display:
2D Structure |
3D Structure
|
| Synonyms |
- 3-Carboxy-N,N,N-trimethyl-2-[(1-oxoheptadecyl)oxy]-1-Propanaminium inner salt
- Carnitine heptadecanoate
- Carnitine heptadecanoic acid
- Heptadecanoate
- Heptadecanoate carnitine
- Heptadecanoic acid
- Heptadecanoyl acid carnitine
- Heptadecanoyl carnitine
- Heptadecanoylcarnitine
|
| Chemical Formula |
C24H47NO4 |
| Average Molecular Weight |
413.6343 |
| Monoisotopic Molecular Weight |
413.350508997 |
| IUPAC Name |
3-(heptadecanoyloxy)-4-(trimethylazaniumyl)butanoate |
| Traditional IUPAC Name |
3-(heptadecanoyloxy)-4-(trimethylaminio)butanoate |
| CAS Registry Number |
106182-29-0 |
| SMILES |
CCCCCCCCCCCCCCCCC(=O)OC(CC([O-])=O)C[N+](C)(C)C |
| InChI Identifier |
InChI=1S/C24H47NO4/c1-5-6-7-8-9-10-11-12-13-14-15-16-17-18-19-24(28)29-22(20-23(26)27)21-25(2,3)4/h22H,5-21H2,1-4H3 |
| InChI Key |
DWSFAVOTORHAAL-UHFFFAOYSA-N |
| Chemical Taxonomy |
| Kingdom |
Organic Compounds |
| Super Class |
Lipids |
| Class |
Fatty Acid Esters |
| Sub Class |
Acyl Carnitines |
| Other Descriptors |
- Aliphatic Acyclic Compounds
- Organic Compounds
|
| Substituents |
- Carboxylic Acid Ester
- Carboxylic Acid Salt
- Carnitine
- Choline
- Dicarboxylic Acid Derivative
- Quaternary Ammonium Salt
|
| Direct Parent |
Acyl Carnitines |
| Ontology |
| Status |
Expected and Not Quantified |
| Origin |
|
| Biofunction |
- Cell signaling
- Fuel and energy storage
- Fuel or energy source
- Lipid catabolism, Fatty acid transport, Energy production
- Membrane integrity/stability
|
| Application |
- Nutrients
- Stabilizers
- Surfactants and Emulsifiers
|
| Cellular locations |
- Cytoplasm
- Extracellular
- Membrane
- Mitochondria
|
| Physical Properties |
| State |
Solid |
| Experimental Properties |
| Property |
Value |
Reference |
| Melting Point |
Not Available |
Not Available |
| Boiling Point |
Not Available |
Not Available |
| Water Solubility |
Not Available |
Not Available |
| LogP |
Not Available |
Not Available |
|
| Predicted Properties |
|
| Spectra |
|
Not Available
|
| Biological Properties |
| Cellular Locations |
- Cytoplasm
- Extracellular
- Membrane
- Mitochondria
|
| Biofluid Locations |
Not Available
|
| Tissue Location |
Not Available
|
| Pathways |
Not Available
|
| Normal Concentrations |
|
Not Available |
| Abnormal Concentrations |
|
Not Available |
| Associated Disorders and Diseases |
| Disease References |
None |
| Associated OMIM IDs |
None |
| External Links |
| DrugBank ID |
Not Available |
| DrugBank Metabolite ID |
Not Available |
| Phenol Explorer Compound ID |
Not Available |
| Phenol Explorer Metabolite ID |
Not Available |
| FoodDB ID |
FDB023836 |
| KNApSAcK ID |
Not Available |
| Chemspider ID |
21233951  |
| KEGG Compound ID |
Not Available |
| BioCyc ID |
Not Available |
| BiGG ID |
2422209  |
| Wikipedia Link |
Not Available |
| NuGOwiki Link |
HMDB06210  |
| Metagene Link |
HMDB06210  |
| METLIN ID |
Not Available |
| PubChem Compound |
53477803  |
| PDB ID |
Not Available |
| ChEBI ID |
Not Available |
| References |
| Synthesis Reference |
Huysmans, L.; Nizigiyimana, L.; Van den Heuvel, H.; Claeys, M. Charge-remote molecular hydrogen removal in protonated and alkali-cationized long-chain fatty acid esters upon cesium ion bombardment. International Journal of Mass Spectrometry (1999), 188(1/2), 39-52. |
| Material Safety Data Sheet (MSDS) |
Not Available
|
| General References |
- Pierre G, Macdonald A, Gray G, Hendriksz C, Preece MA, Chakrapani A: Prospective treatment in carnitine-acylcarnitine translocase deficiency. J Inherit Metab Dis. 2007 Oct;30(5):815. Epub 2007 May 12.
Pubmed: 17508264
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