Accession NumberHMDB00912
Common_NameSuccinyladenosine
DescriptionSuccinyladenosine (SAdo) is one of the dephosphorylated enzyme substrate that accumulates in body fluids of patients with adenylosuccinate lyase (ADSL) deficiency, the other being 5-amino-4-imidazole-N-succinocarboxamide riboside (SAICAr). ADSL is an inherited metabolic disease characterized by various degrees of psychomotor retardation. (PMID 15902552) The severity of the clinical presentation correlates with a low S-Ado/SAICAr ratio in body fluids. (PMID: 15571235) Normally Succinyladenosine is not found in blood or CSF but may be detected in trace amounts in urine. (OMIM 103050)
Chemical_IUPAC_Name(2S)-2-[[9-[(2S,3R,4S,5R)-3,4-dihydroxy-5-(hydroxymethyl)oxolan-2-yl]purin-6-yl]amino]butanedioic acid
Chemical FormulaC14H17N5O8
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Predicted 1H NMR SpectrumDownload
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Predicted 13C NMR PeaklistDownload
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