Accession NumberHMDB00428
Common_Name3-Hydroxyglutaric acid
Description3-Hydroxyglutaric acid is a key metabolite in glutaryl co-enzyme A dehydrogenase deficiency, and is considered to be a potential neurotoxin. The urine level of 3-Hydroxyglutaric acid is elevated in Glutaric Aciduria Type I (glutaryl-CoA dehydrogenase deficiency) patients. (PMID 16573641)
Chemical_IUPAC_Name3-hydroxypentanedioic acid
Chemical FormulaC5H8O5
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Predicted 1H NMR SpectrumDownload
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Predicted 13C NMR PeaklistDownload
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