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Browsing pathways

Displaying pathways 1 - 25 of 19471 in total
11-beta-hydroxylase deficiency (CYP11B1)
Pw000551Pw000551 greyscalePw000551 simple
HMDB IDNamePathway
HMDB0000015CortexoloneShow
HMDB0000016DeoxycorticosteroneShow
HMDB0000037AldosteroneShow
HMDB0000063CortisolShow
HMDB0000067CholesterolShow
HMDB0000217NADPShow
HMDB0000221NADPHShow
HMDB0000253PregnenoloneShow
HMDB0000268TetrahydrocorticosteroneShow
HMDB000031918-HydroxycorticosteroneShow
HMDB000036317a-HydroxypregnenoloneShow
HMDB000037417-HydroxyprogesteroneShow
HMDB0000902NADShow
HMDB0000903TetrahydrocortisoneShow
HMDB0000949TetrahydrocortisolShow
HMDB00013184-MethylpentanalShow
HMDB0001377OxygenShow
HMDB0001487NADHShow
HMDB0001547CorticosteroneShow
HMDB0001830ProgesteroneShow
HMDB0002111WaterShow
HMDB0002802CortisoneShow
HMDB0003178HemeShow
HMDB0003259DihydrocortisolShow
HMDB00037595a-Pregnane-3,20-dioneShow
HMDB000402621-HydroxypregnenoloneShow
HMDB000402911-DehydrocorticosteroneShow
HMDB000403021-DeoxycortisolShow
HMDB000403111b-HydroxyprogesteroneShow
HMDB000403522b-HydroxycholesterolShow
HMDB000628320alpha-HydroxycholesterolShow
HMDB00067533a,11b,21-Trihydroxy-20-oxo-5b-pregnan-18-alShow
HMDB000675411b,21-Dihydroxy-3,20-oxo-5b-pregnan-18-alShow
HMDB00067553a,21-Dihydroxy-5b-pregnane-11,20-dioneShow
HMDB000675621-Hydroxy-5b-pregnane-3,11,20-trioneShow
HMDB000675711b,21-Dihydroxy-5b-pregnane-3,20-dioneShow
HMDB000675817a,21-Dihydroxy-5b-pregnane-3,11,20-trioneShow
HMDB00067593a-Hydroxy-5b-pregnane-20-oneShow
HMDB000676011b,17a,21-Trihydroxypreg-nenoloneShow
HMDB000676217a,21-Dihydroxypreg-nenoloneShow
HMDB000676320a,22b-DihydroxycholesterolShow
HMDB000676417a,20a-DihydroxycholesterolShow
HMDB0059597Hydrogen IonShow
17-alpha-hydroxylase deficiency (CYP17)
Pw000542Pw000542 greyscalePw000542 simple
HMDB IDNamePathway
HMDB0000015CortexoloneShow
HMDB0000016DeoxycorticosteroneShow
HMDB0000037AldosteroneShow
HMDB0000063CortisolShow
HMDB0000067CholesterolShow
HMDB0000217NADPShow
HMDB0000221NADPHShow
HMDB0000253PregnenoloneShow
HMDB0000268TetrahydrocorticosteroneShow
HMDB000031918-HydroxycorticosteroneShow
HMDB000036317a-HydroxypregnenoloneShow
HMDB000037417-HydroxyprogesteroneShow
HMDB0000902NADShow
HMDB0000903TetrahydrocortisoneShow
HMDB0000949TetrahydrocortisolShow
HMDB00013184-MethylpentanalShow
HMDB0001377OxygenShow
HMDB0001487NADHShow
HMDB0001547CorticosteroneShow
HMDB0001830ProgesteroneShow
HMDB0002111WaterShow
HMDB0002802CortisoneShow
HMDB0003178HemeShow
HMDB0003259DihydrocortisolShow
HMDB00037595a-Pregnane-3,20-dioneShow
HMDB000402621-HydroxypregnenoloneShow
HMDB000402911-DehydrocorticosteroneShow
HMDB000403021-DeoxycortisolShow
HMDB000403111b-HydroxyprogesteroneShow
HMDB000403522b-HydroxycholesterolShow
HMDB000628320alpha-HydroxycholesterolShow
HMDB00067533a,11b,21-Trihydroxy-20-oxo-5b-pregnan-18-alShow
HMDB000675411b,21-Dihydroxy-3,20-oxo-5b-pregnan-18-alShow
HMDB00067553a,21-Dihydroxy-5b-pregnane-11,20-dioneShow
HMDB000675621-Hydroxy-5b-pregnane-3,11,20-trioneShow
HMDB000675711b,21-Dihydroxy-5b-pregnane-3,20-dioneShow
HMDB000675817a,21-Dihydroxy-5b-pregnane-3,11,20-trioneShow
HMDB00067593a-Hydroxy-5b-pregnane-20-oneShow
HMDB000676011b,17a,21-Trihydroxypreg-nenoloneShow
HMDB000676217a,21-Dihydroxypreg-nenoloneShow
HMDB000676320a,22b-DihydroxycholesterolShow
HMDB000676417a,20a-DihydroxycholesterolShow
HMDB0059597Hydrogen IonShow
17-Beta Hydroxysteroid Dehydrogenase III Deficiency
Pw000059Pw000059 greyscalePw000059 simple
2-aminoadipic 2-oxoadipic aciduria
Pw000696Pw000696 greyscalePw000696 simple
2-Hydroxyglutric Aciduria (D And L Form)
Pw000212Pw000212 greyscalePw000212 simple
2-ketoglutarate dehydrogenase complex deficiency
Pw000525Pw000525 greyscalePw000525 simple
2-Methyl-3-Hydroxybutryl CoA Dehydrogenase Deficiency
Pw000061Pw000061 greyscalePw000061 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
21-hydroxylase deficiency (CYP21)
Pw000552Pw000552 greyscalePw000552 simple
HMDB IDNamePathway
HMDB0000015CortexoloneShow
HMDB0000016DeoxycorticosteroneShow
HMDB0000037AldosteroneShow
HMDB0000063CortisolShow
HMDB0000067CholesterolShow
HMDB0000217NADPShow
HMDB0000221NADPHShow
HMDB0000253PregnenoloneShow
HMDB0000268TetrahydrocorticosteroneShow
HMDB000031918-HydroxycorticosteroneShow
HMDB000036317a-HydroxypregnenoloneShow
HMDB000037417-HydroxyprogesteroneShow
HMDB0000902NADShow
HMDB0000903TetrahydrocortisoneShow
HMDB0000949TetrahydrocortisolShow
HMDB00013184-MethylpentanalShow
HMDB0001377OxygenShow
HMDB0001487NADHShow
HMDB0001547CorticosteroneShow
HMDB0001830ProgesteroneShow
HMDB0002111WaterShow
HMDB0002802CortisoneShow
HMDB0003178HemeShow
HMDB0003259DihydrocortisolShow
HMDB00037595a-Pregnane-3,20-dioneShow
HMDB000402621-HydroxypregnenoloneShow
HMDB000402911-DehydrocorticosteroneShow
HMDB000403021-DeoxycortisolShow
HMDB000403111b-HydroxyprogesteroneShow
HMDB000403522b-HydroxycholesterolShow
HMDB000628320alpha-HydroxycholesterolShow
HMDB00067533a,11b,21-Trihydroxy-20-oxo-5b-pregnan-18-alShow
HMDB000675411b,21-Dihydroxy-3,20-oxo-5b-pregnan-18-alShow
HMDB00067553a,21-Dihydroxy-5b-pregnane-11,20-dioneShow
HMDB000675621-Hydroxy-5b-pregnane-3,11,20-trioneShow
HMDB000675711b,21-Dihydroxy-5b-pregnane-3,20-dioneShow
HMDB000675817a,21-Dihydroxy-5b-pregnane-3,11,20-trioneShow
HMDB00067593a-Hydroxy-5b-pregnane-20-oneShow
HMDB000676011b,17a,21-Trihydroxypreg-nenoloneShow
HMDB000676217a,21-Dihydroxypreg-nenoloneShow
HMDB000676320a,22b-DihydroxycholesterolShow
HMDB000676417a,20a-DihydroxycholesterolShow
HMDB0059597Hydrogen IonShow
27-Hydroxylase Deficiency
Pw000697Pw000697 greyscalePw000697 simple
HMDB IDNamePathway
HMDB0000036Taurocholic acidShow
HMDB0000067CholesterolShow
HMDB0000123GlycineShow
HMDB0000138Glycocholic acidShow
HMDB0000217NADPShow
HMDB0000220Palmitic acidShow
HMDB0000221NADPHShow
HMDB0000250PyrophosphateShow
HMDB0000251TaurineShow
HMDB00003593a,7a-Dihydroxycoprostanic acidShow
HMDB0000518Chenodeoxycholic acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000619Cholic acidShow
HMDB0000626Deoxycholic acidShow
HMDB0000631Deoxycholic acid glycine conjugateShow
HMDB0000637Chenodeoxycholic acid glycine conjugateShow
HMDB0000698Lithocholic acid glycine conjugateShow
HMDB0000722LithocholyltaurineShow
HMDB0000761Lithocholic acidShow
HMDB0000896Taurodeoxycholic acidShow
HMDB0000902NADShow
HMDB0000951Taurochenodesoxycholic acidShow
HMDB000123127-Deoxy-5b-cyprinolShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB0001374Choloyl-CoAShow
HMDB0001377OxygenShow
HMDB000141924-HydroxycholesterolShow
HMDB0001423Coenzyme AShow
HMDB00014575-b-Cholestane-3a ,7a ,12a-triolShow
HMDB0001487NADHShow
HMDB00014967a-HydroxycholesterolShow
HMDB00019937a-Hydroxy-cholestene-3-oneShow
HMDB000210327-HydroxycholesterolShow
HMDB0002111WaterShow
HMDB00021593a,7a-Dihydroxy-5b-cholestanoyl-CoAShow
HMDB00021977a,12a-Dihydroxy-cholestene-3-oneShow
HMDB0003178HemeShow
HMDB00035333a,7a,12a-Trihydroxy-5b-cholestan-26-alShow
HMDB00035403'-AMPShow
HMDB00038733a,7a,12a-Trihydroxy-5b-cholestanoic acidShow
HMDB000624725-HydroxycholesterolShow
HMDB00062807-a,25-DihydroxycholesterolShow
HMDB00062817-a,27-DihydroxycholesterolShow
HMDB0006292Chenodeoxycholoyl-CoAShow
HMDB0006737CE(22:2(13Z,16Z))Show
HMDB00068877a,12a-Dihydroxy-5b-cholestan-3-oneShow
HMDB00068885b-Cyprinol sulfateShow
HMDB00068893a,7a,12a-Trihydroxy-5b-cholest-24-enoyl-CoAShow
HMDB00068903a,7a,12a,24-Tetrahydroxy-5b-cholestanoyl-CoAShow
HMDB00068913a,7a,12a-Trihydroxy-5b-24-oxocholestanoyl-CoAShow
HMDB00068927a-Hydroxy-5b-cholestan-3-oneShow
HMDB00068933a,7a-Dihydroxy-5b-cholestaneShow
HMDB00068943a,7a-Dihydroxy-5b-cholestan-26-alShow
HMDB00068953a,7a-Dihydroxy-5b-cholest-24-enoyl-CoAShow
HMDB0011644(24R)-Cholest-5-ene-3-beta,7-alpha,24-triol Show
HMDB00124533 beta-Hydroxy-5-cholestenoateShow
HMDB00124543 beta,7 alpha-Dihydroxy-5-cholestenoateShow
HMDB00124553 alpha,7 alpha,26-Trihydroxy-5beta-cholestaneShow
HMDB00124563 alpha,7 alpha,24-Trihydroxy-5beta-cholestanoyl-CoAShow
HMDB00124587 alpha-Hydroxy-3-oxo-4-cholestenoateShow
HMDB00124597 alpha,26-Dihydroxy-4-cholesten-3-oneShow
HMDB0015531IronShow
3-Beta-Hydroxysteroid Dehydrogenase Deficiency
Pw000695Pw000695 greyscalePw000695 simple
HMDB IDNamePathway
HMDB0000015CortexoloneShow
HMDB0000016DeoxycorticosteroneShow
HMDB0000037AldosteroneShow
HMDB0000063CortisolShow
HMDB0000067CholesterolShow
HMDB0000217NADPShow
HMDB0000221NADPHShow
HMDB0000253PregnenoloneShow
HMDB0000268TetrahydrocorticosteroneShow
HMDB000031918-HydroxycorticosteroneShow
HMDB000036317a-HydroxypregnenoloneShow
HMDB000037417-HydroxyprogesteroneShow
HMDB0000902NADShow
HMDB0000903TetrahydrocortisoneShow
HMDB0000949TetrahydrocortisolShow
HMDB00013184-MethylpentanalShow
HMDB0001377OxygenShow
HMDB0001487NADHShow
HMDB0001547CorticosteroneShow
HMDB0001830ProgesteroneShow
HMDB0002111WaterShow
HMDB0002802CortisoneShow
HMDB0003178HemeShow
HMDB0003259DihydrocortisolShow
HMDB00037595a-Pregnane-3,20-dioneShow
HMDB000402621-HydroxypregnenoloneShow
HMDB000402911-DehydrocorticosteroneShow
HMDB000403021-DeoxycortisolShow
HMDB000403111b-HydroxyprogesteroneShow
HMDB000403522b-HydroxycholesterolShow
HMDB000628320alpha-HydroxycholesterolShow
HMDB00067533a,11b,21-Trihydroxy-20-oxo-5b-pregnan-18-alShow
HMDB000675411b,21-Dihydroxy-3,20-oxo-5b-pregnan-18-alShow
HMDB00067553a,21-Dihydroxy-5b-pregnane-11,20-dioneShow
HMDB000675621-Hydroxy-5b-pregnane-3,11,20-trioneShow
HMDB000675711b,21-Dihydroxy-5b-pregnane-3,20-dioneShow
HMDB000675817a,21-Dihydroxy-5b-pregnane-3,11,20-trioneShow
HMDB00067593a-Hydroxy-5b-pregnane-20-oneShow
HMDB000676011b,17a,21-Trihydroxypreg-nenoloneShow
HMDB000676217a,21-Dihydroxypreg-nenoloneShow
HMDB000676320a,22b-DihydroxycholesterolShow
HMDB000676417a,20a-DihydroxycholesterolShow
HMDB0059597Hydrogen IonShow
3-Hydroxy-3-Methylglutaryl-CoA Lyase Deficiency
Pw000063Pw000063 greyscalePw000063 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
3-hydroxyisobutyric acid dehydrogenase deficiency
Pw000497Pw000497 greyscalePw000497 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
3-hydroxyisobutyric aciduria
Pw000498Pw000498 greyscalePw000498 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
3-Methylcrotonyl Coa Carboxylase Deficiency Type I
Pw000065Pw000065 greyscalePw000065 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
3-Methylglutaconic Aciduria Type I
Pw000066Pw000066 greyscalePw000066 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
3-Methylglutaconic Aciduria Type III
Pw000067Pw000067 greyscalePw000067 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
3-Methylglutaconic Aciduria Type IV
Pw000214Pw000214 greyscalePw000214 simple
HMDB IDNamePathway
HMDB0000019Alpha-ketoisovaleric acidShow
HMDB0000023(S)-3-Hydroxyisobutyric acidShow
HMDB0000030BiotinShow
HMDB0000060Acetoacetic acidShow
HMDB0000148L-Glutamic acidShow
HMDB0000172L-IsoleucineShow
HMDB0000202Methylmalonic acidShow
HMDB0000208Oxoglutaric acidShow
HMDB0000254Succinic acidShow
HMDB00004913-Methyl-2-oxovaleric acidShow
HMDB0000538Adenosine triphosphateShow
HMDB0000595Hydrogen carbonateShow
HMDB0000687L-LeucineShow
HMDB0000695KetoleucineShow
HMDB0000883L-ValineShow
HMDB0000902NADShow
HMDB0000962LipoamideShow
HMDB0000985DihydrolipoamideShow
HMDB0001011Methacrylyl-CoAShow
HMDB0001022Succinyl-CoAShow
HMDB00010412-Methylbutyryl-CoAShow
HMDB0001052(S)-3-Hydroxyisobutyryl-CoAShow
HMDB00010573-Methylglutaconyl-CoAShow
HMDB0001113Isovaleryl-CoAShow
HMDB00011572-Methylacetoacetyl-CoAShow
HMDB0001206Acetyl-CoAShow
HMDB0001243Isobutyryl-CoAShow
HMDB0001248FADShow
HMDB0001275Propionyl-CoAShow
HMDB0001341ADPShow
HMDB00013562-Methyl-3-hydroxybutyryl-CoAShow
HMDB0001372Thiamine pyrophosphateShow
HMDB00013753-Hydroxy-3-methylglutaryl-CoAShow
HMDB0001377OxygenShow
HMDB0001423Coenzyme AShow
HMDB0001429PhosphateShow
HMDB0001484Acetoacetyl-CoAShow
HMDB0001487NADHShow
HMDB0001491Pyridoxal 5'-phosphateShow
HMDB00014933-Methylcrotonyl-CoAShow
HMDB0001545PyridoxalShow
HMDB0001967Carbon dioxideShow
HMDB0002054Tiglyl-CoAShow
HMDB0002086AdenosylcobalaminShow
HMDB0002111WaterShow
HMDB0002166(S)-b-aminoisobutyric acidShow
HMDB0002206MolybdopterinShow
HMDB0002217(S)-Methylmalonic acid semialdehydeShow
HMDB0002255R-Methylmalonyl-CoAShow
HMDB0002310S-Methylmalonyl-CoAShow
HMDB0003125Hydrogen peroxideShow
HMDB00068653-Methyl-1-hydroxybutyl-ThPPShow
HMDB00068662-Methyl-1-hydroxypropyl-ThPP Show
HMDB0006867S-(3-Methylbutanoyl)-dihydrolipoamide-EShow
HMDB0006868S-(2-Methylpropionyl)-dihydrolipoamide-EShow
HMDB0006869S-(2-Methylbutanoyl)-dihydrolipoamideShow
HMDB00068703-Hydroxyisovaleryl-CoAShow
HMDB0013617Lipoyl-GMPShow
HMDB0059597Hydrogen IonShow
Displaying pathways 1 - 25 of 19471 in total