| Record Information |
| Version |
3.5 |
| Creation Date |
2006-05-22 08:17:44 -0600 |
| Update Date |
2013-02-08 17:11:38 -0700 |
| HMDB ID |
HMDB02250 |
| Secondary Accession Numbers |
None |
| Metabolite Identification |
| Common Name |
Dodecanoylcarnitine |
| Description |
Dodecanoylcarnitine is an acylcarnitine is present in fatty acid oxidation disorders such as long-chain acyl CoA dehydrogenase deficiency, carnitine palmitoyltransferase I deficiency, and carnitine palmitoyltransferase II deficiency. (PMID 12828998 ). |
| Structure |
Download:
MOL |
SDF |
SMILES |
InChI
Display:
2D Structure |
3D Structure
|
| Synonyms |
- (-)-Lauroylcarnitine
- (R)-Dodecanoylcarnitine
- Dodecanoyl-L-carnitine
- L-Carnitine dodecanoyl ester
- Lauroyl-L(-)-carnitin
- Lauroyl-L-carnitine
- Lauroylcarnitine
|
| Chemical Formula |
C19H37NO4 |
| Average Molecular Weight |
343.5014 |
| Monoisotopic Molecular Weight |
343.272258677 |
| IUPAC Name |
(3R)-3-(dodecanoyloxy)-4-(trimethylazaniumyl)butanoate |
| Traditional IUPAC Name |
(3R)-3-(dodecanoyloxy)-4-(trimethylaminio)butanoate |
| CAS Registry Number |
25518-54-1 |
| SMILES |
CCCCCCCCCCCC(=O)O[C@H](CC([O-])=O)C[N+](C)(C)C |
| InChI Identifier |
InChI=1S/C19H37NO4/c1-5-6-7-8-9-10-11-12-13-14-19(23)24-17(15-18(21)22)16-20(2,3)4/h17H,5-16H2,1-4H3/t17-/m1/s1 |
| InChI Key |
FUJLYHJROOYKRA-QGZVFWFLSA-N |
| Chemical Taxonomy |
| Kingdom |
Organic Compounds |
| Super Class |
Lipids |
| Class |
Fatty Acid Esters |
| Sub Class |
Acyl Carnitines |
| Other Descriptors |
- Aliphatic Acyclic Compounds
- Organic Compounds
|
| Substituents |
- Carboxylic Acid Ester
- Carboxylic Acid Salt
- Carnitine
- Choline
- Dicarboxylic Acid Derivative
- Quaternary Ammonium Salt
|
| Direct Parent |
Acyl Carnitines |
| Ontology |
| Status |
Detected and Quantified |
| Origin |
|
| Biofunction |
- Cell signaling
- Fuel and energy storage
- Fuel or energy source
- Lipid catabolism, Fatty acid transport, Energy production
- Membrane integrity/stability
|
| Application |
- Nutrients
- Stabilizers
- Surfactants and Emulsifiers
|
| Cellular locations |
|
| Physical Properties |
| State |
Solid |
| Experimental Properties |
| Property |
Value |
Reference |
| Melting Point |
Not Available |
Not Available |
| Boiling Point |
Not Available |
Not Available |
| Water Solubility |
Not Available |
Not Available |
| LogP |
Not Available |
Not Available |
|
| Predicted Properties |
|
| Spectra |
|
Not Available
|
| Biological Properties |
| Cellular Locations |
|
| Biofluid Locations |
|
| Tissue Location |
|
| Pathways |
Not Available
|
| Normal Concentrations |
|
| Blood |
Detected and Quantified |
|
0.1 +/- 0.03 uM |
Adult (>18 years old) |
Not Specified |
Normal |
Not Available |
| Blood |
Detected and Quantified |
|
0.052 +/- 0.004 uM |
Adult (>18 years old) |
Both |
Normal |
Not Available |
| Blood |
Detected and Quantified |
|
0.038 (0.005-0.069) uM |
Children (1-13 year old) |
Both |
Normal |
Not Available |
| Urine |
Detected and Quantified |
|
0.02 (0.01-0.04) umol/mmol creatinine |
Adult (>18 years old) |
Both |
Normal |
by DF MS/MS (Biocrates kit)
|
|
| Abnormal Concentrations |
|
| Blood |
Detected and Quantified |
|
0.032 +/- 0.002 uM |
Adult (>18 years old) |
Both |
Celiac disease |
Not Available |
| Blood |
Detected and Quantified |
|
0.124 (0.090-0.162) uM |
Adult (>18 years old) |
Both |
Very long-chain acyl-CoA dehydrogenase deficiency (vLCAD) |
Not Available |
|
| Associated Disorders and Diseases |
| Disease References |
| Celiac disease |
- Bene J, Komlosi K, Gasztonyi B, Juhasz M, Tulassay Z, Melegh B: Plasma carnitine ester profile in adult celiac disease patients maintained on long-term gluten free diet. World J Gastroenterol. 2005 Nov 14;11(42):6671-5.
Pubmed: 16425363
|
| Very Long Chain Acyl-CoA Dehydrogenase Deficiency |
- Costa CG, Struys EA, Bootsma A, ten Brink HJ, Dorland L, Tavares de Almeida I, Duran M, Jakobs C: Quantitative analysis of plasma acylcarnitines using gas chromatography chemical ionization mass fragmentography. J Lipid Res. 1997 Jan;38(1):173-82.
Pubmed: 9034211
|
|
| Associated OMIM IDs |
|
| External Links |
| DrugBank ID |
Not Available |
| Phenol Explorer Compound ID |
Not Available |
| Phenol Explorer Metabolite ID |
Not Available |
| FoodDB ID |
FDB022928 |
| KNApSAcK ID |
Not Available |
| Chemspider ID |
147288  |
| KEGG Compound ID |
Not Available |
| BioCyc ID |
Not Available |
| BiGG ID |
Not Available |
| Wikipedia Link |
Not Available |
| NuGOwiki Link |
HMDB02250  |
| Metagene Link |
HMDB02250  |
| METLIN ID |
6573  |
| PubChem Compound |
168381  |
| PDB ID |
Not Available |
| ChEBI ID |
Not Available |
| References |
| Synthesis Reference |
Not Available |
| Material Safety Data Sheet (MSDS) |
Not Available
|
| General References |
- Moder M, Kiessling A, Loster H, Bruggemann L: The pattern of urinary acylcarnitines determined by electrospray mass spectrometry: a new tool in the diagnosis of diabetes mellitus. Anal Bioanal Chem. 2003 Jan;375(2):200-10. Epub 2003 Jan 4.
Pubmed: 12560963
- Shigematsu Y, Hirano S, Hata I, Tanaka Y, Sudo M, Tajima T, Sakura N, Yamaguchi S, Takayanagi M: Selective screening for fatty acid oxidation disorders by tandem mass spectrometry: difficulties in practical discrimination. J Chromatogr B Analyt Technol Biomed Life Sci. 2003 Jul 15;792(1):63-72.
Pubmed: 12828998
- Vianey-Saban C, Divry P, Brivet M, Nada M, Zabot MT, Mathieu M, Roe C: Mitochondrial very-long-chain acyl-coenzyme A dehydrogenase deficiency: clinical characteristics and diagnostic considerations in 30 patients. Clin Chim Acta. 1998 Jan 12;269(1):43-62.
Pubmed: 9498103
- Morrow RJ, Rose ME: Isolation of acylcarnitines from urine: a comparison of methods and application to long-chain acyl-CoA dehydrogenase deficiency. Clin Chim Acta. 1992 Oct 15;211(1-2):73-81.
Pubmed: 1468155
|